High grade bifasic synovial sarcoma of the lung

Detalhes bibliográficos
Autor(a) principal: Bezerra Junior, Marcos Luiz
Data de Publicação: 2003
Outros Autores: Costa, Erick Santarem da, Nascimento, Marilene F do, Mendes, Gelcio L Quintela, Cavalcanti, Aureliano, Pinel, Maria Izabel Sathler
Tipo de documento: Artigo
Idioma: por
Título da fonte: Revista Brasileira de Cancerologia (Online)
Texto Completo: https://rbc.inca.gov.br/index.php/revista/article/view/2097
Resumo: Synovial sarcoma is a malignant soft tissue neoplasm that occurs more often in young adults, affecting mainly the great joints. Primary lung sarcomas are extremely rare. Among the most common are leimyosarcoma, fibrosarcoma and haemangiopericytoma. The diagnosis of primary synovial is hampered because the difficulty between diagnosis of a primary and metastatic lesions. The translocation t(x;18) (p11;q11) is characteristic of synovial sarcomas and have been used mainly in the diagnosis of the monofasic type. The immunohistochemical and ultrastructural features are considered to be useful in diagnosing it too. The present report addresses a primary lung bifasic synovial sarcoma, confirmed by immunohistochemistry. The pacient was submited to surgery, radiation therapy and chemotherapy. Despite all the efforts she developed distant metastatic lesions and died.
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spelling High grade bifasic synovial sarcoma of the lungSarcoma sinovial bifásico de alto grau primário de pulmãoSarcoma SinovialNeoplasias PulmonaresImunohistoquímicaCitogenéticaSynovial SarcomaLung NeoplasmsImmunohistochemistryCytogeneticsSynovial sarcoma is a malignant soft tissue neoplasm that occurs more often in young adults, affecting mainly the great joints. Primary lung sarcomas are extremely rare. Among the most common are leimyosarcoma, fibrosarcoma and haemangiopericytoma. The diagnosis of primary synovial is hampered because the difficulty between diagnosis of a primary and metastatic lesions. The translocation t(x;18) (p11;q11) is characteristic of synovial sarcomas and have been used mainly in the diagnosis of the monofasic type. The immunohistochemical and ultrastructural features are considered to be useful in diagnosing it too. The present report addresses a primary lung bifasic synovial sarcoma, confirmed by immunohistochemistry. The pacient was submited to surgery, radiation therapy and chemotherapy. Despite all the efforts she developed distant metastatic lesions and died.O sarcoma sinovial é uma neoplasia maligna de partes moles que ocorre com mais freqüência em adultos jovens, localizando-se nas extremidades, próximo às grandes articulações. Sarcomas primários do pulmão são extremamente raros. Entre os tipos mais comuns que ocorrem nesta localização estão o leiomiossarcoma, fibrossarcoma e o hemangiopericitoma. O diagnóstico do sarcoma sinovial é dificultado justamente por essa baixa ocorrência e devido à semelhança de achados histológicos e morfológicos entre lesões primárias e metastáticas. A pesquisa citogenética da translocação t(x;18) (p11;q11) tem um papel mais importante nos casos de tumores monofásicos devido ao seu padrão de crescimento semelhante a de outros sarcomas assim como a análise imunohistoquimica e de ultraestrutura que também são exames que auxiliam o diagnóstico. Relatamos o caso de um sarcoma inovial bifásico, primário de pulmão confirmado por análise imuno-histoquímica compatível com padrões descritos em literatura e que foi abordado com cirurgia, radioterapia conformacional e quimioterapia, evoluindo ao óbito, com doença local e à distância.INCA2003-09-30info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionRelato de Casoapplication/pdfhttps://rbc.inca.gov.br/index.php/revista/article/view/209710.32635/2176-9745.RBC.2003v49n3.2097Revista Brasileira de Cancerologia; Vol. 49 No. 3 (2003): July/Aug./Sept.; 175-178Revista Brasileira de Cancerologia; Vol. 49 Núm. 3 (2003): jul./ago./sept.; 175-178Revista Brasileira de Cancerologia; v. 49 n. 3 (2003): jul./ago./set.; 175-1782176-9745reponame:Revista Brasileira de Cancerologia (Online)instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)instacron:INCAporhttps://rbc.inca.gov.br/index.php/revista/article/view/2097/1301Bezerra Junior, Marcos Luiz Costa, Erick Santarem da Nascimento, Marilene F do Mendes, Gelcio L Quintela Cavalcanti, Aureliano Pinel, Maria Izabel Sathler info:eu-repo/semantics/openAccess2021-11-29T20:35:10Zoai:rbc.inca.gov.br:article/2097Revistahttps://rbc.inca.gov.br/index.php/revistaPUBhttps://rbc.inca.gov.br/index.php/revista/oairbc@inca.gov.br0034-71162176-9745opendoar:2021-11-29T20:35:10Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)false
dc.title.none.fl_str_mv High grade bifasic synovial sarcoma of the lung
Sarcoma sinovial bifásico de alto grau primário de pulmão
title High grade bifasic synovial sarcoma of the lung
spellingShingle High grade bifasic synovial sarcoma of the lung
Bezerra Junior, Marcos Luiz
Sarcoma Sinovial
Neoplasias Pulmonares
Imunohistoquímica
Citogenética
Synovial Sarcoma
Lung Neoplasms
Immunohistochemistry
Cytogenetics
title_short High grade bifasic synovial sarcoma of the lung
title_full High grade bifasic synovial sarcoma of the lung
title_fullStr High grade bifasic synovial sarcoma of the lung
title_full_unstemmed High grade bifasic synovial sarcoma of the lung
title_sort High grade bifasic synovial sarcoma of the lung
author Bezerra Junior, Marcos Luiz
author_facet Bezerra Junior, Marcos Luiz
Costa, Erick Santarem da
Nascimento, Marilene F do
Mendes, Gelcio L Quintela
Cavalcanti, Aureliano
Pinel, Maria Izabel Sathler
author_role author
author2 Costa, Erick Santarem da
Nascimento, Marilene F do
Mendes, Gelcio L Quintela
Cavalcanti, Aureliano
Pinel, Maria Izabel Sathler
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Bezerra Junior, Marcos Luiz
Costa, Erick Santarem da
Nascimento, Marilene F do
Mendes, Gelcio L Quintela
Cavalcanti, Aureliano
Pinel, Maria Izabel Sathler
dc.subject.por.fl_str_mv Sarcoma Sinovial
Neoplasias Pulmonares
Imunohistoquímica
Citogenética
Synovial Sarcoma
Lung Neoplasms
Immunohistochemistry
Cytogenetics
topic Sarcoma Sinovial
Neoplasias Pulmonares
Imunohistoquímica
Citogenética
Synovial Sarcoma
Lung Neoplasms
Immunohistochemistry
Cytogenetics
description Synovial sarcoma is a malignant soft tissue neoplasm that occurs more often in young adults, affecting mainly the great joints. Primary lung sarcomas are extremely rare. Among the most common are leimyosarcoma, fibrosarcoma and haemangiopericytoma. The diagnosis of primary synovial is hampered because the difficulty between diagnosis of a primary and metastatic lesions. The translocation t(x;18) (p11;q11) is characteristic of synovial sarcomas and have been used mainly in the diagnosis of the monofasic type. The immunohistochemical and ultrastructural features are considered to be useful in diagnosing it too. The present report addresses a primary lung bifasic synovial sarcoma, confirmed by immunohistochemistry. The pacient was submited to surgery, radiation therapy and chemotherapy. Despite all the efforts she developed distant metastatic lesions and died.
publishDate 2003
dc.date.none.fl_str_mv 2003-09-30
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
Relato de Caso
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://rbc.inca.gov.br/index.php/revista/article/view/2097
10.32635/2176-9745.RBC.2003v49n3.2097
url https://rbc.inca.gov.br/index.php/revista/article/view/2097
identifier_str_mv 10.32635/2176-9745.RBC.2003v49n3.2097
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://rbc.inca.gov.br/index.php/revista/article/view/2097/1301
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv INCA
publisher.none.fl_str_mv INCA
dc.source.none.fl_str_mv Revista Brasileira de Cancerologia; Vol. 49 No. 3 (2003): July/Aug./Sept.; 175-178
Revista Brasileira de Cancerologia; Vol. 49 Núm. 3 (2003): jul./ago./sept.; 175-178
Revista Brasileira de Cancerologia; v. 49 n. 3 (2003): jul./ago./set.; 175-178
2176-9745
reponame:Revista Brasileira de Cancerologia (Online)
instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
instacron:INCA
instname_str Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
instacron_str INCA
institution INCA
reponame_str Revista Brasileira de Cancerologia (Online)
collection Revista Brasileira de Cancerologia (Online)
repository.name.fl_str_mv Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
repository.mail.fl_str_mv rbc@inca.gov.br
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