An atypical presentation of Ormond’s disease

Detalhes bibliográficos
Autor(a) principal: Carvão,João
Data de Publicação: 2021
Outros Autores: Vida,Carlota, Resende,Luís, Silva,Francisca, Silva,Gil
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: http://scielo.pt/scielo.php?script=sci_arttext&pid=S0872-01692021000400251
Resumo: ABSTRACT Retroperitoneal fibrosis is a rare condition defined by an overproduction of fibro-inflammatory tissue in the retroperitoneum, usually involving the abdominal aorta, but also managing to invade adjacent structures. We report a case of a 47-year-old female patient with an atypical radiological presentation of retroperitoneal fibrosis, involving predominantly the right kidney. Ultimately, the diagnosis was performed by an immunohistochemical study that identified IgG4+ plasmocytes after kidney nephrectomy, also known as Ormond’s disease. There are no universal guidelines for the treatment of retroperitoneal fibrosis, due to its rarity and lack of randomized controlled trials comparing different therapeutic strategies.
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spelling An atypical presentation of Ormond’s diseaseOrmond’s diseaseRetroperitoneal fibrosisEnd-stage kidney diseaseABSTRACT Retroperitoneal fibrosis is a rare condition defined by an overproduction of fibro-inflammatory tissue in the retroperitoneum, usually involving the abdominal aorta, but also managing to invade adjacent structures. We report a case of a 47-year-old female patient with an atypical radiological presentation of retroperitoneal fibrosis, involving predominantly the right kidney. Ultimately, the diagnosis was performed by an immunohistochemical study that identified IgG4+ plasmocytes after kidney nephrectomy, also known as Ormond’s disease. There are no universal guidelines for the treatment of retroperitoneal fibrosis, due to its rarity and lack of randomized controlled trials comparing different therapeutic strategies.Sociedade Portuguesa de Nefrologia2021-12-01info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/reporttext/htmlhttp://scielo.pt/scielo.php?script=sci_arttext&pid=S0872-01692021000400251Portuguese Journal of Nephrology & Hypertension v.35 n.4 2021reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPenghttp://scielo.pt/scielo.php?script=sci_arttext&pid=S0872-01692021000400251Carvão,JoãoVida,CarlotaResende,LuísSilva,FranciscaSilva,Gilinfo:eu-repo/semantics/openAccess2024-02-06T17:05:12Zoai:scielo:S0872-01692021000400251Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-20T02:19:06.810434Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv An atypical presentation of Ormond’s disease
title An atypical presentation of Ormond’s disease
spellingShingle An atypical presentation of Ormond’s disease
Carvão,João
Ormond’s disease
Retroperitoneal fibrosis
End-stage kidney disease
title_short An atypical presentation of Ormond’s disease
title_full An atypical presentation of Ormond’s disease
title_fullStr An atypical presentation of Ormond’s disease
title_full_unstemmed An atypical presentation of Ormond’s disease
title_sort An atypical presentation of Ormond’s disease
author Carvão,João
author_facet Carvão,João
Vida,Carlota
Resende,Luís
Silva,Francisca
Silva,Gil
author_role author
author2 Vida,Carlota
Resende,Luís
Silva,Francisca
Silva,Gil
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Carvão,João
Vida,Carlota
Resende,Luís
Silva,Francisca
Silva,Gil
dc.subject.por.fl_str_mv Ormond’s disease
Retroperitoneal fibrosis
End-stage kidney disease
topic Ormond’s disease
Retroperitoneal fibrosis
End-stage kidney disease
description ABSTRACT Retroperitoneal fibrosis is a rare condition defined by an overproduction of fibro-inflammatory tissue in the retroperitoneum, usually involving the abdominal aorta, but also managing to invade adjacent structures. We report a case of a 47-year-old female patient with an atypical radiological presentation of retroperitoneal fibrosis, involving predominantly the right kidney. Ultimately, the diagnosis was performed by an immunohistochemical study that identified IgG4+ plasmocytes after kidney nephrectomy, also known as Ormond’s disease. There are no universal guidelines for the treatment of retroperitoneal fibrosis, due to its rarity and lack of randomized controlled trials comparing different therapeutic strategies.
publishDate 2021
dc.date.none.fl_str_mv 2021-12-01
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
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status_str publishedVersion
dc.identifier.uri.fl_str_mv http://scielo.pt/scielo.php?script=sci_arttext&pid=S0872-01692021000400251
url http://scielo.pt/scielo.php?script=sci_arttext&pid=S0872-01692021000400251
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv http://scielo.pt/scielo.php?script=sci_arttext&pid=S0872-01692021000400251
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
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dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Portuguesa de Nefrologia
publisher.none.fl_str_mv Sociedade Portuguesa de Nefrologia
dc.source.none.fl_str_mv Portuguese Journal of Nephrology & Hypertension v.35 n.4 2021
reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron:RCAAP
instname_str Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron_str RCAAP
institution RCAAP
reponame_str Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
collection Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
repository.name.fl_str_mv Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
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