Leiomyosarcoma Metastatic to the Skull and Spine: a Case Report
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Data de Publicação: | 2011 |
Outros Autores: | , , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Revista Brasileira de Cancerologia (Online) |
Texto Completo: | https://rbc.inca.gov.br/index.php/revista/article/view/689 |
Resumo: | Background: Uterine leiomyosarcomas account for approximately 30% of uterine sarcomas. The peak incidence age is around the mid-thirties reaching a plateau in the mid-fifties. It rarely metastasizes to the skull and the bone. Case Presentation: In this report, we describe an unusual case of uterine leiomyosarcoma metastasizing to both the spine and the skull. This patient had a known diagnosis of uterine leiomyosarcoma following a total hysterectomy five years before. She underwent resection of the skull mass and radiotherapy for the spinal lesions. Conclusion: Leiomyosarcoma is usually accompanied by widespread metastases and a poor chance of survival. Skull metastases are usually seen in the advanced stage of the disease. Surgery cannot change the course of the underlying disease, but can relieve local discomfort. Treatment options for spinal metastases are varied, and definitive statements regarding efficacy cannot be made. To our knowledge, this is the first case of simultaneous metastatic deposits in both spine and skull. |
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Leiomyosarcoma Metastatic to the Skull and Spine: a Case ReportMetástasis de Leiomiosarcoma en el Cráneo y la Columna Vertebral: Informe de un CasoMetástase de Leiomiossarcoma para o Crânio e Coluna: Relato de CasoLeiomiossarcomaColuna VertebralNeoplasias CranianasEstudos de CasosLeiomyosarcomaSpineSkull NeoplasmsCase StudiesLeiomiosarcomaColumna VertebralNeoplasias CranealesEstudios de CasosBackground: Uterine leiomyosarcomas account for approximately 30% of uterine sarcomas. The peak incidence age is around the mid-thirties reaching a plateau in the mid-fifties. It rarely metastasizes to the skull and the bone. Case Presentation: In this report, we describe an unusual case of uterine leiomyosarcoma metastasizing to both the spine and the skull. This patient had a known diagnosis of uterine leiomyosarcoma following a total hysterectomy five years before. She underwent resection of the skull mass and radiotherapy for the spinal lesions. Conclusion: Leiomyosarcoma is usually accompanied by widespread metastases and a poor chance of survival. Skull metastases are usually seen in the advanced stage of the disease. Surgery cannot change the course of the underlying disease, but can relieve local discomfort. Treatment options for spinal metastases are varied, and definitive statements regarding efficacy cannot be made. To our knowledge, this is the first case of simultaneous metastatic deposits in both spine and skull. Introducción: El leiomiosarcoma uterino representa, aproximadamente, el 30% de los sarcomas uterinos. La edad de mayor incidencia es a mediados de los treinta, estabilizándose a mediados de los cincuenta. En raras ocasiones envía metástasis al cráneo y los huesos. Presentación del caso: Divulgamos aquí un caso raro de leiomiosarcoma uterino con metástasis para el cráneo y columna. La paciente tenía un diagnóstico previo de leiomiosarcoma uterino tras histerectomía total, sucedida cinco años antes. La lesión craneal se resecó y las lesiones de la columna fueran tratadas con radioterapia. Conclusión: El leiomiosarcoma suele acompañarse de metástasis diseminadas y pronóstico reservado. Metástasis del cráneo ocurren en la etapa avanzada de la enfermedad. La cirugía no altera el curso de la enfermedad subyacente, pero alivia el malestar local. Las opciones de tratamiento para las metástasis vertebrales son variadas, y uno no puede hacer declaraciones definitivas sobre sus eficacias. A nuestro entender, es el primer caso reportado que presenta ambas las metástasis de modo simultáneo. Introdução: O leiomiossarcoma uterino corresponde a, aproximadamente, 30% dos sarcomas uterinos. A idade de maior incidência é por volta dos trinta e cinco anos, alcançando seu crescimento máximo aos cinquenta e cinco anos. Raramente envia metástases para o crânio e para os ossos. Apresentação do caso: Neste relato, descreve-se um caso raro de leiomiossarcoma uterino com metástase para o crânio e coluna. A paciente tinha um diagnóstico prévio de leiomiosarcoma uterino após histerectomia total ocorrida há cinco anos. A lesão craniana foi ressecada e as lesões da coluna foram abordadas com radioterapia. Conclusão: O leiomiossarcoma é normalmente acompanhado por metástases disseminadas e um prognóstico reservado. Metástases do crânio são geralmente vistas em um estágio avançado da doença. A cirurgia não pode alterar o curso da doença subjacente, mas pode aliviar o desconforto local. As opções de tratamento para as metástases espinais são variadas, e as indicações definitivas sobre eficácia não podem ser feitas. Ao nosso conhecimento, é o primeiro caso relatado com ambas as metástases apresentando-se simultaneamente.INCA2011-03-31info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionRelato de Casoapplication/pdfhttps://rbc.inca.gov.br/index.php/revista/article/view/68910.32635/2176-9745.RBC.2011v57n1.689Revista Brasileira de Cancerologia; Vol. 57 No. 1 (2011): Jan./Feb./Mar.; 63-66Revista Brasileira de Cancerologia; Vol. 57 Núm. 1 (2011): ene./feb./mar.; 63-66Revista Brasileira de Cancerologia; v. 57 n. 1 (2011): jan./fev./mar.; 63-662176-9745reponame:Revista Brasileira de Cancerologia (Online)instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)instacron:INCAenghttps://rbc.inca.gov.br/index.php/revista/article/view/689/463https://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessPereira, Francisco Otávio Camargo Pereira, Daniel Callegari Aguiar, Rafael de CastroLombardi, Ismael Augusto Silva Zanini, Marco Antonio 2023-07-25T13:06:18Zoai:rbc.inca.gov.br:article/689Revistahttps://rbc.inca.gov.br/index.php/revistaPUBhttps://rbc.inca.gov.br/index.php/revista/oairbc@inca.gov.br0034-71162176-9745opendoar:2023-07-25T13:06:18Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)false |
dc.title.none.fl_str_mv |
Leiomyosarcoma Metastatic to the Skull and Spine: a Case Report Metástasis de Leiomiosarcoma en el Cráneo y la Columna Vertebral: Informe de un Caso Metástase de Leiomiossarcoma para o Crânio e Coluna: Relato de Caso |
title |
Leiomyosarcoma Metastatic to the Skull and Spine: a Case Report |
spellingShingle |
Leiomyosarcoma Metastatic to the Skull and Spine: a Case Report Pereira, Francisco Otávio Camargo Leiomiossarcoma Coluna Vertebral Neoplasias Cranianas Estudos de Casos Leiomyosarcoma Spine Skull Neoplasms Case Studies Leiomiosarcoma Columna Vertebral Neoplasias Craneales Estudios de Casos |
title_short |
Leiomyosarcoma Metastatic to the Skull and Spine: a Case Report |
title_full |
Leiomyosarcoma Metastatic to the Skull and Spine: a Case Report |
title_fullStr |
Leiomyosarcoma Metastatic to the Skull and Spine: a Case Report |
title_full_unstemmed |
Leiomyosarcoma Metastatic to the Skull and Spine: a Case Report |
title_sort |
Leiomyosarcoma Metastatic to the Skull and Spine: a Case Report |
author |
Pereira, Francisco Otávio Camargo |
author_facet |
Pereira, Francisco Otávio Camargo Pereira, Daniel Callegari Aguiar, Rafael de Castro Lombardi, Ismael Augusto Silva Zanini, Marco Antonio |
author_role |
author |
author2 |
Pereira, Daniel Callegari Aguiar, Rafael de Castro Lombardi, Ismael Augusto Silva Zanini, Marco Antonio |
author2_role |
author author author author |
dc.contributor.author.fl_str_mv |
Pereira, Francisco Otávio Camargo Pereira, Daniel Callegari Aguiar, Rafael de Castro Lombardi, Ismael Augusto Silva Zanini, Marco Antonio |
dc.subject.por.fl_str_mv |
Leiomiossarcoma Coluna Vertebral Neoplasias Cranianas Estudos de Casos Leiomyosarcoma Spine Skull Neoplasms Case Studies Leiomiosarcoma Columna Vertebral Neoplasias Craneales Estudios de Casos |
topic |
Leiomiossarcoma Coluna Vertebral Neoplasias Cranianas Estudos de Casos Leiomyosarcoma Spine Skull Neoplasms Case Studies Leiomiosarcoma Columna Vertebral Neoplasias Craneales Estudios de Casos |
description |
Background: Uterine leiomyosarcomas account for approximately 30% of uterine sarcomas. The peak incidence age is around the mid-thirties reaching a plateau in the mid-fifties. It rarely metastasizes to the skull and the bone. Case Presentation: In this report, we describe an unusual case of uterine leiomyosarcoma metastasizing to both the spine and the skull. This patient had a known diagnosis of uterine leiomyosarcoma following a total hysterectomy five years before. She underwent resection of the skull mass and radiotherapy for the spinal lesions. Conclusion: Leiomyosarcoma is usually accompanied by widespread metastases and a poor chance of survival. Skull metastases are usually seen in the advanced stage of the disease. Surgery cannot change the course of the underlying disease, but can relieve local discomfort. Treatment options for spinal metastases are varied, and definitive statements regarding efficacy cannot be made. To our knowledge, this is the first case of simultaneous metastatic deposits in both spine and skull. |
publishDate |
2011 |
dc.date.none.fl_str_mv |
2011-03-31 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion Relato de Caso |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://rbc.inca.gov.br/index.php/revista/article/view/689 10.32635/2176-9745.RBC.2011v57n1.689 |
url |
https://rbc.inca.gov.br/index.php/revista/article/view/689 |
identifier_str_mv |
10.32635/2176-9745.RBC.2011v57n1.689 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
https://rbc.inca.gov.br/index.php/revista/article/view/689/463 |
dc.rights.driver.fl_str_mv |
https://creativecommons.org/licenses/by/4.0 info:eu-repo/semantics/openAccess |
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https://creativecommons.org/licenses/by/4.0 |
eu_rights_str_mv |
openAccess |
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application/pdf |
dc.publisher.none.fl_str_mv |
INCA |
publisher.none.fl_str_mv |
INCA |
dc.source.none.fl_str_mv |
Revista Brasileira de Cancerologia; Vol. 57 No. 1 (2011): Jan./Feb./Mar.; 63-66 Revista Brasileira de Cancerologia; Vol. 57 Núm. 1 (2011): ene./feb./mar.; 63-66 Revista Brasileira de Cancerologia; v. 57 n. 1 (2011): jan./fev./mar.; 63-66 2176-9745 reponame:Revista Brasileira de Cancerologia (Online) instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA) instacron:INCA |
instname_str |
Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA) |
instacron_str |
INCA |
institution |
INCA |
reponame_str |
Revista Brasileira de Cancerologia (Online) |
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Revista Brasileira de Cancerologia (Online) |
repository.name.fl_str_mv |
Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA) |
repository.mail.fl_str_mv |
rbc@inca.gov.br |
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