Dental care management in a child with recessive dystrophic epidermolysis bullosa

Detalhes bibliográficos
Autor(a) principal: Torres,Carolina Paes
Data de Publicação: 2011
Outros Autores: Gomes-Silva,Jaciara Miranda, Mellara,Thalita Siqueira, Carvalho,Lívia Pasqualini, Borsatto,Maria Cristina
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Brazilian Dental Journal
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0103-64402011000600012
Resumo: Epidermolysis bullosa (EB) is a heterogeneous group of rare genetic disorders characterized by marked fragility of the skin and mucous membranes in which vesiculobullous lesions occur in response to trauma, heat or no apparent cause. The recessive form of EB presents the greatest oral alterations including repeated blistering and scar formation leading to limited oral opening, ankyloglossia, tongue denudation, microstomia, vestibule obliteration and predisposition to oral carcinoma. Routine dental care may cause bullae formation on the lips and oral mucosa. Together with the ingestion of soft and frequently carbohydrate food, these anomalies lead to a high caries risk. This paper documents a case of a child diagnosed with recessive dystrophic epidermolysis bullosa (RDEB); describes the phases and difficulties of dental treatment and the measures that dentists and health care providers should adopt in order to provide a safe and effective dental treatment as well as earlier prevention to these patients.
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spelling Dental care management in a child with recessive dystrophic epidermolysis bullosaEpidermolysis bullosadental carespecial needs patientEpidermolysis bullosa (EB) is a heterogeneous group of rare genetic disorders characterized by marked fragility of the skin and mucous membranes in which vesiculobullous lesions occur in response to trauma, heat or no apparent cause. The recessive form of EB presents the greatest oral alterations including repeated blistering and scar formation leading to limited oral opening, ankyloglossia, tongue denudation, microstomia, vestibule obliteration and predisposition to oral carcinoma. Routine dental care may cause bullae formation on the lips and oral mucosa. Together with the ingestion of soft and frequently carbohydrate food, these anomalies lead to a high caries risk. This paper documents a case of a child diagnosed with recessive dystrophic epidermolysis bullosa (RDEB); describes the phases and difficulties of dental treatment and the measures that dentists and health care providers should adopt in order to provide a safe and effective dental treatment as well as earlier prevention to these patients.Fundação Odontológica de Ribeirão Preto2011-01-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0103-64402011000600012Brazilian Dental Journal v.22 n.6 2011reponame:Brazilian Dental Journalinstname:Fundação Odontológica de Ribeirão Preto (FUNORP)instacron:FUNORP10.1590/S0103-64402011000600012info:eu-repo/semantics/openAccessTorres,Carolina PaesGomes-Silva,Jaciara MirandaMellara,Thalita SiqueiraCarvalho,Lívia PasqualiniBorsatto,Maria Cristinaeng2011-12-15T00:00:00Zoai:scielo:S0103-64402011000600012Revistahttps://www.scielo.br/j/bdj/https://old.scielo.br/oai/scielo-oai.phpbdj@forp.usp.br||sergio@fosjc.unesp.br1806-47600103-6440opendoar:2011-12-15T00:00Brazilian Dental Journal - Fundação Odontológica de Ribeirão Preto (FUNORP)false
dc.title.none.fl_str_mv Dental care management in a child with recessive dystrophic epidermolysis bullosa
title Dental care management in a child with recessive dystrophic epidermolysis bullosa
spellingShingle Dental care management in a child with recessive dystrophic epidermolysis bullosa
Torres,Carolina Paes
Epidermolysis bullosa
dental care
special needs patient
title_short Dental care management in a child with recessive dystrophic epidermolysis bullosa
title_full Dental care management in a child with recessive dystrophic epidermolysis bullosa
title_fullStr Dental care management in a child with recessive dystrophic epidermolysis bullosa
title_full_unstemmed Dental care management in a child with recessive dystrophic epidermolysis bullosa
title_sort Dental care management in a child with recessive dystrophic epidermolysis bullosa
author Torres,Carolina Paes
author_facet Torres,Carolina Paes
Gomes-Silva,Jaciara Miranda
Mellara,Thalita Siqueira
Carvalho,Lívia Pasqualini
Borsatto,Maria Cristina
author_role author
author2 Gomes-Silva,Jaciara Miranda
Mellara,Thalita Siqueira
Carvalho,Lívia Pasqualini
Borsatto,Maria Cristina
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Torres,Carolina Paes
Gomes-Silva,Jaciara Miranda
Mellara,Thalita Siqueira
Carvalho,Lívia Pasqualini
Borsatto,Maria Cristina
dc.subject.por.fl_str_mv Epidermolysis bullosa
dental care
special needs patient
topic Epidermolysis bullosa
dental care
special needs patient
description Epidermolysis bullosa (EB) is a heterogeneous group of rare genetic disorders characterized by marked fragility of the skin and mucous membranes in which vesiculobullous lesions occur in response to trauma, heat or no apparent cause. The recessive form of EB presents the greatest oral alterations including repeated blistering and scar formation leading to limited oral opening, ankyloglossia, tongue denudation, microstomia, vestibule obliteration and predisposition to oral carcinoma. Routine dental care may cause bullae formation on the lips and oral mucosa. Together with the ingestion of soft and frequently carbohydrate food, these anomalies lead to a high caries risk. This paper documents a case of a child diagnosed with recessive dystrophic epidermolysis bullosa (RDEB); describes the phases and difficulties of dental treatment and the measures that dentists and health care providers should adopt in order to provide a safe and effective dental treatment as well as earlier prevention to these patients.
publishDate 2011
dc.date.none.fl_str_mv 2011-01-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0103-64402011000600012
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0103-64402011000600012
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/S0103-64402011000600012
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Fundação Odontológica de Ribeirão Preto
publisher.none.fl_str_mv Fundação Odontológica de Ribeirão Preto
dc.source.none.fl_str_mv Brazilian Dental Journal v.22 n.6 2011
reponame:Brazilian Dental Journal
instname:Fundação Odontológica de Ribeirão Preto (FUNORP)
instacron:FUNORP
instname_str Fundação Odontológica de Ribeirão Preto (FUNORP)
instacron_str FUNORP
institution FUNORP
reponame_str Brazilian Dental Journal
collection Brazilian Dental Journal
repository.name.fl_str_mv Brazilian Dental Journal - Fundação Odontológica de Ribeirão Preto (FUNORP)
repository.mail.fl_str_mv bdj@forp.usp.br||sergio@fosjc.unesp.br
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