Familial ‘‘benign’’ pemphigus? Erythroderma and fatal outcome

Detalhes bibliográficos
Autor(a) principal: Tansini, Paula Baldissera
Data de Publicação: 2020
Outros Autores: Boff, Ana Letícia, Weber, Magda Blessmann, Bonamigo, Renan Rangel
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Institucional da UFRGS
Texto Completo: http://hdl.handle.net/10183/212341
Resumo: Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome.
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spelling Tansini, Paula BaldisseraBoff, Ana LetíciaWeber, Magda BlessmannBonamigo, Renan Rangel2020-07-23T03:40:33Z20200365-0596http://hdl.handle.net/10183/212341001114856Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome.application/pdfengAnais brasileiros de dermatologia. Vol. 95, no. 1 (2020), p. 75-77Pênfigo familiar benignoDermatite esfoliativaRelatos de casosPemphigus, benign familialDermatitis, exfoliativeSkin diseasesVesiculobullousFamilial ‘‘benign’’ pemphigus? Erythroderma and fatal outcomeinfo:eu-repo/semantics/articleinfo:eu-repo/semantics/otherinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/openAccessreponame:Repositório Institucional da UFRGSinstname:Universidade Federal do Rio Grande do Sul (UFRGS)instacron:UFRGSTEXT001114856.pdf.txt001114856.pdf.txtExtracted Texttext/plain9249http://www.lume.ufrgs.br/bitstream/10183/212341/2/001114856.pdf.txt0c1cb19a3c927f7c66980602d1092afeMD52ORIGINAL001114856.pdfTexto completo (inglês)application/pdf857822http://www.lume.ufrgs.br/bitstream/10183/212341/1/001114856.pdf0dadf82cb384f5b6280db5e77b0bb93aMD5110183/2123412020-07-24 03:39:50.839742oai:www.lume.ufrgs.br:10183/212341Repositório de PublicaçõesPUBhttps://lume.ufrgs.br/oai/requestopendoar:2020-07-24T06:39:50Repositório Institucional da UFRGS - Universidade Federal do Rio Grande do Sul (UFRGS)false
dc.title.pt_BR.fl_str_mv Familial ‘‘benign’’ pemphigus? Erythroderma and fatal outcome
title Familial ‘‘benign’’ pemphigus? Erythroderma and fatal outcome
spellingShingle Familial ‘‘benign’’ pemphigus? Erythroderma and fatal outcome
Tansini, Paula Baldissera
Pênfigo familiar benigno
Dermatite esfoliativa
Relatos de casos
Pemphigus, benign familial
Dermatitis, exfoliative
Skin diseases
Vesiculobullous
title_short Familial ‘‘benign’’ pemphigus? Erythroderma and fatal outcome
title_full Familial ‘‘benign’’ pemphigus? Erythroderma and fatal outcome
title_fullStr Familial ‘‘benign’’ pemphigus? Erythroderma and fatal outcome
title_full_unstemmed Familial ‘‘benign’’ pemphigus? Erythroderma and fatal outcome
title_sort Familial ‘‘benign’’ pemphigus? Erythroderma and fatal outcome
author Tansini, Paula Baldissera
author_facet Tansini, Paula Baldissera
Boff, Ana Letícia
Weber, Magda Blessmann
Bonamigo, Renan Rangel
author_role author
author2 Boff, Ana Letícia
Weber, Magda Blessmann
Bonamigo, Renan Rangel
author2_role author
author
author
dc.contributor.author.fl_str_mv Tansini, Paula Baldissera
Boff, Ana Letícia
Weber, Magda Blessmann
Bonamigo, Renan Rangel
dc.subject.por.fl_str_mv Pênfigo familiar benigno
Dermatite esfoliativa
Relatos de casos
topic Pênfigo familiar benigno
Dermatite esfoliativa
Relatos de casos
Pemphigus, benign familial
Dermatitis, exfoliative
Skin diseases
Vesiculobullous
dc.subject.eng.fl_str_mv Pemphigus, benign familial
Dermatitis, exfoliative
Skin diseases
Vesiculobullous
description Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome.
publishDate 2020
dc.date.accessioned.fl_str_mv 2020-07-23T03:40:33Z
dc.date.issued.fl_str_mv 2020
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
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dc.identifier.uri.fl_str_mv http://hdl.handle.net/10183/212341
dc.identifier.issn.pt_BR.fl_str_mv 0365-0596
dc.identifier.nrb.pt_BR.fl_str_mv 001114856
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dc.language.iso.fl_str_mv eng
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dc.relation.ispartof.pt_BR.fl_str_mv Anais brasileiros de dermatologia. Vol. 95, no. 1 (2020), p. 75-77
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reponame_str Repositório Institucional da UFRGS
collection Repositório Institucional da UFRGS
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