Banco de Cérebros do Brasil Central (BCBC): prevalência de demências e correlação clínico-patológica
Autor(a) principal: | |
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Data de Publicação: | 2016 |
Tipo de documento: | Tese |
Idioma: | por |
Título da fonte: | Repositório Institucional da UFG |
Texto Completo: | http://repositorio.bc.ufg.br/tede/handle/tede/5794 |
Resumo: | The diagnosis of dementia is made through autopsy. The histopathological and immunohistochemical technique makes it possible to differentiate the subtypes of dementia by pre-established macroscopic and microscopic criteria. Banks brain, although recent, provide biological material quality for multidisciplinary research in normal subjects and with dementia. Objectives: To correlate clinical findings with neuropathological cases with dementia from the Brains Bank of Central of Brazil (BBCB); establish morphological patterns in macroscopic focal dementias; determine the prevalence of diagnosis of other types of dementia. Materials and Methods: Brain Study from autopsies of patients with neurodegenerative diseases of dementia clinic of the HC-UFG (Ethics Committee of the Protocol on research 0692007). The brains were processed following dissection and measurement protocol. Appropriate external and macroscopic morphological descriptions and coronal and sagittal sections were performed. Results: 15 brains, 9 female patients were studied, aged 10 to 89 years. The types of dementias found in BCBC were 5 cases of frontotemporal dementia (FTD), 3 Alzheimer's disease (AD), 3 patients had primary progressive aphasia (PPA) and corticobasal degeneration (CBD), 1 Huntington's disease, 1 disease Creutzfeldt-Jakob 1, Rasmussen's encephalitis and 1 depressive pseudodementia (Cotard’s syndrome). Described frontal gyrus supernumerary in 3 cases of CBD and 2 cases of FTD. Discussion: Most cases presented morphological pattern of the respective type of dementia according to the literature, except PPA with CBD. In BCBC material only 20% of AD cases were 27% and frontotemporal lobar degeneration (FTLD). Conclusion: The higher prevalence of dementia in BCBC was the type FTLD. The frontotemporal focal atrophy was the most observed type of change. The cases with FTD showed classic morphological patterns, while the PPA CBD was different standard literature. The BCBC will enable studies in various research areas. |
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Caixeta, Leonardo Ferreirahttp://lattes.cnpq.br/9536747113677509Caixeta, Leonardo FerreiraCosta, Mauricio BarcelosTeixeira, Kim-Ir-Sen SantosTavares Junior, AntenorSilva, Delson José dahttp://lattes.cnpq.br/6481941077077942Silva, Wesley Gomes da2016-08-02T14:19:57Z2016-01-29DA SILVA, W. G. Banco de Cérebros do Brasil Central (BCBC): prevalência de demências e correlação clínico-patológica. 2016. 119 f. Tese (Doutorado em Ciências da Saúde) - Universidade Federal de Goiás, Goiânia, 2016.http://repositorio.bc.ufg.br/tede/handle/tede/5794The diagnosis of dementia is made through autopsy. The histopathological and immunohistochemical technique makes it possible to differentiate the subtypes of dementia by pre-established macroscopic and microscopic criteria. Banks brain, although recent, provide biological material quality for multidisciplinary research in normal subjects and with dementia. Objectives: To correlate clinical findings with neuropathological cases with dementia from the Brains Bank of Central of Brazil (BBCB); establish morphological patterns in macroscopic focal dementias; determine the prevalence of diagnosis of other types of dementia. Materials and Methods: Brain Study from autopsies of patients with neurodegenerative diseases of dementia clinic of the HC-UFG (Ethics Committee of the Protocol on research 0692007). The brains were processed following dissection and measurement protocol. Appropriate external and macroscopic morphological descriptions and coronal and sagittal sections were performed. Results: 15 brains, 9 female patients were studied, aged 10 to 89 years. The types of dementias found in BCBC were 5 cases of frontotemporal dementia (FTD), 3 Alzheimer's disease (AD), 3 patients had primary progressive aphasia (PPA) and corticobasal degeneration (CBD), 1 Huntington's disease, 1 disease Creutzfeldt-Jakob 1, Rasmussen's encephalitis and 1 depressive pseudodementia (Cotard’s syndrome). Described frontal gyrus supernumerary in 3 cases of CBD and 2 cases of FTD. Discussion: Most cases presented morphological pattern of the respective type of dementia according to the literature, except PPA with CBD. In BCBC material only 20% of AD cases were 27% and frontotemporal lobar degeneration (FTLD). Conclusion: The higher prevalence of dementia in BCBC was the type FTLD. The frontotemporal focal atrophy was the most observed type of change. The cases with FTD showed classic morphological patterns, while the PPA CBD was different standard literature. The BCBC will enable studies in various research areas.O diagnóstico definitivo das demências é feito através de necropsia. Os exames anatomopatológico e imunoistoquímico possibilitam diferenciar os subtipos de demência por critérios macroscópicos e microscópicos pré-estabelecidos. Os bancos de cérebros, apesar de recentes, fornecem material biológico de qualidade para pesquisas multidisciplinares de indivíduos normais e com demência. Objetivos: Correlacionar aspectos clínicos com alterações neuropatológicas de casos com demências provenientes do Banco de Cérebros do Brasil Central (BCBC); estabelecer padrões morfológicos macroscópicos nas demências focais; verificar a prevalência do diagnóstico de outros tipos de demências. Materiais e Métodos: Estudo de cérebros provenientes de necropsias de pacientes com doenças neurodegenerativas do ambulatório de demências do HC-UFG (protocolo do Comitê de ética em pesquisa 0692007). Os cérebros foram processados seguindo protocolo de dissecção e mensuração. Foram realizadas as devidas descrições morfológicas e macroscópicas externas e dos cortes coronais e sagitais. Resultados: Foram estudados 15 cérebros, 9 de pacientes do sexo feminino, com idade entre 10 a 89 anos. Os tipos de demências encontrados no BCBC foram: 5 casos de demência frontotemporal (DFT), 3 de doença de Alzheimer (DA), 3 casos com afasia progressiva primaria (APP) e degeneração corticobasal (DCB), 1 de doença de Huntington, 1 de doença de Creutzfeldt-Jakob, 1 de encefalite de Rasmussen e 1 de pseudodemência depressiva (síndrome de Cotard). Foi observado giro frontal supranumerário nos 3 casos de DCB e em 2 casos de DFT. Discussão: A maioria dos casos apresentou padrão morfológico do respectivo tipo de demência de acordo com a literatura, exceto APP com DCB. No material do BCBC apenas 20% dos casos foram de DA e 27% degeneração lobar frontotemporal (DLFT). Conclusão: A maior prevalência de demências no BCBC foi do tipo DLFT. A atrofia focal frontotemporal foi o tipo de alteração mais observada. Os casos com DFT apresentaram padrões morfológicos clássicos, enquanto que os de APP com DCB apresentaram padrão diferente da literatura. O BCBC possibilitará a realização de estudos em várias linhas de pesquisa.Submitted by Luciana Ferreira (lucgeral@gmail.com) on 2016-08-02T14:17:31Z No. of bitstreams: 2 Tese - Wesley Gomes da Silva - 2016.pdf: 5910954 bytes, checksum: 7d938f9383af006973baacbf56b71a52 (MD5) license_rdf: 0 bytes, checksum: d41d8cd98f00b204e9800998ecf8427e (MD5)Approved for entry into archive by Luciana Ferreira (lucgeral@gmail.com) on 2016-08-02T14:19:57Z (GMT) No. of bitstreams: 2 Tese - Wesley Gomes da Silva - 2016.pdf: 5910954 bytes, checksum: 7d938f9383af006973baacbf56b71a52 (MD5) license_rdf: 0 bytes, checksum: d41d8cd98f00b204e9800998ecf8427e (MD5)Made available in DSpace on 2016-08-02T14:19:57Z (GMT). No. of bitstreams: 2 Tese - Wesley Gomes da Silva - 2016.pdf: 5910954 bytes, checksum: 7d938f9383af006973baacbf56b71a52 (MD5) license_rdf: 0 bytes, checksum: d41d8cd98f00b204e9800998ecf8427e (MD5) Previous issue date: 2016-01-29application/pdfporUniversidade Federal de GoiásPrograma de Pós-graduação em Ciências da Saúde (FM)UFGBrasilFaculdade de Medicina - FM (RG)http://creativecommons.org/licenses/by-nc-nd/4.0/info:eu-repo/semantics/openAccessBanco de CérebrosNecropsiaDoenças neurodegenerativasDemênciaDegeneração lobar frontotemporalBrain BankNecropsyNeurodegenerative diseasesDementiaFrontotemporal lobar degenerationMEDICINA::ANATOMIA PATOLOGICA E PATOLOGIA CLINICABanco de Cérebros do Brasil Central (BCBC): prevalência de demências e correlação clínico-patológicaBrains Bank of Central of Brazil (BBCB): prevalence dementias correlation and climical pathologyinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/doctoralThesis-100686431261774531060060060015457724759504863387337577453819502453reponame:Repositório Institucional da UFGinstname:Universidade Federal de Goiás (UFG)instacron:UFGLICENSElicense.txtlicense.txttext/plain; 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dc.title.por.fl_str_mv |
Banco de Cérebros do Brasil Central (BCBC): prevalência de demências e correlação clínico-patológica |
dc.title.alternative.eng.fl_str_mv |
Brains Bank of Central of Brazil (BBCB): prevalence dementias correlation and climical pathology |
title |
Banco de Cérebros do Brasil Central (BCBC): prevalência de demências e correlação clínico-patológica |
spellingShingle |
Banco de Cérebros do Brasil Central (BCBC): prevalência de demências e correlação clínico-patológica Silva, Wesley Gomes da Banco de Cérebros Necropsia Doenças neurodegenerativas Demência Degeneração lobar frontotemporal Brain Bank Necropsy Neurodegenerative diseases Dementia Frontotemporal lobar degeneration MEDICINA::ANATOMIA PATOLOGICA E PATOLOGIA CLINICA |
title_short |
Banco de Cérebros do Brasil Central (BCBC): prevalência de demências e correlação clínico-patológica |
title_full |
Banco de Cérebros do Brasil Central (BCBC): prevalência de demências e correlação clínico-patológica |
title_fullStr |
Banco de Cérebros do Brasil Central (BCBC): prevalência de demências e correlação clínico-patológica |
title_full_unstemmed |
Banco de Cérebros do Brasil Central (BCBC): prevalência de demências e correlação clínico-patológica |
title_sort |
Banco de Cérebros do Brasil Central (BCBC): prevalência de demências e correlação clínico-patológica |
author |
Silva, Wesley Gomes da |
author_facet |
Silva, Wesley Gomes da |
author_role |
author |
dc.contributor.advisor1.fl_str_mv |
Caixeta, Leonardo Ferreira |
dc.contributor.advisor1Lattes.fl_str_mv |
http://lattes.cnpq.br/9536747113677509 |
dc.contributor.referee1.fl_str_mv |
Caixeta, Leonardo Ferreira |
dc.contributor.referee2.fl_str_mv |
Costa, Mauricio Barcelos |
dc.contributor.referee3.fl_str_mv |
Teixeira, Kim-Ir-Sen Santos |
dc.contributor.referee4.fl_str_mv |
Tavares Junior, Antenor |
dc.contributor.referee5.fl_str_mv |
Silva, Delson José da |
dc.contributor.authorLattes.fl_str_mv |
http://lattes.cnpq.br/6481941077077942 |
dc.contributor.author.fl_str_mv |
Silva, Wesley Gomes da |
contributor_str_mv |
Caixeta, Leonardo Ferreira Caixeta, Leonardo Ferreira Costa, Mauricio Barcelos Teixeira, Kim-Ir-Sen Santos Tavares Junior, Antenor Silva, Delson José da |
dc.subject.por.fl_str_mv |
Banco de Cérebros Necropsia Doenças neurodegenerativas Demência Degeneração lobar frontotemporal |
topic |
Banco de Cérebros Necropsia Doenças neurodegenerativas Demência Degeneração lobar frontotemporal Brain Bank Necropsy Neurodegenerative diseases Dementia Frontotemporal lobar degeneration MEDICINA::ANATOMIA PATOLOGICA E PATOLOGIA CLINICA |
dc.subject.eng.fl_str_mv |
Brain Bank Necropsy Neurodegenerative diseases Dementia Frontotemporal lobar degeneration |
dc.subject.cnpq.fl_str_mv |
MEDICINA::ANATOMIA PATOLOGICA E PATOLOGIA CLINICA |
description |
The diagnosis of dementia is made through autopsy. The histopathological and immunohistochemical technique makes it possible to differentiate the subtypes of dementia by pre-established macroscopic and microscopic criteria. Banks brain, although recent, provide biological material quality for multidisciplinary research in normal subjects and with dementia. Objectives: To correlate clinical findings with neuropathological cases with dementia from the Brains Bank of Central of Brazil (BBCB); establish morphological patterns in macroscopic focal dementias; determine the prevalence of diagnosis of other types of dementia. Materials and Methods: Brain Study from autopsies of patients with neurodegenerative diseases of dementia clinic of the HC-UFG (Ethics Committee of the Protocol on research 0692007). The brains were processed following dissection and measurement protocol. Appropriate external and macroscopic morphological descriptions and coronal and sagittal sections were performed. Results: 15 brains, 9 female patients were studied, aged 10 to 89 years. The types of dementias found in BCBC were 5 cases of frontotemporal dementia (FTD), 3 Alzheimer's disease (AD), 3 patients had primary progressive aphasia (PPA) and corticobasal degeneration (CBD), 1 Huntington's disease, 1 disease Creutzfeldt-Jakob 1, Rasmussen's encephalitis and 1 depressive pseudodementia (Cotard’s syndrome). Described frontal gyrus supernumerary in 3 cases of CBD and 2 cases of FTD. Discussion: Most cases presented morphological pattern of the respective type of dementia according to the literature, except PPA with CBD. In BCBC material only 20% of AD cases were 27% and frontotemporal lobar degeneration (FTLD). Conclusion: The higher prevalence of dementia in BCBC was the type FTLD. The frontotemporal focal atrophy was the most observed type of change. The cases with FTD showed classic morphological patterns, while the PPA CBD was different standard literature. The BCBC will enable studies in various research areas. |
publishDate |
2016 |
dc.date.accessioned.fl_str_mv |
2016-08-02T14:19:57Z |
dc.date.issued.fl_str_mv |
2016-01-29 |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/doctoralThesis |
format |
doctoralThesis |
status_str |
publishedVersion |
dc.identifier.citation.fl_str_mv |
DA SILVA, W. G. Banco de Cérebros do Brasil Central (BCBC): prevalência de demências e correlação clínico-patológica. 2016. 119 f. Tese (Doutorado em Ciências da Saúde) - Universidade Federal de Goiás, Goiânia, 2016. |
dc.identifier.uri.fl_str_mv |
http://repositorio.bc.ufg.br/tede/handle/tede/5794 |
identifier_str_mv |
DA SILVA, W. G. Banco de Cérebros do Brasil Central (BCBC): prevalência de demências e correlação clínico-patológica. 2016. 119 f. Tese (Doutorado em Ciências da Saúde) - Universidade Federal de Goiás, Goiânia, 2016. |
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http://repositorio.bc.ufg.br/tede/handle/tede/5794 |
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por |
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por |
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600 600 600 |
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1545772475950486338 |
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http://creativecommons.org/licenses/by-nc-nd/4.0/ info:eu-repo/semantics/openAccess |
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http://creativecommons.org/licenses/by-nc-nd/4.0/ |
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openAccess |
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Universidade Federal de Goiás |
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Programa de Pós-graduação em Ciências da Saúde (FM) |
dc.publisher.initials.fl_str_mv |
UFG |
dc.publisher.country.fl_str_mv |
Brasil |
dc.publisher.department.fl_str_mv |
Faculdade de Medicina - FM (RG) |
publisher.none.fl_str_mv |
Universidade Federal de Goiás |
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