Left Lung and Pulmonary Artery Hypoplasia: A Rare Case of Hemoptysis
Autor(a) principal: | |
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Data de Publicação: | 2020 |
Outros Autores: | , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | http://hdl.handle.net/10400.16/2599 |
Resumo: | Pulmonary hypoplasia or agenesis is a rare congenital disorder that results in lung underdevelopment. This disease is usually found in children but rarely encountered in adults. We describe the case of an 84-year-old woman diagnosed with a unilateral pulmonary hypoplasia presenting simultaneously with left pulmonary artery hypoplasia. Due to this condition, the patient had a lifelong history of pulmonary infections that resulted in several bronchiectases in the affected lung. Moreover, the pulmonary artery hypoplasia led to the development of pulmonary hypertension and collateral circulation causing hemoptysis, giving rise to the patient attending the emergency department. Although we were able to medically manage the hemoptysis, it can be fatal and require surgical intervention. Hence, an early diagnosis is essential so that appropriate follow-up and prompt prevention and treatment of complications, such as pulmonary infections, hemoptysis and pulmonary hypertension, are achieved. Learning points: Although rare and typically associated with childhood, lung and pulmonary artery hypoplasia can in exceptional cases be present in adult life.The diagnosis of lung and pulmonary artery hypoplasia is challenging in adults as they can easily be mistaken for more common diseases.Symptoms and complications may be life-threatening, including dyspnea, hemoptysis, recurrent pulmonary infections and pulmonary hypertension.An early diagnosis is extremely important because it allows a close follow-up with consequent timely detection and treatment of serious complications, especially pulmonary hypertension. |
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Left Lung and Pulmonary Artery Hypoplasia: A Rare Case of HemoptysisRadiologycongenital disordershemoptysislung hypoplasiapulmonary artery agenesispulmonary artery hypoplasiarespiratory medicinePulmonary hypoplasia or agenesis is a rare congenital disorder that results in lung underdevelopment. This disease is usually found in children but rarely encountered in adults. We describe the case of an 84-year-old woman diagnosed with a unilateral pulmonary hypoplasia presenting simultaneously with left pulmonary artery hypoplasia. Due to this condition, the patient had a lifelong history of pulmonary infections that resulted in several bronchiectases in the affected lung. Moreover, the pulmonary artery hypoplasia led to the development of pulmonary hypertension and collateral circulation causing hemoptysis, giving rise to the patient attending the emergency department. Although we were able to medically manage the hemoptysis, it can be fatal and require surgical intervention. Hence, an early diagnosis is essential so that appropriate follow-up and prompt prevention and treatment of complications, such as pulmonary infections, hemoptysis and pulmonary hypertension, are achieved. Learning points: Although rare and typically associated with childhood, lung and pulmonary artery hypoplasia can in exceptional cases be present in adult life.The diagnosis of lung and pulmonary artery hypoplasia is challenging in adults as they can easily be mistaken for more common diseases.Symptoms and complications may be life-threatening, including dyspnea, hemoptysis, recurrent pulmonary infections and pulmonary hypertension.An early diagnosis is extremely important because it allows a close follow-up with consequent timely detection and treatment of serious complications, especially pulmonary hypertension.SMC MediaRepositório Científico do Centro Hospitalar Universitário de Santo AntónioPinheiro, Maria GuiomarAlves, Ana MargaridaNeves, IsabelSequeira, Teresa2021-11-22T15:23:17Z2020-04-302020-04-30T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttp://hdl.handle.net/10400.16/2599engPinheiro G, Alves AM, Rodrigues Neves I, Sequeira T. Left Lung and Pulmonary Artery Hypoplasia: A Rare Case of Hemoptysis. Eur J Case Rep Intern Med. 2020;7(7):001490. doi:10.12890/2020_0014902284-259410.12890/2020_001490info:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2023-10-20T11:01:14Zoai:repositorio.chporto.pt:10400.16/2599Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T20:38:47.825613Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
Left Lung and Pulmonary Artery Hypoplasia: A Rare Case of Hemoptysis |
title |
Left Lung and Pulmonary Artery Hypoplasia: A Rare Case of Hemoptysis |
spellingShingle |
Left Lung and Pulmonary Artery Hypoplasia: A Rare Case of Hemoptysis Pinheiro, Maria Guiomar Radiology congenital disorders hemoptysis lung hypoplasia pulmonary artery agenesis pulmonary artery hypoplasia respiratory medicine |
title_short |
Left Lung and Pulmonary Artery Hypoplasia: A Rare Case of Hemoptysis |
title_full |
Left Lung and Pulmonary Artery Hypoplasia: A Rare Case of Hemoptysis |
title_fullStr |
Left Lung and Pulmonary Artery Hypoplasia: A Rare Case of Hemoptysis |
title_full_unstemmed |
Left Lung and Pulmonary Artery Hypoplasia: A Rare Case of Hemoptysis |
title_sort |
Left Lung and Pulmonary Artery Hypoplasia: A Rare Case of Hemoptysis |
author |
Pinheiro, Maria Guiomar |
author_facet |
Pinheiro, Maria Guiomar Alves, Ana Margarida Neves, Isabel Sequeira, Teresa |
author_role |
author |
author2 |
Alves, Ana Margarida Neves, Isabel Sequeira, Teresa |
author2_role |
author author author |
dc.contributor.none.fl_str_mv |
Repositório Científico do Centro Hospitalar Universitário de Santo António |
dc.contributor.author.fl_str_mv |
Pinheiro, Maria Guiomar Alves, Ana Margarida Neves, Isabel Sequeira, Teresa |
dc.subject.por.fl_str_mv |
Radiology congenital disorders hemoptysis lung hypoplasia pulmonary artery agenesis pulmonary artery hypoplasia respiratory medicine |
topic |
Radiology congenital disorders hemoptysis lung hypoplasia pulmonary artery agenesis pulmonary artery hypoplasia respiratory medicine |
description |
Pulmonary hypoplasia or agenesis is a rare congenital disorder that results in lung underdevelopment. This disease is usually found in children but rarely encountered in adults. We describe the case of an 84-year-old woman diagnosed with a unilateral pulmonary hypoplasia presenting simultaneously with left pulmonary artery hypoplasia. Due to this condition, the patient had a lifelong history of pulmonary infections that resulted in several bronchiectases in the affected lung. Moreover, the pulmonary artery hypoplasia led to the development of pulmonary hypertension and collateral circulation causing hemoptysis, giving rise to the patient attending the emergency department. Although we were able to medically manage the hemoptysis, it can be fatal and require surgical intervention. Hence, an early diagnosis is essential so that appropriate follow-up and prompt prevention and treatment of complications, such as pulmonary infections, hemoptysis and pulmonary hypertension, are achieved. Learning points: Although rare and typically associated with childhood, lung and pulmonary artery hypoplasia can in exceptional cases be present in adult life.The diagnosis of lung and pulmonary artery hypoplasia is challenging in adults as they can easily be mistaken for more common diseases.Symptoms and complications may be life-threatening, including dyspnea, hemoptysis, recurrent pulmonary infections and pulmonary hypertension.An early diagnosis is extremely important because it allows a close follow-up with consequent timely detection and treatment of serious complications, especially pulmonary hypertension. |
publishDate |
2020 |
dc.date.none.fl_str_mv |
2020-04-30 2020-04-30T00:00:00Z 2021-11-22T15:23:17Z |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://hdl.handle.net/10400.16/2599 |
url |
http://hdl.handle.net/10400.16/2599 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
Pinheiro G, Alves AM, Rodrigues Neves I, Sequeira T. Left Lung and Pulmonary Artery Hypoplasia: A Rare Case of Hemoptysis. Eur J Case Rep Intern Med. 2020;7(7):001490. doi:10.12890/2020_001490 2284-2594 10.12890/2020_001490 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
SMC Media |
publisher.none.fl_str_mv |
SMC Media |
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reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
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Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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RCAAP |
institution |
RCAAP |
reponame_str |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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