Klippel-Trenaunay and Parkes-Weber syndromes: two case reports

Detalhes bibliográficos
Autor(a) principal: Chagas,Carlos Alberto Araujo
Data de Publicação: 2017
Outros Autores: Pires,Lucas Alves Sarmento, Babinski,Marcio Antonio, Leite,Tulio Fabiano de Oliveira
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Jornal Vascular Brasileiro (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1677-54492017000400320
Resumo: Abstract Parkes-Weber syndrome is a congenital vascular disease that comprises capillary, venous, lymphatic, and arteriovenous malformations. Although Parkes-Weber syndrome is a clinically distinct entity with serious complications, it is still frequently misdiagnosed as Klippel-Trenaunay syndrome, which consists of a triad of malformations involving the capillary, venous, and lymphatic vessels, without arteriovenous fistulas. Both syndromes are generally diagnosed with Doppler ultrasound and confirmed by magnetic resonance angiography. The aim of this study is to describe one case of Klippel-Trenaunay syndrome, in a 36-year-old patient, and one case of Parkes-Weber syndrome, in a 21-year-old patient. We review the literature in order to discuss the possible causes and consequences of these diseases related to venous hypertension and angiodysplasia, taking a clearer approach to their differences, and discussing their treatment.
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spelling Klippel-Trenaunay and Parkes-Weber syndromes: two case reportsKlippel-Trenaunay syndromeParkes-Weber syndromeangiodysplasianevusarteriovenous malformationsAbstract Parkes-Weber syndrome is a congenital vascular disease that comprises capillary, venous, lymphatic, and arteriovenous malformations. Although Parkes-Weber syndrome is a clinically distinct entity with serious complications, it is still frequently misdiagnosed as Klippel-Trenaunay syndrome, which consists of a triad of malformations involving the capillary, venous, and lymphatic vessels, without arteriovenous fistulas. Both syndromes are generally diagnosed with Doppler ultrasound and confirmed by magnetic resonance angiography. The aim of this study is to describe one case of Klippel-Trenaunay syndrome, in a 36-year-old patient, and one case of Parkes-Weber syndrome, in a 21-year-old patient. We review the literature in order to discuss the possible causes and consequences of these diseases related to venous hypertension and angiodysplasia, taking a clearer approach to their differences, and discussing their treatment.Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV)2017-12-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S1677-54492017000400320Jornal Vascular Brasileiro v.16 n.4 2017reponame:Jornal Vascular Brasileiro (Online)instname:Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV)instacron:SBACV10.1590/1677-5449.005417info:eu-repo/semantics/openAccessChagas,Carlos Alberto AraujoPires,Lucas Alves SarmentoBabinski,Marcio AntonioLeite,Tulio Fabiano de Oliveiraeng2018-02-08T00:00:00Zoai:scielo:S1677-54492017000400320Revistahttp://www.scielo.br/jvbhttps://old.scielo.br/oai/scielo-oai.php||secretaria@sbacv.org.br1677-73011677-5449opendoar:2018-02-08T00:00Jornal Vascular Brasileiro (Online) - Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV)false
dc.title.none.fl_str_mv Klippel-Trenaunay and Parkes-Weber syndromes: two case reports
title Klippel-Trenaunay and Parkes-Weber syndromes: two case reports
spellingShingle Klippel-Trenaunay and Parkes-Weber syndromes: two case reports
Chagas,Carlos Alberto Araujo
Klippel-Trenaunay syndrome
Parkes-Weber syndrome
angiodysplasia
nevus
arteriovenous malformations
title_short Klippel-Trenaunay and Parkes-Weber syndromes: two case reports
title_full Klippel-Trenaunay and Parkes-Weber syndromes: two case reports
title_fullStr Klippel-Trenaunay and Parkes-Weber syndromes: two case reports
title_full_unstemmed Klippel-Trenaunay and Parkes-Weber syndromes: two case reports
title_sort Klippel-Trenaunay and Parkes-Weber syndromes: two case reports
author Chagas,Carlos Alberto Araujo
author_facet Chagas,Carlos Alberto Araujo
Pires,Lucas Alves Sarmento
Babinski,Marcio Antonio
Leite,Tulio Fabiano de Oliveira
author_role author
author2 Pires,Lucas Alves Sarmento
Babinski,Marcio Antonio
Leite,Tulio Fabiano de Oliveira
author2_role author
author
author
dc.contributor.author.fl_str_mv Chagas,Carlos Alberto Araujo
Pires,Lucas Alves Sarmento
Babinski,Marcio Antonio
Leite,Tulio Fabiano de Oliveira
dc.subject.por.fl_str_mv Klippel-Trenaunay syndrome
Parkes-Weber syndrome
angiodysplasia
nevus
arteriovenous malformations
topic Klippel-Trenaunay syndrome
Parkes-Weber syndrome
angiodysplasia
nevus
arteriovenous malformations
description Abstract Parkes-Weber syndrome is a congenital vascular disease that comprises capillary, venous, lymphatic, and arteriovenous malformations. Although Parkes-Weber syndrome is a clinically distinct entity with serious complications, it is still frequently misdiagnosed as Klippel-Trenaunay syndrome, which consists of a triad of malformations involving the capillary, venous, and lymphatic vessels, without arteriovenous fistulas. Both syndromes are generally diagnosed with Doppler ultrasound and confirmed by magnetic resonance angiography. The aim of this study is to describe one case of Klippel-Trenaunay syndrome, in a 36-year-old patient, and one case of Parkes-Weber syndrome, in a 21-year-old patient. We review the literature in order to discuss the possible causes and consequences of these diseases related to venous hypertension and angiodysplasia, taking a clearer approach to their differences, and discussing their treatment.
publishDate 2017
dc.date.none.fl_str_mv 2017-12-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1677-54492017000400320
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1677-54492017000400320
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/1677-5449.005417
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV)
publisher.none.fl_str_mv Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV)
dc.source.none.fl_str_mv Jornal Vascular Brasileiro v.16 n.4 2017
reponame:Jornal Vascular Brasileiro (Online)
instname:Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV)
instacron:SBACV
instname_str Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV)
instacron_str SBACV
institution SBACV
reponame_str Jornal Vascular Brasileiro (Online)
collection Jornal Vascular Brasileiro (Online)
repository.name.fl_str_mv Jornal Vascular Brasileiro (Online) - Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV)
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