Ectopia Cordis Associated with Pentalogy of Cantrell-A Case Report

Detalhes bibliográficos
Autor(a) principal: Madi,José Mauro
Data de Publicação: 2019
Outros Autores: Festugatto,José Roberto, Rizzon,Matheus, Agostini,Ana Paula, Araújo,Breno Fauth de, Garcia,Rosa Maria Rahmi
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Revista brasileira de ginecologia e obstetrícia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-72032019000500352
Resumo: Abstract Pentalogy of Cantrell (PC) is a rare congenital anomaly characterized by changes in the mesodermal median structures and congenital heart disease, often with a poor prognosis. In 1958, Cantrell et al2 defined the full spectrum of the syndrome with the following anomalies: defects of the anterior diaphragm, of the lower part of the sternum, of the supraumbilical region and the abdominal wall, of the diaphragmatic pericardium, and various intracardiac congenital abnormalities. The present report describes a case of ectopia cordis associated with PC and the importance of the participation of a multidisciplinary team in the treatment of this condition.
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spelling Ectopia Cordis Associated with Pentalogy of Cantrell-A Case Reportectopia cordispentalogy of Cantrellabdominal wall defectscongenital heart defectsumbilical herniaAbstract Pentalogy of Cantrell (PC) is a rare congenital anomaly characterized by changes in the mesodermal median structures and congenital heart disease, often with a poor prognosis. In 1958, Cantrell et al2 defined the full spectrum of the syndrome with the following anomalies: defects of the anterior diaphragm, of the lower part of the sternum, of the supraumbilical region and the abdominal wall, of the diaphragmatic pericardium, and various intracardiac congenital abnormalities. The present report describes a case of ectopia cordis associated with PC and the importance of the participation of a multidisciplinary team in the treatment of this condition.Federação Brasileira das Sociedades de Ginecologia e Obstetrícia2019-05-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-72032019000500352Revista Brasileira de Ginecologia e Obstetrícia v.41 n.5 2019reponame:Revista brasileira de ginecologia e obstetrícia (Online)instname:Federação Brasileira das Sociedades de Ginecologia e Obstetrícia (FEBRASGO)instacron:FEBRASGO10.1055/s-0039-1679878info:eu-repo/semantics/openAccessMadi,José MauroFestugatto,José RobertoRizzon,MatheusAgostini,Ana PaulaAraújo,Breno Fauth deGarcia,Rosa Maria Rahmieng2019-06-25T00:00:00Zoai:scielo:S0100-72032019000500352Revistahttp://www.scielo.br/rbgohttps://old.scielo.br/oai/scielo-oai.phppublicações@febrasgo.org.br||rbgo@fmrp.usp.br1806-93390100-7203opendoar:2019-06-25T00:00Revista brasileira de ginecologia e obstetrícia (Online) - Federação Brasileira das Sociedades de Ginecologia e Obstetrícia (FEBRASGO)false
dc.title.none.fl_str_mv Ectopia Cordis Associated with Pentalogy of Cantrell-A Case Report
title Ectopia Cordis Associated with Pentalogy of Cantrell-A Case Report
spellingShingle Ectopia Cordis Associated with Pentalogy of Cantrell-A Case Report
Madi,José Mauro
ectopia cordis
pentalogy of Cantrell
abdominal wall defects
congenital heart defects
umbilical hernia
title_short Ectopia Cordis Associated with Pentalogy of Cantrell-A Case Report
title_full Ectopia Cordis Associated with Pentalogy of Cantrell-A Case Report
title_fullStr Ectopia Cordis Associated with Pentalogy of Cantrell-A Case Report
title_full_unstemmed Ectopia Cordis Associated with Pentalogy of Cantrell-A Case Report
title_sort Ectopia Cordis Associated with Pentalogy of Cantrell-A Case Report
author Madi,José Mauro
author_facet Madi,José Mauro
Festugatto,José Roberto
Rizzon,Matheus
Agostini,Ana Paula
Araújo,Breno Fauth de
Garcia,Rosa Maria Rahmi
author_role author
author2 Festugatto,José Roberto
Rizzon,Matheus
Agostini,Ana Paula
Araújo,Breno Fauth de
Garcia,Rosa Maria Rahmi
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Madi,José Mauro
Festugatto,José Roberto
Rizzon,Matheus
Agostini,Ana Paula
Araújo,Breno Fauth de
Garcia,Rosa Maria Rahmi
dc.subject.por.fl_str_mv ectopia cordis
pentalogy of Cantrell
abdominal wall defects
congenital heart defects
umbilical hernia
topic ectopia cordis
pentalogy of Cantrell
abdominal wall defects
congenital heart defects
umbilical hernia
description Abstract Pentalogy of Cantrell (PC) is a rare congenital anomaly characterized by changes in the mesodermal median structures and congenital heart disease, often with a poor prognosis. In 1958, Cantrell et al2 defined the full spectrum of the syndrome with the following anomalies: defects of the anterior diaphragm, of the lower part of the sternum, of the supraumbilical region and the abdominal wall, of the diaphragmatic pericardium, and various intracardiac congenital abnormalities. The present report describes a case of ectopia cordis associated with PC and the importance of the participation of a multidisciplinary team in the treatment of this condition.
publishDate 2019
dc.date.none.fl_str_mv 2019-05-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-72032019000500352
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-72032019000500352
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1055/s-0039-1679878
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Federação Brasileira das Sociedades de Ginecologia e Obstetrícia
publisher.none.fl_str_mv Federação Brasileira das Sociedades de Ginecologia e Obstetrícia
dc.source.none.fl_str_mv Revista Brasileira de Ginecologia e Obstetrícia v.41 n.5 2019
reponame:Revista brasileira de ginecologia e obstetrícia (Online)
instname:Federação Brasileira das Sociedades de Ginecologia e Obstetrícia (FEBRASGO)
instacron:FEBRASGO
instname_str Federação Brasileira das Sociedades de Ginecologia e Obstetrícia (FEBRASGO)
instacron_str FEBRASGO
institution FEBRASGO
reponame_str Revista brasileira de ginecologia e obstetrícia (Online)
collection Revista brasileira de ginecologia e obstetrícia (Online)
repository.name.fl_str_mv Revista brasileira de ginecologia e obstetrícia (Online) - Federação Brasileira das Sociedades de Ginecologia e Obstetrícia (FEBRASGO)
repository.mail.fl_str_mv publicações@febrasgo.org.br||rbgo@fmrp.usp.br
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