Familial “benign” pemphigus? Erythroderma and fatal outcome,

Detalhes bibliográficos
Autor(a) principal: Tansini,Paula Baldissera
Data de Publicação: 2020
Outros Autores: Boff,Ana Letícia, Weber,Magda Blessmann, Bonamigo,Renan Rangel
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Anais brasileiros de dermatologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962020000100075
Resumo: Abstract Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome.
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spelling Familial “benign” pemphigus? Erythroderma and fatal outcome,Pemphigus, benign familialDermatitis, exfoliativeSkin diseases, vesiculobullousAbstract Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome.Sociedade Brasileira de Dermatologia2020-02-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962020000100075Anais Brasileiros de Dermatologia v.95 n.1 2020reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1016/j.abd.2019.02.006info:eu-repo/semantics/openAccessTansini,Paula BaldisseraBoff,Ana LetíciaWeber,Magda BlessmannBonamigo,Renan Rangeleng2020-03-26T00:00:00Zoai:scielo:S0365-05962020000100075Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2020-03-26T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false
dc.title.none.fl_str_mv Familial “benign” pemphigus? Erythroderma and fatal outcome,
title Familial “benign” pemphigus? Erythroderma and fatal outcome,
spellingShingle Familial “benign” pemphigus? Erythroderma and fatal outcome,
Tansini,Paula Baldissera
Pemphigus, benign familial
Dermatitis, exfoliative
Skin diseases, vesiculobullous
title_short Familial “benign” pemphigus? Erythroderma and fatal outcome,
title_full Familial “benign” pemphigus? Erythroderma and fatal outcome,
title_fullStr Familial “benign” pemphigus? Erythroderma and fatal outcome,
title_full_unstemmed Familial “benign” pemphigus? Erythroderma and fatal outcome,
title_sort Familial “benign” pemphigus? Erythroderma and fatal outcome,
author Tansini,Paula Baldissera
author_facet Tansini,Paula Baldissera
Boff,Ana Letícia
Weber,Magda Blessmann
Bonamigo,Renan Rangel
author_role author
author2 Boff,Ana Letícia
Weber,Magda Blessmann
Bonamigo,Renan Rangel
author2_role author
author
author
dc.contributor.author.fl_str_mv Tansini,Paula Baldissera
Boff,Ana Letícia
Weber,Magda Blessmann
Bonamigo,Renan Rangel
dc.subject.por.fl_str_mv Pemphigus, benign familial
Dermatitis, exfoliative
Skin diseases, vesiculobullous
topic Pemphigus, benign familial
Dermatitis, exfoliative
Skin diseases, vesiculobullous
description Abstract Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome.
publishDate 2020
dc.date.none.fl_str_mv 2020-02-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
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status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962020000100075
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962020000100075
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1016/j.abd.2019.02.006
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv Anais Brasileiros de Dermatologia v.95 n.1 2020
reponame:Anais brasileiros de dermatologia (Online)
instname:Sociedade Brasileira de Dermatologia (SBD)
instacron:SBD
instname_str Sociedade Brasileira de Dermatologia (SBD)
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institution SBD
reponame_str Anais brasileiros de dermatologia (Online)
collection Anais brasileiros de dermatologia (Online)
repository.name.fl_str_mv Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)
repository.mail.fl_str_mv abd@sbd.org.br||revista@sbd.org.br
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