Congenital chylothorax: A series of eight cases
Autor(a) principal: | |
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Data de Publicação: | 2023 |
Outros Autores: | , , , , , , , , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | https://doi.org/10.25753/BirthGrowthMJ.v32.i3.25442 |
Resumo: | Introduction: Congenital chylothorax (CC) is the accumulation of lymph in the pleural space. The aim of this study was to review the cases of CC diagnosed in newborns admitted to a level III neonatal intensive care unit between January 2014 and December 2020. Results: Eight cases of CC were identified, all with prenatal diagnosis. After postnatal confirmation of the diagnosis, supportive care and conservative therapy were initiated. Six cases underwent mechanical ventilation, two were treated with surfactant and inhaled nitric oxide, four required inotropic support, and one underwent extracorporeal membrane oxygenation. Five newborns were effectively treated with octreotide. One patient with hydrops fetalis died after birth. Discussion: The prognosis of CC depends on the severity of the effusion and on associated abnormalities. Medical treatment is based on supportive and conservative treatment. Although the use of octreotide is not unanimous, it proved to be an effective and safe adjuvant therapy in these patients. |
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Congenital chylothorax: A series of eight casesQuilotórax congénito: Uma série de oito casosCase ReportsIntroduction: Congenital chylothorax (CC) is the accumulation of lymph in the pleural space. The aim of this study was to review the cases of CC diagnosed in newborns admitted to a level III neonatal intensive care unit between January 2014 and December 2020. Results: Eight cases of CC were identified, all with prenatal diagnosis. After postnatal confirmation of the diagnosis, supportive care and conservative therapy were initiated. Six cases underwent mechanical ventilation, two were treated with surfactant and inhaled nitric oxide, four required inotropic support, and one underwent extracorporeal membrane oxygenation. Five newborns were effectively treated with octreotide. One patient with hydrops fetalis died after birth. Discussion: The prognosis of CC depends on the severity of the effusion and on associated abnormalities. Medical treatment is based on supportive and conservative treatment. Although the use of octreotide is not unanimous, it proved to be an effective and safe adjuvant therapy in these patients.Introdução: O quilotórax congénito consiste na acumulação de linfa no espaço pleural. O objetivo deste estudo foi analisar os casos de recém-nascidos com diagnóstico de quilotórax congénito admitidos numa unidade de cuidados intensivos neonatais de nível III entre janeiro de 2014 e dezembro de 2020. Resultados: Foram identificados oito casos de quilotórax congénito, todos com diagnóstico pré-natal. Após confirmação pós-natal do diagnóstico, foi iniciado tratamento de suporte e conservador. Seis casos foram submetidos a ventilação mecânica invasiva, dois foram tratados com surfactante e óxido nítrico inalado, quatro tiveram necessidade de suporte inotrópico e um recebeu oxigenação por membrana extracorporal. Cinco casos foram efetivamente tratados com octreótido. Um recém-nascido com hidrópsia fetal faleceu após o nascimento. Discussão: O prognóstico do quilotórax congénito depende da gravidade do derrame pleural e das anomalias associadas. O tratamento inicial deve ser de suporte e conservador. Embora a utilização de octreótido não seja consensual, demonstrou ser uma terapêutica efetiva e segura nesta amostra de doentes.Centro Hospitalar Universitário de Santo António2023-11-16info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articlehttps://doi.org/10.25753/BirthGrowthMJ.v32.i3.25442eng2183-9417Jorge Antunes, JoanaBorges, MadalenaMascarenhas, AndreiaBrito, SaraIglesias, CéliaFernandes, EduardoVieira, EunicePinto, FilomenaFerreira, LeonorTomé, TeresaNona, Joséinfo:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2023-11-16T17:28:48Zoai:ojs.revistas.rcaap.pt:article/25442Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T22:53:51.688014Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
Congenital chylothorax: A series of eight cases Quilotórax congénito: Uma série de oito casos |
title |
Congenital chylothorax: A series of eight cases |
spellingShingle |
Congenital chylothorax: A series of eight cases Jorge Antunes, Joana Case Reports |
title_short |
Congenital chylothorax: A series of eight cases |
title_full |
Congenital chylothorax: A series of eight cases |
title_fullStr |
Congenital chylothorax: A series of eight cases |
title_full_unstemmed |
Congenital chylothorax: A series of eight cases |
title_sort |
Congenital chylothorax: A series of eight cases |
author |
Jorge Antunes, Joana |
author_facet |
Jorge Antunes, Joana Borges, Madalena Mascarenhas, Andreia Brito, Sara Iglesias, Célia Fernandes, Eduardo Vieira, Eunice Pinto, Filomena Ferreira, Leonor Tomé, Teresa Nona, José |
author_role |
author |
author2 |
Borges, Madalena Mascarenhas, Andreia Brito, Sara Iglesias, Célia Fernandes, Eduardo Vieira, Eunice Pinto, Filomena Ferreira, Leonor Tomé, Teresa Nona, José |
author2_role |
author author author author author author author author author author |
dc.contributor.author.fl_str_mv |
Jorge Antunes, Joana Borges, Madalena Mascarenhas, Andreia Brito, Sara Iglesias, Célia Fernandes, Eduardo Vieira, Eunice Pinto, Filomena Ferreira, Leonor Tomé, Teresa Nona, José |
dc.subject.por.fl_str_mv |
Case Reports |
topic |
Case Reports |
description |
Introduction: Congenital chylothorax (CC) is the accumulation of lymph in the pleural space. The aim of this study was to review the cases of CC diagnosed in newborns admitted to a level III neonatal intensive care unit between January 2014 and December 2020. Results: Eight cases of CC were identified, all with prenatal diagnosis. After postnatal confirmation of the diagnosis, supportive care and conservative therapy were initiated. Six cases underwent mechanical ventilation, two were treated with surfactant and inhaled nitric oxide, four required inotropic support, and one underwent extracorporeal membrane oxygenation. Five newborns were effectively treated with octreotide. One patient with hydrops fetalis died after birth. Discussion: The prognosis of CC depends on the severity of the effusion and on associated abnormalities. Medical treatment is based on supportive and conservative treatment. Although the use of octreotide is not unanimous, it proved to be an effective and safe adjuvant therapy in these patients. |
publishDate |
2023 |
dc.date.none.fl_str_mv |
2023-11-16 |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://doi.org/10.25753/BirthGrowthMJ.v32.i3.25442 |
url |
https://doi.org/10.25753/BirthGrowthMJ.v32.i3.25442 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
2183-9417 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.publisher.none.fl_str_mv |
Centro Hospitalar Universitário de Santo António |
publisher.none.fl_str_mv |
Centro Hospitalar Universitário de Santo António |
dc.source.none.fl_str_mv |
reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
instname_str |
Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
instacron_str |
RCAAP |
institution |
RCAAP |
reponame_str |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
collection |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
repository.name.fl_str_mv |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
repository.mail.fl_str_mv |
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1799135136409714688 |