PREVENTION MEASURES IN PATIENTS WITH MASTOCYTOSIS – PROTOCOL
Autor(a) principal: | |
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Data de Publicação: | 2011 |
Outros Autores: | |
Tipo de documento: | Artigo |
Idioma: | por |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | https://doi.org/10.29021/spdv.69.2.604 |
Resumo: | Mastocytosis comprises a group of rare disorders with diverse clinical presentations, characterized by an abnormal increase number of mast cells in various organs. All patients with mastocytosis are at risk for anaphylaxis due to excessive mast cell mediator release that can occur during anesthesia, administration of radiographic contrast media or after hymenoptera stings. Beside the symptomatic treatment of acute and chronic mast cell-mediator release, and the reduction of the local or systemic mast cell burden, a rational management approach in mastocytosis must include a careful counseling of patients (parents in pediatric cases) and care providers, and avoidance of factors triggering acute mediator release. This protocol forms a pratical guideline for the management of patients with mastocytosis. It includes global preventive measures and measures in specific contexts: local and general anesthesia, administration of radiographic contrast media, and hymenoptera stings. As there are many anaphylaxis triggers in patients with mastocytosis, it is important to have a protocol with guidelines for physicians who are involved in these patients care. |
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PREVENTION MEASURES IN PATIENTS WITH MASTOCYTOSIS – PROTOCOLMEDIDAS DE PREVENÇÃO EM DOENTES COM MASTOCITOSE – PROTOCOLOMastocytosisAnaphylaxisAnesthesiaRadiographic contrast mediaHymenoptera stingsMastocitoseAnafilaxiaAnestesiaMeios radiológicos de contrastePicadas de himenópterosMastocytosis comprises a group of rare disorders with diverse clinical presentations, characterized by an abnormal increase number of mast cells in various organs. All patients with mastocytosis are at risk for anaphylaxis due to excessive mast cell mediator release that can occur during anesthesia, administration of radiographic contrast media or after hymenoptera stings. Beside the symptomatic treatment of acute and chronic mast cell-mediator release, and the reduction of the local or systemic mast cell burden, a rational management approach in mastocytosis must include a careful counseling of patients (parents in pediatric cases) and care providers, and avoidance of factors triggering acute mediator release. This protocol forms a pratical guideline for the management of patients with mastocytosis. It includes global preventive measures and measures in specific contexts: local and general anesthesia, administration of radiographic contrast media, and hymenoptera stings. As there are many anaphylaxis triggers in patients with mastocytosis, it is important to have a protocol with guidelines for physicians who are involved in these patients care.As mastocitoses são um grupo de doenças raras com diversas apresentações clínicas, caracterizadas por um aumento do número de mastócitos presentes num ou mais órgãos. Todos os doentes com mastocitose estão em risco de desenvolver episódios de anafilaxia, devido à libertação excessiva de mediadores mastocitários, que podem ocorrer em múltiplas situações, tais como administração de anestesia ou de meios de contraste radiológico ou após picadas de insectos. Além do tratamento sintomático da libertação aguda ou crónica dos mediadores mastocitários e da redução da massa mastocitária total, a terapêutica destes doentes deve incluir: aconselhamento dos doentes (pais nos casos pediátricos) e prestadores de cuidados de saúde e evicção de potenciais factores desencadeantes de libertação de mediadores mastocitários. O protocolo proposto inclui medidas gerais preventivas, assim como medidas de prevenção em contextos específicos: anestesia local e geral, realização de exames radiológicos com contraste e picadas de insectos. Existindo diversos agentes capazes de provocar reacções anafilácticas nos doentes com mastocitose, é importante a existência de um protocolo com guidelines para os profissionais de saúde envolvidos na prestação de cuidados a estes doentes.Sociedade Portuguesa de Dermatologia e Venereologia2011-06-23T00:00:00Zjournal articleinfo:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://doi.org/10.29021/spdv.69.2.604oai:ojs.revista.spdv.com.pt:article/604Journal of the Portuguese Society of Dermatology and Venereology; Vol 69 No 2 (2011): Abril / Junho; 189-194Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 69 n. 2 (2011): Abril / Junho; 189-1942182-24092182-2395reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPporhttps://revista.spdv.com.pt/index.php/spdv/article/view/604https://doi.org/10.29021/spdv.69.2.604https://revista.spdv.com.pt/index.php/spdv/article/view/604/426Devesa Parente, JoanaSilva, Maria Joãoinfo:eu-repo/semantics/openAccess2022-10-06T12:34:58Zoai:ojs.revista.spdv.com.pt:article/604Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T16:10:57.967928Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
PREVENTION MEASURES IN PATIENTS WITH MASTOCYTOSIS – PROTOCOL MEDIDAS DE PREVENÇÃO EM DOENTES COM MASTOCITOSE – PROTOCOLO |
title |
PREVENTION MEASURES IN PATIENTS WITH MASTOCYTOSIS – PROTOCOL |
spellingShingle |
PREVENTION MEASURES IN PATIENTS WITH MASTOCYTOSIS – PROTOCOL Devesa Parente, Joana Mastocytosis Anaphylaxis Anesthesia Radiographic contrast media Hymenoptera stings Mastocitose Anafilaxia Anestesia Meios radiológicos de contraste Picadas de himenópteros |
title_short |
PREVENTION MEASURES IN PATIENTS WITH MASTOCYTOSIS – PROTOCOL |
title_full |
PREVENTION MEASURES IN PATIENTS WITH MASTOCYTOSIS – PROTOCOL |
title_fullStr |
PREVENTION MEASURES IN PATIENTS WITH MASTOCYTOSIS – PROTOCOL |
title_full_unstemmed |
PREVENTION MEASURES IN PATIENTS WITH MASTOCYTOSIS – PROTOCOL |
title_sort |
PREVENTION MEASURES IN PATIENTS WITH MASTOCYTOSIS – PROTOCOL |
author |
Devesa Parente, Joana |
author_facet |
Devesa Parente, Joana Silva, Maria João |
author_role |
author |
author2 |
Silva, Maria João |
author2_role |
author |
dc.contributor.author.fl_str_mv |
Devesa Parente, Joana Silva, Maria João |
dc.subject.por.fl_str_mv |
Mastocytosis Anaphylaxis Anesthesia Radiographic contrast media Hymenoptera stings Mastocitose Anafilaxia Anestesia Meios radiológicos de contraste Picadas de himenópteros |
topic |
Mastocytosis Anaphylaxis Anesthesia Radiographic contrast media Hymenoptera stings Mastocitose Anafilaxia Anestesia Meios radiológicos de contraste Picadas de himenópteros |
description |
Mastocytosis comprises a group of rare disorders with diverse clinical presentations, characterized by an abnormal increase number of mast cells in various organs. All patients with mastocytosis are at risk for anaphylaxis due to excessive mast cell mediator release that can occur during anesthesia, administration of radiographic contrast media or after hymenoptera stings. Beside the symptomatic treatment of acute and chronic mast cell-mediator release, and the reduction of the local or systemic mast cell burden, a rational management approach in mastocytosis must include a careful counseling of patients (parents in pediatric cases) and care providers, and avoidance of factors triggering acute mediator release. This protocol forms a pratical guideline for the management of patients with mastocytosis. It includes global preventive measures and measures in specific contexts: local and general anesthesia, administration of radiographic contrast media, and hymenoptera stings. As there are many anaphylaxis triggers in patients with mastocytosis, it is important to have a protocol with guidelines for physicians who are involved in these patients care. |
publishDate |
2011 |
dc.date.none.fl_str_mv |
2011-06-23T00:00:00Z |
dc.type.driver.fl_str_mv |
journal article info:eu-repo/semantics/article |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://doi.org/10.29021/spdv.69.2.604 oai:ojs.revista.spdv.com.pt:article/604 |
url |
https://doi.org/10.29021/spdv.69.2.604 |
identifier_str_mv |
oai:ojs.revista.spdv.com.pt:article/604 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
https://revista.spdv.com.pt/index.php/spdv/article/view/604 https://doi.org/10.29021/spdv.69.2.604 https://revista.spdv.com.pt/index.php/spdv/article/view/604/426 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Sociedade Portuguesa de Dermatologia e Venereologia |
publisher.none.fl_str_mv |
Sociedade Portuguesa de Dermatologia e Venereologia |
dc.source.none.fl_str_mv |
Journal of the Portuguese Society of Dermatology and Venereology; Vol 69 No 2 (2011): Abril / Junho; 189-194 Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 69 n. 2 (2011): Abril / Junho; 189-194 2182-2409 2182-2395 reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
instname_str |
Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
instacron_str |
RCAAP |
institution |
RCAAP |
reponame_str |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
collection |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
repository.name.fl_str_mv |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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