Multisystemic Sarcoidosis with Early Gastrointestinal Symptoms
Autor(a) principal: | |
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Data de Publicação: | 2017 |
Outros Autores: | , , , |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | http://scielo.pt/scielo.php?script=sci_arttext&pid=S2341-45452017000300007 |
Resumo: | Sarcoidosis involving the digestive tract is very rare and requires a strict differential diagnosis with other systemic granulomatous diseases. We present a case of multisystemic granulomatosis involving the stomach and colon, causing initial digestive symptoms. Pulmonary nodules, pleural effusion, ascites, hepatomegaly, splenomegaly, and mesenteric as well as retroperitoneal and axillary lymphadenopathy were subsequently identified. The reticulo-endothelial expression, the hypercalcemia and, above all, a rapid and complete resolution after corticosteroids supported the hypothesis of sarcoidosis involving the digestive tract. A brief review of digestive tract involvement in sarcoidosis and of the distinctive features of sarcoidosis with gastrointestinal involvement and Crohns disease with a rare form of pleuropulmonary involvement is presented. |
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Multisystemic Sarcoidosis with Early Gastrointestinal SymptomsCrohns diseaseGastrointestinal diseasesSarcoidosis/complicationsSarcoidosis involving the digestive tract is very rare and requires a strict differential diagnosis with other systemic granulomatous diseases. We present a case of multisystemic granulomatosis involving the stomach and colon, causing initial digestive symptoms. Pulmonary nodules, pleural effusion, ascites, hepatomegaly, splenomegaly, and mesenteric as well as retroperitoneal and axillary lymphadenopathy were subsequently identified. The reticulo-endothelial expression, the hypercalcemia and, above all, a rapid and complete resolution after corticosteroids supported the hypothesis of sarcoidosis involving the digestive tract. A brief review of digestive tract involvement in sarcoidosis and of the distinctive features of sarcoidosis with gastrointestinal involvement and Crohns disease with a rare form of pleuropulmonary involvement is presented.Sociedade Portuguesa de Gastrenterologia2017-06-01info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/reporttext/htmlhttp://scielo.pt/scielo.php?script=sci_arttext&pid=S2341-45452017000300007GE-Portuguese Journal of Gastroenterology v.24 n.3 2017reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPenghttp://scielo.pt/scielo.php?script=sci_arttext&pid=S2341-45452017000300007Mota,CatarinaFerreira,CarlosOliveira,Maria EmíliaSantos,João MenesesVictorino,Rui M.M.info:eu-repo/semantics/openAccess2024-02-06T17:33:45Zoai:scielo:S2341-45452017000300007Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-20T02:36:00.489530Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
Multisystemic Sarcoidosis with Early Gastrointestinal Symptoms |
title |
Multisystemic Sarcoidosis with Early Gastrointestinal Symptoms |
spellingShingle |
Multisystemic Sarcoidosis with Early Gastrointestinal Symptoms Mota,Catarina Crohns disease Gastrointestinal diseases Sarcoidosis/complications |
title_short |
Multisystemic Sarcoidosis with Early Gastrointestinal Symptoms |
title_full |
Multisystemic Sarcoidosis with Early Gastrointestinal Symptoms |
title_fullStr |
Multisystemic Sarcoidosis with Early Gastrointestinal Symptoms |
title_full_unstemmed |
Multisystemic Sarcoidosis with Early Gastrointestinal Symptoms |
title_sort |
Multisystemic Sarcoidosis with Early Gastrointestinal Symptoms |
author |
Mota,Catarina |
author_facet |
Mota,Catarina Ferreira,Carlos Oliveira,Maria Emília Santos,João Meneses Victorino,Rui M.M. |
author_role |
author |
author2 |
Ferreira,Carlos Oliveira,Maria Emília Santos,João Meneses Victorino,Rui M.M. |
author2_role |
author author author author |
dc.contributor.author.fl_str_mv |
Mota,Catarina Ferreira,Carlos Oliveira,Maria Emília Santos,João Meneses Victorino,Rui M.M. |
dc.subject.por.fl_str_mv |
Crohns disease Gastrointestinal diseases Sarcoidosis/complications |
topic |
Crohns disease Gastrointestinal diseases Sarcoidosis/complications |
description |
Sarcoidosis involving the digestive tract is very rare and requires a strict differential diagnosis with other systemic granulomatous diseases. We present a case of multisystemic granulomatosis involving the stomach and colon, causing initial digestive symptoms. Pulmonary nodules, pleural effusion, ascites, hepatomegaly, splenomegaly, and mesenteric as well as retroperitoneal and axillary lymphadenopathy were subsequently identified. The reticulo-endothelial expression, the hypercalcemia and, above all, a rapid and complete resolution after corticosteroids supported the hypothesis of sarcoidosis involving the digestive tract. A brief review of digestive tract involvement in sarcoidosis and of the distinctive features of sarcoidosis with gastrointestinal involvement and Crohns disease with a rare form of pleuropulmonary involvement is presented. |
publishDate |
2017 |
dc.date.none.fl_str_mv |
2017-06-01 |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://scielo.pt/scielo.php?script=sci_arttext&pid=S2341-45452017000300007 |
url |
http://scielo.pt/scielo.php?script=sci_arttext&pid=S2341-45452017000300007 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
http://scielo.pt/scielo.php?script=sci_arttext&pid=S2341-45452017000300007 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade Portuguesa de Gastrenterologia |
publisher.none.fl_str_mv |
Sociedade Portuguesa de Gastrenterologia |
dc.source.none.fl_str_mv |
GE-Portuguese Journal of Gastroenterology v.24 n.3 2017 reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
instname_str |
Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
instacron_str |
RCAAP |
institution |
RCAAP |
reponame_str |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
collection |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
repository.name.fl_str_mv |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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1799137412355457024 |