Steatocystoma multiplex suppurativa: case report of a rare condition

Detalhes bibliográficos
Autor(a) principal: Santana,Cândida Naira Lima e Lima
Data de Publicação: 2016
Outros Autores: Pereira,Daniele do Nascimento, Lisboa,Alice Paixão, Leal,Juliana Martins, Obadia,Daniel Lago, Silva,Roberto Souto da
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Anais brasileiros de dermatologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016001100051
Resumo: Abstract Steatocystoma multiplex is a rare genetic disorder characterized by the presence of hamartomatous malformations at the junction of the pilosebaceous duct. It consists of encapsulated cystic lesions in the dermis, with adjacent sebaceous gland. When associated with inflammation, resembling hidradenitis, it is called steatocystoma multiplex suppurativa, a condition rarely reported. This is the first case of steatocystoma multiplex suppurativa reported in the Brazilian literature. Female patient, 23 years old, with papular and nodular cystic lesions that started in the armpits and groin, later spreading to the trunk, lower limbs, anticubital fossa, face and scalp. The presence of papular-nodular lesions associated with disseminated hidradenitis-like lesions in flexural areas and the histopathological diagnosis of steatocystoma defined the diagnosis of steatocystoma multiplex suppurativa.
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spelling Steatocystoma multiplex suppurativa: case report of a rare conditionSteatocystoma MultiplexHidradenitis SuppurativaSuppurationAbstract Steatocystoma multiplex is a rare genetic disorder characterized by the presence of hamartomatous malformations at the junction of the pilosebaceous duct. It consists of encapsulated cystic lesions in the dermis, with adjacent sebaceous gland. When associated with inflammation, resembling hidradenitis, it is called steatocystoma multiplex suppurativa, a condition rarely reported. This is the first case of steatocystoma multiplex suppurativa reported in the Brazilian literature. Female patient, 23 years old, with papular and nodular cystic lesions that started in the armpits and groin, later spreading to the trunk, lower limbs, anticubital fossa, face and scalp. The presence of papular-nodular lesions associated with disseminated hidradenitis-like lesions in flexural areas and the histopathological diagnosis of steatocystoma defined the diagnosis of steatocystoma multiplex suppurativa.Sociedade Brasileira de Dermatologia2016-10-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016001100051Anais Brasileiros de Dermatologia v.91 n.5 suppl.1 2016reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20164539info:eu-repo/semantics/openAccessSantana,Cândida Naira Lima e LimaPereira,Daniele do NascimentoLisboa,Alice PaixãoLeal,Juliana MartinsObadia,Daniel LagoSilva,Roberto Souto daeng2017-03-03T00:00:00Zoai:scielo:S0365-05962016001100051Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2017-03-03T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false
dc.title.none.fl_str_mv Steatocystoma multiplex suppurativa: case report of a rare condition
title Steatocystoma multiplex suppurativa: case report of a rare condition
spellingShingle Steatocystoma multiplex suppurativa: case report of a rare condition
Santana,Cândida Naira Lima e Lima
Steatocystoma Multiplex
Hidradenitis Suppurativa
Suppuration
title_short Steatocystoma multiplex suppurativa: case report of a rare condition
title_full Steatocystoma multiplex suppurativa: case report of a rare condition
title_fullStr Steatocystoma multiplex suppurativa: case report of a rare condition
title_full_unstemmed Steatocystoma multiplex suppurativa: case report of a rare condition
title_sort Steatocystoma multiplex suppurativa: case report of a rare condition
author Santana,Cândida Naira Lima e Lima
author_facet Santana,Cândida Naira Lima e Lima
Pereira,Daniele do Nascimento
Lisboa,Alice Paixão
Leal,Juliana Martins
Obadia,Daniel Lago
Silva,Roberto Souto da
author_role author
author2 Pereira,Daniele do Nascimento
Lisboa,Alice Paixão
Leal,Juliana Martins
Obadia,Daniel Lago
Silva,Roberto Souto da
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Santana,Cândida Naira Lima e Lima
Pereira,Daniele do Nascimento
Lisboa,Alice Paixão
Leal,Juliana Martins
Obadia,Daniel Lago
Silva,Roberto Souto da
dc.subject.por.fl_str_mv Steatocystoma Multiplex
Hidradenitis Suppurativa
Suppuration
topic Steatocystoma Multiplex
Hidradenitis Suppurativa
Suppuration
description Abstract Steatocystoma multiplex is a rare genetic disorder characterized by the presence of hamartomatous malformations at the junction of the pilosebaceous duct. It consists of encapsulated cystic lesions in the dermis, with adjacent sebaceous gland. When associated with inflammation, resembling hidradenitis, it is called steatocystoma multiplex suppurativa, a condition rarely reported. This is the first case of steatocystoma multiplex suppurativa reported in the Brazilian literature. Female patient, 23 years old, with papular and nodular cystic lesions that started in the armpits and groin, later spreading to the trunk, lower limbs, anticubital fossa, face and scalp. The presence of papular-nodular lesions associated with disseminated hidradenitis-like lesions in flexural areas and the histopathological diagnosis of steatocystoma defined the diagnosis of steatocystoma multiplex suppurativa.
publishDate 2016
dc.date.none.fl_str_mv 2016-10-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016001100051
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962016001100051
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/abd1806-4841.20164539
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv Anais Brasileiros de Dermatologia v.91 n.5 suppl.1 2016
reponame:Anais brasileiros de dermatologia (Online)
instname:Sociedade Brasileira de Dermatologia (SBD)
instacron:SBD
instname_str Sociedade Brasileira de Dermatologia (SBD)
instacron_str SBD
institution SBD
reponame_str Anais brasileiros de dermatologia (Online)
collection Anais brasileiros de dermatologia (Online)
repository.name.fl_str_mv Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)
repository.mail.fl_str_mv abd@sbd.org.br||revista@sbd.org.br
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