Paracoccidioidomycosis in an Elderly Simulating Cholangiocarcinoma
Autor(a) principal: | |
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Data de Publicação: | 2021 |
Outros Autores: | , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | https://doi.org/10.29021/spdv.79.3.1364 |
Resumo: | Paracoccidioidomycosis, the most prevalent deep mycosis in Latin America, is caused by dimorphic species of the genus Paracoccidioides, affects predominantly male rural workers between 30-50 years of age and is an important cause of morbidity and mortality. It can present in two clinical forms: acute/subacute or chronic. In rare cases paracoccidioidomycosis may simulate neoplasia and must be considered as a differential diagnosis of intra-abdominal tumors in endemic areas. We report an exuberant case of subacute paracoccidioidomycosis in an elderly lady, although it is more frequent in the juvenile form. Multiple facial skin lesions were associated with a wasting syndrome and extensive adenopathy including in the hepatic area, causing bile duct dilatation simulating a cholangiocarcinoma. Skin histopathology was diagnostic and antifungal treatment allowed complete resolution of cutaneous and systemic lesions, thus highlighting the merit of the dermatologist, who was fundamental for the conclusive diagnosis and institution of specific therapy, resulting in a favorable outcome. |
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Paracoccidioidomycosis in an Elderly Simulating CholangiocarcinomaParacoccidioidomicose em Idosa Simulando ColangiocarcinomaCholangiocarcinomaParacoccidioidomycosisColangiocarcinomaParacoccidioidomicoseParacoccidioidomycosis, the most prevalent deep mycosis in Latin America, is caused by dimorphic species of the genus Paracoccidioides, affects predominantly male rural workers between 30-50 years of age and is an important cause of morbidity and mortality. It can present in two clinical forms: acute/subacute or chronic. In rare cases paracoccidioidomycosis may simulate neoplasia and must be considered as a differential diagnosis of intra-abdominal tumors in endemic areas. We report an exuberant case of subacute paracoccidioidomycosis in an elderly lady, although it is more frequent in the juvenile form. Multiple facial skin lesions were associated with a wasting syndrome and extensive adenopathy including in the hepatic area, causing bile duct dilatation simulating a cholangiocarcinoma. Skin histopathology was diagnostic and antifungal treatment allowed complete resolution of cutaneous and systemic lesions, thus highlighting the merit of the dermatologist, who was fundamental for the conclusive diagnosis and institution of specific therapy, resulting in a favorable outcome.Paracoccidioidomicose, micose profunda mais prevalente na América Latina, causada por fungos dimórficos do género Paracoccidioides, afeta predominantemente homens trabalhadores rurais entre 30 e 50 anos de idade e é uma importante causa de morbimortalidade. Pode se apresentar de duas formas: aguda/subaguda ou crónica. Em raros casos, a paracoccidioidomicose pode simular neoplasia e deve ser considerada como diagnóstico diferencial de tumor intra-abdominal nas áreas endémicas. Reportamos um caso exuberante de paracoccidioidomicose subaguda em uma mulher idosa, embora essa apresentação seja mais frequente na forma juvenil. Múltiplas lesões cutâneas na face estavam associadas à síndrome consumptiva e extensas adenopatias incluindo região hepática, causando dilatação do ducto biliar e simulando um colangiocarcinoma. A histopatologia da pele foi diagnóstica e o tratamento antifúngico permitiu a completa resolução das lesões cutâneas e sistémicas, o que enaltece o mérito do dermatologista, que foi fundamental para o diagnóstico conclusivo e instituição de terapia específica, resultando em desfecho favorável.Sociedade Portuguesa de Dermatologia e Venereologia2021-10-17T00:00:00Zjournal articleinfo:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://doi.org/10.29021/spdv.79.3.1364oai:ojs.revista.spdv.com.pt:article/1364Journal of the Portuguese Society of Dermatology and Venereology; Vol 79 No 3 (2021): July - September; 273-277Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 79 n. 3 (2021): Julho - Setembro; 273-2772182-24092182-2395reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPenghttps://revista.spdv.com.pt/index.php/spdv/article/view/1364https://doi.org/10.29021/spdv.79.3.1364https://revista.spdv.com.pt/index.php/spdv/article/view/1364/924Copyright (c) 2021 Journal of the Portuguese Society of Dermatology and Venereologyhttps://creativecommons.org/licenses/by-nc/4.0info:eu-repo/semantics/openAccessGuerra, IsabelL. P. Simões, HisabellaF. Valle, AnnairC. M. N. Castañon, Maria2022-10-06T12:35:19Zoai:ojs.revista.spdv.com.pt:article/1364Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T16:11:20.421841Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
Paracoccidioidomycosis in an Elderly Simulating Cholangiocarcinoma Paracoccidioidomicose em Idosa Simulando Colangiocarcinoma |
title |
Paracoccidioidomycosis in an Elderly Simulating Cholangiocarcinoma |
spellingShingle |
Paracoccidioidomycosis in an Elderly Simulating Cholangiocarcinoma Guerra, Isabel Cholangiocarcinoma Paracoccidioidomycosis Colangiocarcinoma Paracoccidioidomicose |
title_short |
Paracoccidioidomycosis in an Elderly Simulating Cholangiocarcinoma |
title_full |
Paracoccidioidomycosis in an Elderly Simulating Cholangiocarcinoma |
title_fullStr |
Paracoccidioidomycosis in an Elderly Simulating Cholangiocarcinoma |
title_full_unstemmed |
Paracoccidioidomycosis in an Elderly Simulating Cholangiocarcinoma |
title_sort |
Paracoccidioidomycosis in an Elderly Simulating Cholangiocarcinoma |
author |
Guerra, Isabel |
author_facet |
Guerra, Isabel L. P. Simões, Hisabella F. Valle, Annair C. M. N. Castañon, Maria |
author_role |
author |
author2 |
L. P. Simões, Hisabella F. Valle, Annair C. M. N. Castañon, Maria |
author2_role |
author author author |
dc.contributor.author.fl_str_mv |
Guerra, Isabel L. P. Simões, Hisabella F. Valle, Annair C. M. N. Castañon, Maria |
dc.subject.por.fl_str_mv |
Cholangiocarcinoma Paracoccidioidomycosis Colangiocarcinoma Paracoccidioidomicose |
topic |
Cholangiocarcinoma Paracoccidioidomycosis Colangiocarcinoma Paracoccidioidomicose |
description |
Paracoccidioidomycosis, the most prevalent deep mycosis in Latin America, is caused by dimorphic species of the genus Paracoccidioides, affects predominantly male rural workers between 30-50 years of age and is an important cause of morbidity and mortality. It can present in two clinical forms: acute/subacute or chronic. In rare cases paracoccidioidomycosis may simulate neoplasia and must be considered as a differential diagnosis of intra-abdominal tumors in endemic areas. We report an exuberant case of subacute paracoccidioidomycosis in an elderly lady, although it is more frequent in the juvenile form. Multiple facial skin lesions were associated with a wasting syndrome and extensive adenopathy including in the hepatic area, causing bile duct dilatation simulating a cholangiocarcinoma. Skin histopathology was diagnostic and antifungal treatment allowed complete resolution of cutaneous and systemic lesions, thus highlighting the merit of the dermatologist, who was fundamental for the conclusive diagnosis and institution of specific therapy, resulting in a favorable outcome. |
publishDate |
2021 |
dc.date.none.fl_str_mv |
2021-10-17T00:00:00Z |
dc.type.driver.fl_str_mv |
journal article info:eu-repo/semantics/article |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://doi.org/10.29021/spdv.79.3.1364 oai:ojs.revista.spdv.com.pt:article/1364 |
url |
https://doi.org/10.29021/spdv.79.3.1364 |
identifier_str_mv |
oai:ojs.revista.spdv.com.pt:article/1364 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
https://revista.spdv.com.pt/index.php/spdv/article/view/1364 https://doi.org/10.29021/spdv.79.3.1364 https://revista.spdv.com.pt/index.php/spdv/article/view/1364/924 |
dc.rights.driver.fl_str_mv |
Copyright (c) 2021 Journal of the Portuguese Society of Dermatology and Venereology https://creativecommons.org/licenses/by-nc/4.0 info:eu-repo/semantics/openAccess |
rights_invalid_str_mv |
Copyright (c) 2021 Journal of the Portuguese Society of Dermatology and Venereology https://creativecommons.org/licenses/by-nc/4.0 |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Sociedade Portuguesa de Dermatologia e Venereologia |
publisher.none.fl_str_mv |
Sociedade Portuguesa de Dermatologia e Venereologia |
dc.source.none.fl_str_mv |
Journal of the Portuguese Society of Dermatology and Venereology; Vol 79 No 3 (2021): July - September; 273-277 Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 79 n. 3 (2021): Julho - Setembro; 273-277 2182-2409 2182-2395 reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
instname_str |
Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
instacron_str |
RCAAP |
institution |
RCAAP |
reponame_str |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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