Familial “benign” pemphigus? Erythroderma and fatal outcome,
Autor(a) principal: | |
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Data de Publicação: | 2020 |
Outros Autores: | , , |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | Anais brasileiros de dermatologia (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962020000100075 |
Resumo: | Abstract Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome. |
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Familial “benign” pemphigus? Erythroderma and fatal outcome,Pemphigus, benign familialDermatitis, exfoliativeSkin diseases, vesiculobullousAbstract Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome.Sociedade Brasileira de Dermatologia2020-02-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962020000100075Anais Brasileiros de Dermatologia v.95 n.1 2020reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1016/j.abd.2019.02.006info:eu-repo/semantics/openAccessTansini,Paula BaldisseraBoff,Ana LetíciaWeber,Magda BlessmannBonamigo,Renan Rangeleng2020-03-26T00:00:00Zoai:scielo:S0365-05962020000100075Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2020-03-26T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false |
dc.title.none.fl_str_mv |
Familial “benign” pemphigus? Erythroderma and fatal outcome, |
title |
Familial “benign” pemphigus? Erythroderma and fatal outcome, |
spellingShingle |
Familial “benign” pemphigus? Erythroderma and fatal outcome, Tansini,Paula Baldissera Pemphigus, benign familial Dermatitis, exfoliative Skin diseases, vesiculobullous |
title_short |
Familial “benign” pemphigus? Erythroderma and fatal outcome, |
title_full |
Familial “benign” pemphigus? Erythroderma and fatal outcome, |
title_fullStr |
Familial “benign” pemphigus? Erythroderma and fatal outcome, |
title_full_unstemmed |
Familial “benign” pemphigus? Erythroderma and fatal outcome, |
title_sort |
Familial “benign” pemphigus? Erythroderma and fatal outcome, |
author |
Tansini,Paula Baldissera |
author_facet |
Tansini,Paula Baldissera Boff,Ana Letícia Weber,Magda Blessmann Bonamigo,Renan Rangel |
author_role |
author |
author2 |
Boff,Ana Letícia Weber,Magda Blessmann Bonamigo,Renan Rangel |
author2_role |
author author author |
dc.contributor.author.fl_str_mv |
Tansini,Paula Baldissera Boff,Ana Letícia Weber,Magda Blessmann Bonamigo,Renan Rangel |
dc.subject.por.fl_str_mv |
Pemphigus, benign familial Dermatitis, exfoliative Skin diseases, vesiculobullous |
topic |
Pemphigus, benign familial Dermatitis, exfoliative Skin diseases, vesiculobullous |
description |
Abstract Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome. |
publishDate |
2020 |
dc.date.none.fl_str_mv |
2020-02-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962020000100075 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962020000100075 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1016/j.abd.2019.02.006 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
dc.source.none.fl_str_mv |
Anais Brasileiros de Dermatologia v.95 n.1 2020 reponame:Anais brasileiros de dermatologia (Online) instname:Sociedade Brasileira de Dermatologia (SBD) instacron:SBD |
instname_str |
Sociedade Brasileira de Dermatologia (SBD) |
instacron_str |
SBD |
institution |
SBD |
reponame_str |
Anais brasileiros de dermatologia (Online) |
collection |
Anais brasileiros de dermatologia (Online) |
repository.name.fl_str_mv |
Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD) |
repository.mail.fl_str_mv |
abd@sbd.org.br||revista@sbd.org.br |
_version_ |
1752126423802314752 |