Case for diagnosis

Detalhes bibliográficos
Autor(a) principal: Franco,Joanna Pimenta de Araujo
Data de Publicação: 2014
Outros Autores: Barbosa,Caroline Cruz, Fonseca,Bárbara Ferreira Saraiva da, Lima,Ricardo Barbosa, D'Acri,Antônio Macedo, Martins,Carlos José
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Anais brasileiros de dermatologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000200357
Resumo: Dermatofibrosarcoma protuberans is a fibrohistiocytic tumor of intermediate malignancy with aggressive localized growth, high recurrence rate, but low metastatic potential. It appears as a hardened plaque, with slow growth, upon which the development of nodules occurs. It predominates in the trunk and is unusual in acral locations. Histopathology reveals spindle cells with storiform pattern and cartwheel-like or whirlwind-like aspect. Immunohistochemistry shows positivity for CD34. The treatment is surgical. We report a case of long evolution, with an unusual location, that relapsed after surgery, to emphasize the importance of early diagnosis and proper treatment, avoiding aggressive resections with increased morbidity.
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spelling Case for diagnosisDermatofibrosarcomaExtremitiesSkin neoplasmsDermatofibrosarcoma protuberans is a fibrohistiocytic tumor of intermediate malignancy with aggressive localized growth, high recurrence rate, but low metastatic potential. It appears as a hardened plaque, with slow growth, upon which the development of nodules occurs. It predominates in the trunk and is unusual in acral locations. Histopathology reveals spindle cells with storiform pattern and cartwheel-like or whirlwind-like aspect. Immunohistochemistry shows positivity for CD34. The treatment is surgical. We report a case of long evolution, with an unusual location, that relapsed after surgery, to emphasize the importance of early diagnosis and proper treatment, avoiding aggressive resections with increased morbidity.Sociedade Brasileira de Dermatologia2014-04-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000200357Anais Brasileiros de Dermatologia v.89 n.2 2014reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20142696info:eu-repo/semantics/openAccessFranco,Joanna Pimenta de AraujoBarbosa,Caroline CruzFonseca,Bárbara Ferreira Saraiva daLima,Ricardo BarbosaD'Acri,Antônio MacedoMartins,Carlos Joséeng2014-06-11T00:00:00Zoai:scielo:S0365-05962014000200357Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2014-06-11T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false
dc.title.none.fl_str_mv Case for diagnosis
title Case for diagnosis
spellingShingle Case for diagnosis
Franco,Joanna Pimenta de Araujo
Dermatofibrosarcoma
Extremities
Skin neoplasms
title_short Case for diagnosis
title_full Case for diagnosis
title_fullStr Case for diagnosis
title_full_unstemmed Case for diagnosis
title_sort Case for diagnosis
author Franco,Joanna Pimenta de Araujo
author_facet Franco,Joanna Pimenta de Araujo
Barbosa,Caroline Cruz
Fonseca,Bárbara Ferreira Saraiva da
Lima,Ricardo Barbosa
D'Acri,Antônio Macedo
Martins,Carlos José
author_role author
author2 Barbosa,Caroline Cruz
Fonseca,Bárbara Ferreira Saraiva da
Lima,Ricardo Barbosa
D'Acri,Antônio Macedo
Martins,Carlos José
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Franco,Joanna Pimenta de Araujo
Barbosa,Caroline Cruz
Fonseca,Bárbara Ferreira Saraiva da
Lima,Ricardo Barbosa
D'Acri,Antônio Macedo
Martins,Carlos José
dc.subject.por.fl_str_mv Dermatofibrosarcoma
Extremities
Skin neoplasms
topic Dermatofibrosarcoma
Extremities
Skin neoplasms
description Dermatofibrosarcoma protuberans is a fibrohistiocytic tumor of intermediate malignancy with aggressive localized growth, high recurrence rate, but low metastatic potential. It appears as a hardened plaque, with slow growth, upon which the development of nodules occurs. It predominates in the trunk and is unusual in acral locations. Histopathology reveals spindle cells with storiform pattern and cartwheel-like or whirlwind-like aspect. Immunohistochemistry shows positivity for CD34. The treatment is surgical. We report a case of long evolution, with an unusual location, that relapsed after surgery, to emphasize the importance of early diagnosis and proper treatment, avoiding aggressive resections with increased morbidity.
publishDate 2014
dc.date.none.fl_str_mv 2014-04-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000200357
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000200357
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/abd1806-4841.20142696
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv Anais Brasileiros de Dermatologia v.89 n.2 2014
reponame:Anais brasileiros de dermatologia (Online)
instname:Sociedade Brasileira de Dermatologia (SBD)
instacron:SBD
instname_str Sociedade Brasileira de Dermatologia (SBD)
instacron_str SBD
institution SBD
reponame_str Anais brasileiros de dermatologia (Online)
collection Anais brasileiros de dermatologia (Online)
repository.name.fl_str_mv Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)
repository.mail.fl_str_mv abd@sbd.org.br||revista@sbd.org.br
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