Case for diagnosis
Autor(a) principal: | |
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Data de Publicação: | 2014 |
Outros Autores: | , , , , |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | Anais brasileiros de dermatologia (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000200357 |
Resumo: | Dermatofibrosarcoma protuberans is a fibrohistiocytic tumor of intermediate malignancy with aggressive localized growth, high recurrence rate, but low metastatic potential. It appears as a hardened plaque, with slow growth, upon which the development of nodules occurs. It predominates in the trunk and is unusual in acral locations. Histopathology reveals spindle cells with storiform pattern and cartwheel-like or whirlwind-like aspect. Immunohistochemistry shows positivity for CD34. The treatment is surgical. We report a case of long evolution, with an unusual location, that relapsed after surgery, to emphasize the importance of early diagnosis and proper treatment, avoiding aggressive resections with increased morbidity. |
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Anais brasileiros de dermatologia (Online) |
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Case for diagnosisDermatofibrosarcomaExtremitiesSkin neoplasmsDermatofibrosarcoma protuberans is a fibrohistiocytic tumor of intermediate malignancy with aggressive localized growth, high recurrence rate, but low metastatic potential. It appears as a hardened plaque, with slow growth, upon which the development of nodules occurs. It predominates in the trunk and is unusual in acral locations. Histopathology reveals spindle cells with storiform pattern and cartwheel-like or whirlwind-like aspect. Immunohistochemistry shows positivity for CD34. The treatment is surgical. We report a case of long evolution, with an unusual location, that relapsed after surgery, to emphasize the importance of early diagnosis and proper treatment, avoiding aggressive resections with increased morbidity.Sociedade Brasileira de Dermatologia2014-04-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000200357Anais Brasileiros de Dermatologia v.89 n.2 2014reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20142696info:eu-repo/semantics/openAccessFranco,Joanna Pimenta de AraujoBarbosa,Caroline CruzFonseca,Bárbara Ferreira Saraiva daLima,Ricardo BarbosaD'Acri,Antônio MacedoMartins,Carlos Joséeng2014-06-11T00:00:00Zoai:scielo:S0365-05962014000200357Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2014-06-11T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false |
dc.title.none.fl_str_mv |
Case for diagnosis |
title |
Case for diagnosis |
spellingShingle |
Case for diagnosis Franco,Joanna Pimenta de Araujo Dermatofibrosarcoma Extremities Skin neoplasms |
title_short |
Case for diagnosis |
title_full |
Case for diagnosis |
title_fullStr |
Case for diagnosis |
title_full_unstemmed |
Case for diagnosis |
title_sort |
Case for diagnosis |
author |
Franco,Joanna Pimenta de Araujo |
author_facet |
Franco,Joanna Pimenta de Araujo Barbosa,Caroline Cruz Fonseca,Bárbara Ferreira Saraiva da Lima,Ricardo Barbosa D'Acri,Antônio Macedo Martins,Carlos José |
author_role |
author |
author2 |
Barbosa,Caroline Cruz Fonseca,Bárbara Ferreira Saraiva da Lima,Ricardo Barbosa D'Acri,Antônio Macedo Martins,Carlos José |
author2_role |
author author author author author |
dc.contributor.author.fl_str_mv |
Franco,Joanna Pimenta de Araujo Barbosa,Caroline Cruz Fonseca,Bárbara Ferreira Saraiva da Lima,Ricardo Barbosa D'Acri,Antônio Macedo Martins,Carlos José |
dc.subject.por.fl_str_mv |
Dermatofibrosarcoma Extremities Skin neoplasms |
topic |
Dermatofibrosarcoma Extremities Skin neoplasms |
description |
Dermatofibrosarcoma protuberans is a fibrohistiocytic tumor of intermediate malignancy with aggressive localized growth, high recurrence rate, but low metastatic potential. It appears as a hardened plaque, with slow growth, upon which the development of nodules occurs. It predominates in the trunk and is unusual in acral locations. Histopathology reveals spindle cells with storiform pattern and cartwheel-like or whirlwind-like aspect. Immunohistochemistry shows positivity for CD34. The treatment is surgical. We report a case of long evolution, with an unusual location, that relapsed after surgery, to emphasize the importance of early diagnosis and proper treatment, avoiding aggressive resections with increased morbidity. |
publishDate |
2014 |
dc.date.none.fl_str_mv |
2014-04-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000200357 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000200357 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/abd1806-4841.20142696 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
dc.source.none.fl_str_mv |
Anais Brasileiros de Dermatologia v.89 n.2 2014 reponame:Anais brasileiros de dermatologia (Online) instname:Sociedade Brasileira de Dermatologia (SBD) instacron:SBD |
instname_str |
Sociedade Brasileira de Dermatologia (SBD) |
instacron_str |
SBD |
institution |
SBD |
reponame_str |
Anais brasileiros de dermatologia (Online) |
collection |
Anais brasileiros de dermatologia (Online) |
repository.name.fl_str_mv |
Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD) |
repository.mail.fl_str_mv |
abd@sbd.org.br||revista@sbd.org.br |
_version_ |
1752126419519930368 |