Case for diagnosis

Detalhes bibliográficos
Autor(a) principal: Lima,Lourenço de Azevedo
Data de Publicação: 2014
Outros Autores: Haddad,Natacha de Carvalho Mello, Lima,Ricardo Barbosa, D'Acri,Antonio Macedo, Martins,Carlos José
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Anais brasileiros de dermatologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000300521
Resumo: Degos disease, also known as malignant atrophic papulosis, is a rare occlusive vasculopathy of unknown etiology characterized by infarcts in the dermis, gastrointestinal tract, central nervous system, and other organs. It is characterized by papules, which become umbilicated and evolve with a depressed porcelain-white central area, with an erythematous halo with telangiectasias. Histological findings include wedge-shaped dermoepidermal necrosis and blood vessel thrombosis. Approximately 50-60% of patients with systemic symptoms die within 2-3 years, most due to gastrointestinal perforation. We report a typical case, with lethal outcome, in a 45-year-old woman.
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spelling Case for diagnosisComplement C5Malignant atrophic papulosisVascular diseasesDegos disease, also known as malignant atrophic papulosis, is a rare occlusive vasculopathy of unknown etiology characterized by infarcts in the dermis, gastrointestinal tract, central nervous system, and other organs. It is characterized by papules, which become umbilicated and evolve with a depressed porcelain-white central area, with an erythematous halo with telangiectasias. Histological findings include wedge-shaped dermoepidermal necrosis and blood vessel thrombosis. Approximately 50-60% of patients with systemic symptoms die within 2-3 years, most due to gastrointestinal perforation. We report a typical case, with lethal outcome, in a 45-year-old woman.Sociedade Brasileira de Dermatologia2014-06-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000300521Anais Brasileiros de Dermatologia v.89 n.3 2014reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20142863info:eu-repo/semantics/openAccessLima,Lourenço de AzevedoHaddad,Natacha de Carvalho MelloLima,Ricardo BarbosaD'Acri,Antonio MacedoMartins,Carlos Joséeng2015-10-19T00:00:00Zoai:scielo:S0365-05962014000300521Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2015-10-19T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false
dc.title.none.fl_str_mv Case for diagnosis
title Case for diagnosis
spellingShingle Case for diagnosis
Lima,Lourenço de Azevedo
Complement C5
Malignant atrophic papulosis
Vascular diseases
title_short Case for diagnosis
title_full Case for diagnosis
title_fullStr Case for diagnosis
title_full_unstemmed Case for diagnosis
title_sort Case for diagnosis
author Lima,Lourenço de Azevedo
author_facet Lima,Lourenço de Azevedo
Haddad,Natacha de Carvalho Mello
Lima,Ricardo Barbosa
D'Acri,Antonio Macedo
Martins,Carlos José
author_role author
author2 Haddad,Natacha de Carvalho Mello
Lima,Ricardo Barbosa
D'Acri,Antonio Macedo
Martins,Carlos José
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Lima,Lourenço de Azevedo
Haddad,Natacha de Carvalho Mello
Lima,Ricardo Barbosa
D'Acri,Antonio Macedo
Martins,Carlos José
dc.subject.por.fl_str_mv Complement C5
Malignant atrophic papulosis
Vascular diseases
topic Complement C5
Malignant atrophic papulosis
Vascular diseases
description Degos disease, also known as malignant atrophic papulosis, is a rare occlusive vasculopathy of unknown etiology characterized by infarcts in the dermis, gastrointestinal tract, central nervous system, and other organs. It is characterized by papules, which become umbilicated and evolve with a depressed porcelain-white central area, with an erythematous halo with telangiectasias. Histological findings include wedge-shaped dermoepidermal necrosis and blood vessel thrombosis. Approximately 50-60% of patients with systemic symptoms die within 2-3 years, most due to gastrointestinal perforation. We report a typical case, with lethal outcome, in a 45-year-old woman.
publishDate 2014
dc.date.none.fl_str_mv 2014-06-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000300521
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000300521
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/abd1806-4841.20142863
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv Anais Brasileiros de Dermatologia v.89 n.3 2014
reponame:Anais brasileiros de dermatologia (Online)
instname:Sociedade Brasileira de Dermatologia (SBD)
instacron:SBD
instname_str Sociedade Brasileira de Dermatologia (SBD)
instacron_str SBD
institution SBD
reponame_str Anais brasileiros de dermatologia (Online)
collection Anais brasileiros de dermatologia (Online)
repository.name.fl_str_mv Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)
repository.mail.fl_str_mv abd@sbd.org.br||revista@sbd.org.br
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