Poorly differentiated synovial sarcoma in the wrist - Case report

Detalhes bibliográficos
Autor(a) principal: Maia,Daniela Cristina Caetano
Data de Publicação: 2014
Outros Autores: Menezes,Carla Kellen da Silva, Bastos,Thales Costa, Ferreira,Luiz Carlos de Lima, Francesconi,Fabio
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Anais brasileiros de dermatologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000500816
Resumo: Synovial sarcomas are rare malignant tumors affecting mainly young adults, presenting as a slow growth mass located in deep soft tissues of extremities, near the joints. In this report a 34-year-old male patient, presented an ulcerovegetative lesion on the right wrist which was completely excised. Histopathology and immunohistochemistry confirmed synovial sarcomas with poorly differentiated cells. This patient presented 11 months later with ipsilateral axillary lymph node metastasis, which emphasizes the unfavorable prognosis of this synovial sarcoma variant. The indolent growth pattern of this sarcoma justifies the well circumscribed initial stages, which progressively infiltrate adjacent structures with lung metastasis (80%) and lymph node involvement (20%) and thus corroborates the importance of early diagnosis and proper treatment.
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spelling Poorly differentiated synovial sarcoma in the wrist - Case reportPathologySarcoma, synovialSoft tissue neoplasmsSynovial sarcomas are rare malignant tumors affecting mainly young adults, presenting as a slow growth mass located in deep soft tissues of extremities, near the joints. In this report a 34-year-old male patient, presented an ulcerovegetative lesion on the right wrist which was completely excised. Histopathology and immunohistochemistry confirmed synovial sarcomas with poorly differentiated cells. This patient presented 11 months later with ipsilateral axillary lymph node metastasis, which emphasizes the unfavorable prognosis of this synovial sarcoma variant. The indolent growth pattern of this sarcoma justifies the well circumscribed initial stages, which progressively infiltrate adjacent structures with lung metastasis (80%) and lymph node involvement (20%) and thus corroborates the importance of early diagnosis and proper treatment.Sociedade Brasileira de Dermatologia2014-10-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000500816Anais Brasileiros de Dermatologia v.89 n.5 2014reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20143015info:eu-repo/semantics/openAccessMaia,Daniela Cristina CaetanoMenezes,Carla Kellen da SilvaBastos,Thales CostaFerreira,Luiz Carlos de LimaFrancesconi,Fabioeng2014-09-16T00:00:00Zoai:scielo:S0365-05962014000500816Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2014-09-16T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false
dc.title.none.fl_str_mv Poorly differentiated synovial sarcoma in the wrist - Case report
title Poorly differentiated synovial sarcoma in the wrist - Case report
spellingShingle Poorly differentiated synovial sarcoma in the wrist - Case report
Maia,Daniela Cristina Caetano
Pathology
Sarcoma, synovial
Soft tissue neoplasms
title_short Poorly differentiated synovial sarcoma in the wrist - Case report
title_full Poorly differentiated synovial sarcoma in the wrist - Case report
title_fullStr Poorly differentiated synovial sarcoma in the wrist - Case report
title_full_unstemmed Poorly differentiated synovial sarcoma in the wrist - Case report
title_sort Poorly differentiated synovial sarcoma in the wrist - Case report
author Maia,Daniela Cristina Caetano
author_facet Maia,Daniela Cristina Caetano
Menezes,Carla Kellen da Silva
Bastos,Thales Costa
Ferreira,Luiz Carlos de Lima
Francesconi,Fabio
author_role author
author2 Menezes,Carla Kellen da Silva
Bastos,Thales Costa
Ferreira,Luiz Carlos de Lima
Francesconi,Fabio
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Maia,Daniela Cristina Caetano
Menezes,Carla Kellen da Silva
Bastos,Thales Costa
Ferreira,Luiz Carlos de Lima
Francesconi,Fabio
dc.subject.por.fl_str_mv Pathology
Sarcoma, synovial
Soft tissue neoplasms
topic Pathology
Sarcoma, synovial
Soft tissue neoplasms
description Synovial sarcomas are rare malignant tumors affecting mainly young adults, presenting as a slow growth mass located in deep soft tissues of extremities, near the joints. In this report a 34-year-old male patient, presented an ulcerovegetative lesion on the right wrist which was completely excised. Histopathology and immunohistochemistry confirmed synovial sarcomas with poorly differentiated cells. This patient presented 11 months later with ipsilateral axillary lymph node metastasis, which emphasizes the unfavorable prognosis of this synovial sarcoma variant. The indolent growth pattern of this sarcoma justifies the well circumscribed initial stages, which progressively infiltrate adjacent structures with lung metastasis (80%) and lymph node involvement (20%) and thus corroborates the importance of early diagnosis and proper treatment.
publishDate 2014
dc.date.none.fl_str_mv 2014-10-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000500816
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000500816
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/abd1806-4841.20143015
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv Anais Brasileiros de Dermatologia v.89 n.5 2014
reponame:Anais brasileiros de dermatologia (Online)
instname:Sociedade Brasileira de Dermatologia (SBD)
instacron:SBD
instname_str Sociedade Brasileira de Dermatologia (SBD)
instacron_str SBD
institution SBD
reponame_str Anais brasileiros de dermatologia (Online)
collection Anais brasileiros de dermatologia (Online)
repository.name.fl_str_mv Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)
repository.mail.fl_str_mv abd@sbd.org.br||revista@sbd.org.br
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