Anesthesia for surgical repair of the pentalogy of Cantrell: case report

• Autor(a) principal: Costa,Jorge Victor da Silva
• Data de Publicação: 2019
• Outros Autores: Melonio,Carlos Eduardo Coimbra, Vieira,Ciro Bezerra, Oliveira,Caio Marcio Barros de, Leal,Plínio da Cunha, Servín,Elizabeth Teixeira Noguera, Gomes,Lyvia Maria Rodrigues de Sousa, Moura,Ed Carlos Rey
• Tipo de documento: Relatório
• Idioma: eng
• Título da fonte: Revista Brasileira de Anestesiologia (Online)
• Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0034-70942019000300322
• topic: Pentalogy of Cantrell; Congenital malformation; Rare disease

Abstract Pentalogy of Cantrell is a congenital anomaly associated with defects in the abdominal wall, sternum, diaphragm, and diaphragmatic pericardium formation, in addition to the development of cardiac abnormalities. It is a rare disease with an estimated incidence of one case for every 65,000 births, being more common in males (60% of cases). It has a reserved prognosis with mortality around 63%, and a maximum of 9 months survival after surgery. There are few case reports addressing the pentalogy of Cantrell, which is justified by the rarity of this pathology. In this report our objective was to describe a surgical case of a female patient and make some anesthetic considerations about this rare congenital malformation.