Klippel-Trenaunay and Parkes-Weber syndromes: two case reports
Autor(a) principal: | |
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Data de Publicação: | 2017 |
Outros Autores: | , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Jornal Vascular Brasileiro (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1677-54492017000400320 |
Resumo: | Abstract Parkes-Weber syndrome is a congenital vascular disease that comprises capillary, venous, lymphatic, and arteriovenous malformations. Although Parkes-Weber syndrome is a clinically distinct entity with serious complications, it is still frequently misdiagnosed as Klippel-Trenaunay syndrome, which consists of a triad of malformations involving the capillary, venous, and lymphatic vessels, without arteriovenous fistulas. Both syndromes are generally diagnosed with Doppler ultrasound and confirmed by magnetic resonance angiography. The aim of this study is to describe one case of Klippel-Trenaunay syndrome, in a 36-year-old patient, and one case of Parkes-Weber syndrome, in a 21-year-old patient. We review the literature in order to discuss the possible causes and consequences of these diseases related to venous hypertension and angiodysplasia, taking a clearer approach to their differences, and discussing their treatment. |
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Klippel-Trenaunay and Parkes-Weber syndromes: two case reportsKlippel-Trenaunay syndromeParkes-Weber syndromeangiodysplasianevusarteriovenous malformationsAbstract Parkes-Weber syndrome is a congenital vascular disease that comprises capillary, venous, lymphatic, and arteriovenous malformations. Although Parkes-Weber syndrome is a clinically distinct entity with serious complications, it is still frequently misdiagnosed as Klippel-Trenaunay syndrome, which consists of a triad of malformations involving the capillary, venous, and lymphatic vessels, without arteriovenous fistulas. Both syndromes are generally diagnosed with Doppler ultrasound and confirmed by magnetic resonance angiography. The aim of this study is to describe one case of Klippel-Trenaunay syndrome, in a 36-year-old patient, and one case of Parkes-Weber syndrome, in a 21-year-old patient. We review the literature in order to discuss the possible causes and consequences of these diseases related to venous hypertension and angiodysplasia, taking a clearer approach to their differences, and discussing their treatment.Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV)2017-12-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S1677-54492017000400320Jornal Vascular Brasileiro v.16 n.4 2017reponame:Jornal Vascular Brasileiro (Online)instname:Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV)instacron:SBACV10.1590/1677-5449.005417info:eu-repo/semantics/openAccessChagas,Carlos Alberto AraujoPires,Lucas Alves SarmentoBabinski,Marcio AntonioLeite,Tulio Fabiano de Oliveiraeng2018-02-08T00:00:00Zoai:scielo:S1677-54492017000400320Revistahttp://www.scielo.br/jvbhttps://old.scielo.br/oai/scielo-oai.php||secretaria@sbacv.org.br1677-73011677-5449opendoar:2018-02-08T00:00Jornal Vascular Brasileiro (Online) - Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV)false |
dc.title.none.fl_str_mv |
Klippel-Trenaunay and Parkes-Weber syndromes: two case reports |
title |
Klippel-Trenaunay and Parkes-Weber syndromes: two case reports |
spellingShingle |
Klippel-Trenaunay and Parkes-Weber syndromes: two case reports Chagas,Carlos Alberto Araujo Klippel-Trenaunay syndrome Parkes-Weber syndrome angiodysplasia nevus arteriovenous malformations |
title_short |
Klippel-Trenaunay and Parkes-Weber syndromes: two case reports |
title_full |
Klippel-Trenaunay and Parkes-Weber syndromes: two case reports |
title_fullStr |
Klippel-Trenaunay and Parkes-Weber syndromes: two case reports |
title_full_unstemmed |
Klippel-Trenaunay and Parkes-Weber syndromes: two case reports |
title_sort |
Klippel-Trenaunay and Parkes-Weber syndromes: two case reports |
author |
Chagas,Carlos Alberto Araujo |
author_facet |
Chagas,Carlos Alberto Araujo Pires,Lucas Alves Sarmento Babinski,Marcio Antonio Leite,Tulio Fabiano de Oliveira |
author_role |
author |
author2 |
Pires,Lucas Alves Sarmento Babinski,Marcio Antonio Leite,Tulio Fabiano de Oliveira |
author2_role |
author author author |
dc.contributor.author.fl_str_mv |
Chagas,Carlos Alberto Araujo Pires,Lucas Alves Sarmento Babinski,Marcio Antonio Leite,Tulio Fabiano de Oliveira |
dc.subject.por.fl_str_mv |
Klippel-Trenaunay syndrome Parkes-Weber syndrome angiodysplasia nevus arteriovenous malformations |
topic |
Klippel-Trenaunay syndrome Parkes-Weber syndrome angiodysplasia nevus arteriovenous malformations |
description |
Abstract Parkes-Weber syndrome is a congenital vascular disease that comprises capillary, venous, lymphatic, and arteriovenous malformations. Although Parkes-Weber syndrome is a clinically distinct entity with serious complications, it is still frequently misdiagnosed as Klippel-Trenaunay syndrome, which consists of a triad of malformations involving the capillary, venous, and lymphatic vessels, without arteriovenous fistulas. Both syndromes are generally diagnosed with Doppler ultrasound and confirmed by magnetic resonance angiography. The aim of this study is to describe one case of Klippel-Trenaunay syndrome, in a 36-year-old patient, and one case of Parkes-Weber syndrome, in a 21-year-old patient. We review the literature in order to discuss the possible causes and consequences of these diseases related to venous hypertension and angiodysplasia, taking a clearer approach to their differences, and discussing their treatment. |
publishDate |
2017 |
dc.date.none.fl_str_mv |
2017-12-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1677-54492017000400320 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1677-54492017000400320 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/1677-5449.005417 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV) |
publisher.none.fl_str_mv |
Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV) |
dc.source.none.fl_str_mv |
Jornal Vascular Brasileiro v.16 n.4 2017 reponame:Jornal Vascular Brasileiro (Online) instname:Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV) instacron:SBACV |
instname_str |
Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV) |
instacron_str |
SBACV |
institution |
SBACV |
reponame_str |
Jornal Vascular Brasileiro (Online) |
collection |
Jornal Vascular Brasileiro (Online) |
repository.name.fl_str_mv |
Jornal Vascular Brasileiro (Online) - Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV) |
repository.mail.fl_str_mv |
||secretaria@sbacv.org.br |
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1752126647749836800 |