Retroperitoneal desmoid tumor during pregnancy - case report

Detalhes bibliográficos
Autor(a) principal: Xavier,Marta
Data de Publicação: 2021
Outros Autores: Ferreira,Carla, Furtado,Antónia, Ramalho,Graça
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: http://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-58302021000400384
Resumo: Abstract Desmoid-type fibromatosis is a rare neoplastic tumor of fibroblastic proliferation that arises from muscle, fascia or aponeurotic complexes. Although usually benign, it is capable of significant local morbidity resulting from infiltration of surrounding structures. The etiology of desmoid-type fibromatosis is multifactorial since genetic, endocrine, and physical factors play an important role in its pathogenesis. Prognosis is mainly related to the anatomical site. We report a case of an intra-abdominal desmoid-type fibromatosis, arising from the retroperitoneum, diagnosed at 15 weeks of gestation and resected during pregnancy. This case demonstrates de diagnostic and management challenge posed by an abdominal mass during pregnancy.
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spelling Retroperitoneal desmoid tumor during pregnancy - case reportDesmoidPregnancyCase report.Abstract Desmoid-type fibromatosis is a rare neoplastic tumor of fibroblastic proliferation that arises from muscle, fascia or aponeurotic complexes. Although usually benign, it is capable of significant local morbidity resulting from infiltration of surrounding structures. The etiology of desmoid-type fibromatosis is multifactorial since genetic, endocrine, and physical factors play an important role in its pathogenesis. Prognosis is mainly related to the anatomical site. We report a case of an intra-abdominal desmoid-type fibromatosis, arising from the retroperitoneum, diagnosed at 15 weeks of gestation and resected during pregnancy. This case demonstrates de diagnostic and management challenge posed by an abdominal mass during pregnancy.Euromédice, Edições Médicas Lda.2021-12-01info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/reporttext/htmlhttp://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-58302021000400384Acta Obstétrica e Ginecológica Portuguesa v.15 n.4 2021reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPenghttp://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-58302021000400384Xavier,MartaFerreira,CarlaFurtado,AntóniaRamalho,Graçainfo:eu-repo/semantics/openAccess2024-02-06T17:21:55Zoai:scielo:S1646-58302021000400384Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-20T02:28:46.043323Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv Retroperitoneal desmoid tumor during pregnancy - case report
title Retroperitoneal desmoid tumor during pregnancy - case report
spellingShingle Retroperitoneal desmoid tumor during pregnancy - case report
Xavier,Marta
Desmoid
Pregnancy
Case report.
title_short Retroperitoneal desmoid tumor during pregnancy - case report
title_full Retroperitoneal desmoid tumor during pregnancy - case report
title_fullStr Retroperitoneal desmoid tumor during pregnancy - case report
title_full_unstemmed Retroperitoneal desmoid tumor during pregnancy - case report
title_sort Retroperitoneal desmoid tumor during pregnancy - case report
author Xavier,Marta
author_facet Xavier,Marta
Ferreira,Carla
Furtado,Antónia
Ramalho,Graça
author_role author
author2 Ferreira,Carla
Furtado,Antónia
Ramalho,Graça
author2_role author
author
author
dc.contributor.author.fl_str_mv Xavier,Marta
Ferreira,Carla
Furtado,Antónia
Ramalho,Graça
dc.subject.por.fl_str_mv Desmoid
Pregnancy
Case report.
topic Desmoid
Pregnancy
Case report.
description Abstract Desmoid-type fibromatosis is a rare neoplastic tumor of fibroblastic proliferation that arises from muscle, fascia or aponeurotic complexes. Although usually benign, it is capable of significant local morbidity resulting from infiltration of surrounding structures. The etiology of desmoid-type fibromatosis is multifactorial since genetic, endocrine, and physical factors play an important role in its pathogenesis. Prognosis is mainly related to the anatomical site. We report a case of an intra-abdominal desmoid-type fibromatosis, arising from the retroperitoneum, diagnosed at 15 weeks of gestation and resected during pregnancy. This case demonstrates de diagnostic and management challenge posed by an abdominal mass during pregnancy.
publishDate 2021
dc.date.none.fl_str_mv 2021-12-01
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dc.publisher.none.fl_str_mv Euromédice, Edições Médicas Lda.
publisher.none.fl_str_mv Euromédice, Edições Médicas Lda.
dc.source.none.fl_str_mv Acta Obstétrica e Ginecológica Portuguesa v.15 n.4 2021
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