POROKERATOSIS OF MIBELLI – A CASE REPORT

Detalhes bibliográficos
Autor(a) principal: Laureano, André
Data de Publicação: 2013
Outros Autores: Macias, Vasco Coelho, Pacheco, Fernando Assis
Tipo de documento: Artigo
Idioma: por
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: https://doi.org/10.29021/spdv.70.2.28
Resumo: Porokeratosis are the result of a clonal proliferation of keratinocytes. About six clinical variants were des- cribed to date, sharing the histological feature of cornoid lamella in the stratum corneum. The authors report a porokeratosis of Mibelli in a 27-year-old black female appearing in childhood successfully treated with a topical retinoid. Common manifestations of a rare dermatosis are presented with emphasis to the role of histo- pathology in the diagnosis. Porokeratosis of Mibelli is a chronic and progressive dermatosis, rarely with spontaneous remission. Malignant degeneration has been described with a reported incidence of 7%, with highest malignant trans- formation into squamous cell carcinoma, therefore the importance of regular skin checks.KEYWORDS – Porokeratosis; Keratinocytes.
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spelling POROKERATOSIS OF MIBELLI – A CASE REPORTPOROQUERATOSE DE MIBELLI – UM CASO CLÍNICOPorokeratosis are the result of a clonal proliferation of keratinocytes. About six clinical variants were des- cribed to date, sharing the histological feature of cornoid lamella in the stratum corneum. The authors report a porokeratosis of Mibelli in a 27-year-old black female appearing in childhood successfully treated with a topical retinoid. Common manifestations of a rare dermatosis are presented with emphasis to the role of histo- pathology in the diagnosis. Porokeratosis of Mibelli is a chronic and progressive dermatosis, rarely with spontaneous remission. Malignant degeneration has been described with a reported incidence of 7%, with highest malignant trans- formation into squamous cell carcinoma, therefore the importance of regular skin checks.KEYWORDS – Porokeratosis; Keratinocytes.As poroqueratoses resultam de uma hiper-proliferação clonal dos queratinócitos, encontrando-se pelo menos descritas seis formas clínicas, que partilham o achado da lamela cornóide no exame histopatológico. Os autores descrevem o caso de uma poroqueratose de Mibelli numa mulher de 27 anos, raça negra, com início na infância, eficazmente tratada com retinóide tópico, apresentando-se as manifestações típicas de uma dermatose pou- co frequente e destacando-se a importância da histopatologia na confirmação do seu diagnóstico. A poroqueratose de Mibelli é uma dermatose crónica e progressiva, raramente com remissão espontânea. A sua evolução para neo- plasia maligna, particularmente carcinoma espino-celular, pode ocorrer em cerca de 7% dos doentes, reforçando-se a importância de uma adequada vigilância.PALAVRAS-CHAVE – Poroqueratoses; Poroqueratose de Mibelli; Queratinócitos.Sociedade Portuguesa de Dermatologia e Venereologia2013-01-17T00:00:00Zjournal articleinfo:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://doi.org/10.29021/spdv.70.2.28oai:ojs.revista.spdv.com.pt:article/28Journal of the Portuguese Society of Dermatology and Venereology; Vol 70 No 2 (2012): Abril - Junho; 209Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 70 n. 2 (2012): Abril - Junho; 2092182-24092182-2395reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPporhttps://revista.spdv.com.pt/index.php/spdv/article/view/28https://doi.org/10.29021/spdv.70.2.28https://revista.spdv.com.pt/index.php/spdv/article/view/28/28Laureano, AndréMacias, Vasco CoelhoPacheco, Fernando Assisinfo:eu-repo/semantics/openAccess2022-10-06T12:34:36Zoai:ojs.revista.spdv.com.pt:article/28Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T16:10:38.019703Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv POROKERATOSIS OF MIBELLI – A CASE REPORT
POROQUERATOSE DE MIBELLI – UM CASO CLÍNICO
title POROKERATOSIS OF MIBELLI – A CASE REPORT
spellingShingle POROKERATOSIS OF MIBELLI – A CASE REPORT
Laureano, André
title_short POROKERATOSIS OF MIBELLI – A CASE REPORT
title_full POROKERATOSIS OF MIBELLI – A CASE REPORT
title_fullStr POROKERATOSIS OF MIBELLI – A CASE REPORT
title_full_unstemmed POROKERATOSIS OF MIBELLI – A CASE REPORT
title_sort POROKERATOSIS OF MIBELLI – A CASE REPORT
author Laureano, André
author_facet Laureano, André
Macias, Vasco Coelho
Pacheco, Fernando Assis
author_role author
author2 Macias, Vasco Coelho
Pacheco, Fernando Assis
author2_role author
author
dc.contributor.author.fl_str_mv Laureano, André
Macias, Vasco Coelho
Pacheco, Fernando Assis
description Porokeratosis are the result of a clonal proliferation of keratinocytes. About six clinical variants were des- cribed to date, sharing the histological feature of cornoid lamella in the stratum corneum. The authors report a porokeratosis of Mibelli in a 27-year-old black female appearing in childhood successfully treated with a topical retinoid. Common manifestations of a rare dermatosis are presented with emphasis to the role of histo- pathology in the diagnosis. Porokeratosis of Mibelli is a chronic and progressive dermatosis, rarely with spontaneous remission. Malignant degeneration has been described with a reported incidence of 7%, with highest malignant trans- formation into squamous cell carcinoma, therefore the importance of regular skin checks.KEYWORDS – Porokeratosis; Keratinocytes.
publishDate 2013
dc.date.none.fl_str_mv 2013-01-17T00:00:00Z
dc.type.driver.fl_str_mv journal article
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dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
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status_str publishedVersion
dc.identifier.uri.fl_str_mv https://doi.org/10.29021/spdv.70.2.28
oai:ojs.revista.spdv.com.pt:article/28
url https://doi.org/10.29021/spdv.70.2.28
identifier_str_mv oai:ojs.revista.spdv.com.pt:article/28
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://revista.spdv.com.pt/index.php/spdv/article/view/28
https://doi.org/10.29021/spdv.70.2.28
https://revista.spdv.com.pt/index.php/spdv/article/view/28/28
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
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dc.publisher.none.fl_str_mv Sociedade Portuguesa de Dermatologia e Venereologia
publisher.none.fl_str_mv Sociedade Portuguesa de Dermatologia e Venereologia
dc.source.none.fl_str_mv Journal of the Portuguese Society of Dermatology and Venereology; Vol 70 No 2 (2012): Abril - Junho; 209
Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 70 n. 2 (2012): Abril - Junho; 209
2182-2409
2182-2395
reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
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instacron:RCAAP
instname_str Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
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reponame_str Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
collection Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
repository.name.fl_str_mv Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
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