MONOPHASIC SYNOVIAL SARCOMA

• Autor(a) principal: Mendonça, Gabriel Soares
• Data de Publicação: 2015
• Outros Autores: Artiles, Camilla Burla, Freitas, Ney Artiles, Mendonça, Sandro Bichara
• Tipo de documento: Artigo
• Idioma: por
• Título da fonte: Revista Científica da Faculdade de Medicina de Campos
• Texto Completo: https://www.fmc.br/ojs/index.php/RCFMC/article/view/30
• topic: Sarcomas Sinoviais; Sarcoma Sinovial; Monofásico; Tumores de Partes Moles; synovial sarcoma; monophasic synovial; sarcoma; soft-tissue tumors

Synovial Sarcomas (SS) correspond to rare malignancies; represent between 5-10% of soft tissue sarcomas. More prevalent in males (1.2/ 1.0), between 15 and 40 years. Arise from multipotent mesenchymal cells; usually progressing to slow growth; most common in the extremities, especially the legs. There are four histological subtypes described: biphasic, monophasic fibrous, monophasic epithelial and poorly differentiated. The most pathologists consider the SS as a disease of high grade. The five-year survival rate is between 30 and 74%5 . Objective: To describe a case of synovial sarcoma-phase at the elbow joint. Method: We report the case of a patient 48 years old, male, black, married, high school education, farm laborer, residing in Campos-RJ, complaining of increased volume in the left elbow joint, diagnosed by biopsy and study histopathological / immunohistochemical as carrier Monophasic Synovial Sarcoma. Result: Ten months ago, the patient developed increased joint volume in left elbow, evolving with progressive growth of the lesion, the irregular appearance, firm and elastic, with the presence of local inflammatory signs, measuring approximately 12.0 x 12.0 cm on initial clinical evaluation. Study was performed by MRI, punch biopsy histopathology and immunohistochemistry. Conclusion: The Synovial sarcomas are classified as rare malignancies derived from multipotent mesenchymal cells, whose diagnosis requires histopathologic study, MRI, and treatment as early as possible, routinely characterized by resection surgery associated with chemotherapy or radiotherapy