Primitive Neuroectodermic Tumor in Childwood: a Report of 13 Cases and Literature Review

Detalhes bibliográficos
Autor(a) principal: Costa, Cecília M. L.
Data de Publicação: 2000
Outros Autores: Rondinelli, Patricia, Camargo, Beatriz de
Tipo de documento: Artigo
Idioma: por
Título da fonte: Revista Brasileira de Cancerologia (Online)
Texto Completo: https://rbc.inca.gov.br/index.php/revista/article/view/2440
Resumo: Proposal: The autors review the chart of 13 patients with diagnosis of peripheral primitive neuroectodermal tumor (PNET), admitted at the Pediatric Department of Cancer Hospital between the period of 1989 and 1996. Patients and methods: All patients with PNET were analysed in a retrospective way, using epidemiologic clinical data, treatment and outcome. Results: Surgery was the first therapeutic approach in 2 patients. Chemotherapy was administered in 12 patient and radiotherapy in 2. From the 13 patient, five are alive with an average follow up of 48 months after the end of the treatment. Conclusion: This analyis confirms the heterogeneity and agressiveness of PNET tumors. Multicentric studies are necessary for prognostic factors analysis.
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spelling Primitive Neuroectodermic Tumor in Childwood: a Report of 13 Cases and Literature ReviewTumor Neuroectodérmico Primitivo na Infância: Relato de 13 Casos e Revisão da LiteraturaTumor Neuroectodérmico PrimitivoSarcomaNeoplasias de Tecidos MolesPrimitive Neuroectodermic TumorSarcomaSoft Tissue NeoplasmsProposal: The autors review the chart of 13 patients with diagnosis of peripheral primitive neuroectodermal tumor (PNET), admitted at the Pediatric Department of Cancer Hospital between the period of 1989 and 1996. Patients and methods: All patients with PNET were analysed in a retrospective way, using epidemiologic clinical data, treatment and outcome. Results: Surgery was the first therapeutic approach in 2 patients. Chemotherapy was administered in 12 patient and radiotherapy in 2. From the 13 patient, five are alive with an average follow up of 48 months after the end of the treatment. Conclusion: This analyis confirms the heterogeneity and agressiveness of PNET tumors. Multicentric studies are necessary for prognostic factors analysis.Proposta: A proposta desse estudo é a análise retrospectiva dos pacientes com diagnóstico de tumor neuroectodérmico primitivo (PNET), admitidos no Departamento de Pediatria do Hospital do Câncer no periodo de 1989 a 1996. Pacienttes e métodos: Todos os 13 pacientes portadores de PNET foram analisados retrospectivamente utilizando uma ficha para obtenção dos dados epidemiológicos clínicos, terapêuticos e seguimento de cada paciente. Resultados: A cirurgia foi a primeira abordagem terapêutica em 2 pacientes. Quimioterapia foi administrada em 12 pacientes e radioterapia em 2. Dos 13 pacientes 5 estão vivos em seguimento médio de 48 meses após o término do tratamento. Conclusão: A análise dos 13 pacientes com PNET e revisão da literatura demonstram a agressividade desse tumor. Devido a raridade dessa patologia, estudos multiinstitucionais, podem ter papel importante para análise de fatores prognósticos e consequente abordagem terapêutica.INCA2000-09-29info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionRevisão de literaturaapplication/pdfhttps://rbc.inca.gov.br/index.php/revista/article/view/244010.32635/2176-9745.RBC.2000v46n3.2440Revista Brasileira de Cancerologia; Vol. 46 No. 3 (2000): July/Aug./Sept.; 293-98Revista Brasileira de Cancerologia; Vol. 46 Núm. 3 (2000): jul./ago./sept.; 293-98Revista Brasileira de Cancerologia; v. 46 n. 3 (2000): jul./ago./set.; 293-982176-9745reponame:Revista Brasileira de Cancerologia (Online)instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)instacron:INCAporhttps://rbc.inca.gov.br/index.php/revista/article/view/2440/1519https://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessCosta, Cecília M. L. Rondinelli, Patricia Camargo, Beatriz de 2023-01-18T18:19:57Zoai:rbc.inca.gov.br:article/2440Revistahttps://rbc.inca.gov.br/index.php/revistaPUBhttps://rbc.inca.gov.br/index.php/revista/oairbc@inca.gov.br0034-71162176-9745opendoar:2023-01-18T18:19:57Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)false
dc.title.none.fl_str_mv Primitive Neuroectodermic Tumor in Childwood: a Report of 13 Cases and Literature Review
Tumor Neuroectodérmico Primitivo na Infância: Relato de 13 Casos e Revisão da Literatura
title Primitive Neuroectodermic Tumor in Childwood: a Report of 13 Cases and Literature Review
spellingShingle Primitive Neuroectodermic Tumor in Childwood: a Report of 13 Cases and Literature Review
Costa, Cecília M. L.
Tumor Neuroectodérmico Primitivo
Sarcoma
Neoplasias de Tecidos Moles
Primitive Neuroectodermic Tumor
Sarcoma
Soft Tissue Neoplasms
title_short Primitive Neuroectodermic Tumor in Childwood: a Report of 13 Cases and Literature Review
title_full Primitive Neuroectodermic Tumor in Childwood: a Report of 13 Cases and Literature Review
title_fullStr Primitive Neuroectodermic Tumor in Childwood: a Report of 13 Cases and Literature Review
title_full_unstemmed Primitive Neuroectodermic Tumor in Childwood: a Report of 13 Cases and Literature Review
title_sort Primitive Neuroectodermic Tumor in Childwood: a Report of 13 Cases and Literature Review
author Costa, Cecília M. L.
author_facet Costa, Cecília M. L.
Rondinelli, Patricia
Camargo, Beatriz de
author_role author
author2 Rondinelli, Patricia
Camargo, Beatriz de
author2_role author
author
dc.contributor.author.fl_str_mv Costa, Cecília M. L.
Rondinelli, Patricia
Camargo, Beatriz de
dc.subject.por.fl_str_mv Tumor Neuroectodérmico Primitivo
Sarcoma
Neoplasias de Tecidos Moles
Primitive Neuroectodermic Tumor
Sarcoma
Soft Tissue Neoplasms
topic Tumor Neuroectodérmico Primitivo
Sarcoma
Neoplasias de Tecidos Moles
Primitive Neuroectodermic Tumor
Sarcoma
Soft Tissue Neoplasms
description Proposal: The autors review the chart of 13 patients with diagnosis of peripheral primitive neuroectodermal tumor (PNET), admitted at the Pediatric Department of Cancer Hospital between the period of 1989 and 1996. Patients and methods: All patients with PNET were analysed in a retrospective way, using epidemiologic clinical data, treatment and outcome. Results: Surgery was the first therapeutic approach in 2 patients. Chemotherapy was administered in 12 patient and radiotherapy in 2. From the 13 patient, five are alive with an average follow up of 48 months after the end of the treatment. Conclusion: This analyis confirms the heterogeneity and agressiveness of PNET tumors. Multicentric studies are necessary for prognostic factors analysis.
publishDate 2000
dc.date.none.fl_str_mv 2000-09-29
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
Revisão de literatura
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://rbc.inca.gov.br/index.php/revista/article/view/2440
10.32635/2176-9745.RBC.2000v46n3.2440
url https://rbc.inca.gov.br/index.php/revista/article/view/2440
identifier_str_mv 10.32635/2176-9745.RBC.2000v46n3.2440
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://rbc.inca.gov.br/index.php/revista/article/view/2440/1519
dc.rights.driver.fl_str_mv https://creativecommons.org/licenses/by/4.0
info:eu-repo/semantics/openAccess
rights_invalid_str_mv https://creativecommons.org/licenses/by/4.0
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv INCA
publisher.none.fl_str_mv INCA
dc.source.none.fl_str_mv Revista Brasileira de Cancerologia; Vol. 46 No. 3 (2000): July/Aug./Sept.; 293-98
Revista Brasileira de Cancerologia; Vol. 46 Núm. 3 (2000): jul./ago./sept.; 293-98
Revista Brasileira de Cancerologia; v. 46 n. 3 (2000): jul./ago./set.; 293-98
2176-9745
reponame:Revista Brasileira de Cancerologia (Online)
instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
instacron:INCA
instname_str Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
instacron_str INCA
institution INCA
reponame_str Revista Brasileira de Cancerologia (Online)
collection Revista Brasileira de Cancerologia (Online)
repository.name.fl_str_mv Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
repository.mail.fl_str_mv rbc@inca.gov.br
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