Case for diagnosis

Detalhes bibliográficos
Autor(a) principal: Zanuncio,Virginia Vinha
Data de Publicação: 2013
Outros Autores: Carvalho,Luciana Rabelo de, Guedes,Antônio Carlos Martins, Silva,Cláudia Márcia Resende, Gontijo,Bernardo
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Anais brasileiros de dermatologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000601001
Resumo: Langerhans cell histiocytosis is a rare, clinically heterogeneous desease. Since there is considerable clinical overlap among the four described variants (Hand-Schüller-Christian, eosinophilic granuloma, Letterer-Siwe and Hashimoto-Pritzker), the concept of spectral disease applies to this entity. The Hashimoto-Pritzker variant was first described in 1973. Characteristically, it is present at birth or during the first days of life, impairment is limited to the skin and prognosis is favorable with spontaneous resolution. We report a newborn male patient with Hashimoto-Pritzker disease presenting as a S100 + and CD1a + single congenital perianal lesion with rapid involution in two months.
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spelling Case for diagnosisHistiocytosis, Langerhans-cellImmunohistochemistryPrognosisLangerhans cell histiocytosis is a rare, clinically heterogeneous desease. Since there is considerable clinical overlap among the four described variants (Hand-Schüller-Christian, eosinophilic granuloma, Letterer-Siwe and Hashimoto-Pritzker), the concept of spectral disease applies to this entity. The Hashimoto-Pritzker variant was first described in 1973. Characteristically, it is present at birth or during the first days of life, impairment is limited to the skin and prognosis is favorable with spontaneous resolution. We report a newborn male patient with Hashimoto-Pritzker disease presenting as a S100 + and CD1a + single congenital perianal lesion with rapid involution in two months.Sociedade Brasileira de Dermatologia2013-12-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000601001Anais Brasileiros de Dermatologia v.88 n.6 2013reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20132451info:eu-repo/semantics/openAccessZanuncio,Virginia VinhaCarvalho,Luciana Rabelo deGuedes,Antônio Carlos MartinsSilva,Cláudia Márcia ResendeGontijo,Bernardoeng2014-08-29T00:00:00Zoai:scielo:S0365-05962013000601001Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2014-08-29T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false
dc.title.none.fl_str_mv Case for diagnosis
title Case for diagnosis
spellingShingle Case for diagnosis
Zanuncio,Virginia Vinha
Histiocytosis, Langerhans-cell
Immunohistochemistry
Prognosis
title_short Case for diagnosis
title_full Case for diagnosis
title_fullStr Case for diagnosis
title_full_unstemmed Case for diagnosis
title_sort Case for diagnosis
author Zanuncio,Virginia Vinha
author_facet Zanuncio,Virginia Vinha
Carvalho,Luciana Rabelo de
Guedes,Antônio Carlos Martins
Silva,Cláudia Márcia Resende
Gontijo,Bernardo
author_role author
author2 Carvalho,Luciana Rabelo de
Guedes,Antônio Carlos Martins
Silva,Cláudia Márcia Resende
Gontijo,Bernardo
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Zanuncio,Virginia Vinha
Carvalho,Luciana Rabelo de
Guedes,Antônio Carlos Martins
Silva,Cláudia Márcia Resende
Gontijo,Bernardo
dc.subject.por.fl_str_mv Histiocytosis, Langerhans-cell
Immunohistochemistry
Prognosis
topic Histiocytosis, Langerhans-cell
Immunohistochemistry
Prognosis
description Langerhans cell histiocytosis is a rare, clinically heterogeneous desease. Since there is considerable clinical overlap among the four described variants (Hand-Schüller-Christian, eosinophilic granuloma, Letterer-Siwe and Hashimoto-Pritzker), the concept of spectral disease applies to this entity. The Hashimoto-Pritzker variant was first described in 1973. Characteristically, it is present at birth or during the first days of life, impairment is limited to the skin and prognosis is favorable with spontaneous resolution. We report a newborn male patient with Hashimoto-Pritzker disease presenting as a S100 + and CD1a + single congenital perianal lesion with rapid involution in two months.
publishDate 2013
dc.date.none.fl_str_mv 2013-12-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000601001
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000601001
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/abd1806-4841.20132451
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv Anais Brasileiros de Dermatologia v.88 n.6 2013
reponame:Anais brasileiros de dermatologia (Online)
instname:Sociedade Brasileira de Dermatologia (SBD)
instacron:SBD
instname_str Sociedade Brasileira de Dermatologia (SBD)
instacron_str SBD
institution SBD
reponame_str Anais brasileiros de dermatologia (Online)
collection Anais brasileiros de dermatologia (Online)
repository.name.fl_str_mv Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)
repository.mail.fl_str_mv abd@sbd.org.br||revista@sbd.org.br
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