Do you know this syndrome? Heerfordt-Waldenström syndrome
Autor(a) principal: | |
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Data de Publicação: | 2017 |
Outros Autores: | , , , , |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | Anais brasileiros de dermatologia (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000400571 |
Resumo: | Abstract: Heerfordt-Waldenström syndrome is a rare subacute variant of sarcoidosis, characterized by enlargement of the parotid or salivary glands, facial nerve paralysis and anterior uveitis. Granulomas with a peripheral lymphocyte deficit are found in the anatomic pathology of affected organs. It is normally self-limiting, with cure achieved between 12 and 36 months, but some prolonged cases have been reported. Diagnosis of the syndrome is clinical, and treatment depends on the degree of systemic impairment. Oral corticosteroids represent the first line treatment option. The mortality rate ranges between 1 and 5% of cases. |
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Do you know this syndrome? Heerfordt-Waldenström syndromeUveoparotid feverParotid glandFacial ParalysisSarcoidosisUveitisAbstract: Heerfordt-Waldenström syndrome is a rare subacute variant of sarcoidosis, characterized by enlargement of the parotid or salivary glands, facial nerve paralysis and anterior uveitis. Granulomas with a peripheral lymphocyte deficit are found in the anatomic pathology of affected organs. It is normally self-limiting, with cure achieved between 12 and 36 months, but some prolonged cases have been reported. Diagnosis of the syndrome is clinical, and treatment depends on the degree of systemic impairment. Oral corticosteroids represent the first line treatment option. The mortality rate ranges between 1 and 5% of cases.Sociedade Brasileira de Dermatologia2017-08-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000400571Anais Brasileiros de Dermatologia v.92 n.4 2017reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20175211info:eu-repo/semantics/openAccessFraga,Rafael CavanellasKakizaki,PriscilaValente,Neusa Yuriko SakaiPortocarrero,Larissa Karine LeiteTeixeira,Mônica Fernandes SeniseSenise,Priscilla Fernandeseng2017-09-14T00:00:00Zoai:scielo:S0365-05962017000400571Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2017-09-14T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false |
dc.title.none.fl_str_mv |
Do you know this syndrome? Heerfordt-Waldenström syndrome |
title |
Do you know this syndrome? Heerfordt-Waldenström syndrome |
spellingShingle |
Do you know this syndrome? Heerfordt-Waldenström syndrome Fraga,Rafael Cavanellas Uveoparotid fever Parotid gland Facial Paralysis Sarcoidosis Uveitis |
title_short |
Do you know this syndrome? Heerfordt-Waldenström syndrome |
title_full |
Do you know this syndrome? Heerfordt-Waldenström syndrome |
title_fullStr |
Do you know this syndrome? Heerfordt-Waldenström syndrome |
title_full_unstemmed |
Do you know this syndrome? Heerfordt-Waldenström syndrome |
title_sort |
Do you know this syndrome? Heerfordt-Waldenström syndrome |
author |
Fraga,Rafael Cavanellas |
author_facet |
Fraga,Rafael Cavanellas Kakizaki,Priscila Valente,Neusa Yuriko Sakai Portocarrero,Larissa Karine Leite Teixeira,Mônica Fernandes Senise Senise,Priscilla Fernandes |
author_role |
author |
author2 |
Kakizaki,Priscila Valente,Neusa Yuriko Sakai Portocarrero,Larissa Karine Leite Teixeira,Mônica Fernandes Senise Senise,Priscilla Fernandes |
author2_role |
author author author author author |
dc.contributor.author.fl_str_mv |
Fraga,Rafael Cavanellas Kakizaki,Priscila Valente,Neusa Yuriko Sakai Portocarrero,Larissa Karine Leite Teixeira,Mônica Fernandes Senise Senise,Priscilla Fernandes |
dc.subject.por.fl_str_mv |
Uveoparotid fever Parotid gland Facial Paralysis Sarcoidosis Uveitis |
topic |
Uveoparotid fever Parotid gland Facial Paralysis Sarcoidosis Uveitis |
description |
Abstract: Heerfordt-Waldenström syndrome is a rare subacute variant of sarcoidosis, characterized by enlargement of the parotid or salivary glands, facial nerve paralysis and anterior uveitis. Granulomas with a peripheral lymphocyte deficit are found in the anatomic pathology of affected organs. It is normally self-limiting, with cure achieved between 12 and 36 months, but some prolonged cases have been reported. Diagnosis of the syndrome is clinical, and treatment depends on the degree of systemic impairment. Oral corticosteroids represent the first line treatment option. The mortality rate ranges between 1 and 5% of cases. |
publishDate |
2017 |
dc.date.none.fl_str_mv |
2017-08-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000400571 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000400571 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/abd1806-4841.20175211 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
dc.source.none.fl_str_mv |
Anais Brasileiros de Dermatologia v.92 n.4 2017 reponame:Anais brasileiros de dermatologia (Online) instname:Sociedade Brasileira de Dermatologia (SBD) instacron:SBD |
instname_str |
Sociedade Brasileira de Dermatologia (SBD) |
instacron_str |
SBD |
institution |
SBD |
reponame_str |
Anais brasileiros de dermatologia (Online) |
collection |
Anais brasileiros de dermatologia (Online) |
repository.name.fl_str_mv |
Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD) |
repository.mail.fl_str_mv |
abd@sbd.org.br||revista@sbd.org.br |
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1752126422170730496 |