Langerhans cell histiocytosis: case report

Detalhes bibliográficos
Autor(a) principal: Nogueira Freire, Karina Camillozzi
Data de Publicação: 2018
Outros Autores: Cardoso, Lia Quintães, de Miranda, Paulo Bittencourt, Pignaton, Christiane Chambo, Mendes, Cristiane Aparecida, Campostrini, Thayla Baptista
Tipo de documento: Artigo
Idioma: por
Título da fonte: HU Revista (Online)
Texto Completo: https://periodicos.ufjf.br/index.php/hurevista/article/view/2892
Resumo: Langerhans cell histiocytosis corresponds a heterogeneous group of disorders characterized by monoclonal dendritic cells proliferation, it predominates in childhood which may affect any organ of the body. The case reports of a female patient, aged 44, presentingthick plates with scales adhering to the hairs, scalp located, similar to seborrheic dermatitis, besides fistulas in axillas, inguinal and infra mammary regions. The hypothesis of Langerhans cell histiocytosis was confirmed by cutaneous biopsy and immunohistochemistry. Systemical investigation accused pulmonary involvement. Until now are few publications about adult cutaneous cases, so none treatment protocols are avaible for them. More specific studies are demanded for better management of these patients.
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spelling Langerhans cell histiocytosis: case reportHistiocitose de células de Langerhans: relato de um casoHistiocitoseHistiocitose de células de LangerhansAdultoAntígenos CD1QuimioterapiaLangerhans cell histiocytosis corresponds a heterogeneous group of disorders characterized by monoclonal dendritic cells proliferation, it predominates in childhood which may affect any organ of the body. The case reports of a female patient, aged 44, presentingthick plates with scales adhering to the hairs, scalp located, similar to seborrheic dermatitis, besides fistulas in axillas, inguinal and infra mammary regions. The hypothesis of Langerhans cell histiocytosis was confirmed by cutaneous biopsy and immunohistochemistry. Systemical investigation accused pulmonary involvement. Until now are few publications about adult cutaneous cases, so none treatment protocols are avaible for them. More specific studies are demanded for better management of these patients. A histiocitose de células de Langerhans corresponde a um grupo heterogêneo de desordens caracterizadas pela proliferação monoclonal de células dendríticas. Predomina na infância e pode afetar qualquer órgão. Relata-se caso de paciente, sexo feminino, 44 anos, apresentando placas espessas, exsudativas, com escamas aderentes aos pelos, localizadas no couro cabeludo, semelhantes a dermatite seborreica, além de fístulas nas axilas, regiões inframamárias e inguinais de evolução há 16 anos. Realizou-se biópsia da lesão cutânea seguida de imunohistoquímica que concluiu diagnóstico de Histiocitose de células de Langerhans. Investigação sistêmica evidenciou acometimento pulmonar concomitante. Até o presente momento existem poucas publicações sobre envolvimento cutâneo em adultos, assim como não há protocolos de tratamento para os mesmos, necessitando maiores estudos para melhor manejo desses pacientes.Editora UFJF2018-10-15info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionRelCasapplication/pdfapplication/vnd.openxmlformats-officedocument.wordprocessingml.documentimage/jpegapplication/vnd.openxmlformats-officedocument.wordprocessingml.documentapplication/pdfapplication/vnd.openxmlformats-officedocument.wordprocessingml.documentapplication/vnd.openxmlformats-officedocument.wordprocessingml.documenthttps://periodicos.ufjf.br/index.php/hurevista/article/view/289210.34019/1982-8047.2017.v43.2892HU Revista; v. 43 n. 3 (2017); 301 - 3041982-80470103-3123reponame:HU Revista (Online)instname:Universidade Federal de Juiz de Fora (UFJF)instacron:UFJFporhttps://periodicos.ufjf.br/index.php/hurevista/article/view/2892/pdfhttps://periodicos.ufjf.br/index.php/hurevista/article/view/2892/16124https://periodicos.ufjf.br/index.php/hurevista/article/view/2892/16125https://periodicos.ufjf.br/index.php/hurevista/article/view/2892/16129https://periodicos.ufjf.br/index.php/hurevista/article/view/2892/16130https://periodicos.ufjf.br/index.php/hurevista/article/view/2892/16131https://periodicos.ufjf.br/index.php/hurevista/article/view/2892/16137Nogueira Freire, Karina CamillozziCardoso, Lia Quintãesde Miranda, Paulo BittencourtPignaton, Christiane ChamboMendes, Cristiane AparecidaCampostrini, Thayla Baptistainfo:eu-repo/semantics/openAccess2019-07-19T03:27:22Zoai:periodicos.ufjf.br:article/2892Revistahttps://periodicos.ufjf.br/index.php/hurevistaPUBhttps://periodicos.ufjf.br/index.php/hurevista/oairevista.hurevista@ufjf.edu.br1982-80470103-3123opendoar:2019-07-19T03:27:22HU Revista (Online) - Universidade Federal de Juiz de Fora (UFJF)false
dc.title.none.fl_str_mv Langerhans cell histiocytosis: case report
Histiocitose de células de Langerhans: relato de um caso
title Langerhans cell histiocytosis: case report
spellingShingle Langerhans cell histiocytosis: case report
Nogueira Freire, Karina Camillozzi
Histiocitose
Histiocitose de células de Langerhans
Adulto
Antígenos CD1
Quimioterapia
title_short Langerhans cell histiocytosis: case report
title_full Langerhans cell histiocytosis: case report
title_fullStr Langerhans cell histiocytosis: case report
title_full_unstemmed Langerhans cell histiocytosis: case report
title_sort Langerhans cell histiocytosis: case report
author Nogueira Freire, Karina Camillozzi
author_facet Nogueira Freire, Karina Camillozzi
Cardoso, Lia Quintães
de Miranda, Paulo Bittencourt
Pignaton, Christiane Chambo
Mendes, Cristiane Aparecida
Campostrini, Thayla Baptista
author_role author
author2 Cardoso, Lia Quintães
de Miranda, Paulo Bittencourt
Pignaton, Christiane Chambo
Mendes, Cristiane Aparecida
Campostrini, Thayla Baptista
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Nogueira Freire, Karina Camillozzi
Cardoso, Lia Quintães
de Miranda, Paulo Bittencourt
Pignaton, Christiane Chambo
Mendes, Cristiane Aparecida
Campostrini, Thayla Baptista
dc.subject.por.fl_str_mv Histiocitose
Histiocitose de células de Langerhans
Adulto
Antígenos CD1
Quimioterapia
topic Histiocitose
Histiocitose de células de Langerhans
Adulto
Antígenos CD1
Quimioterapia
description Langerhans cell histiocytosis corresponds a heterogeneous group of disorders characterized by monoclonal dendritic cells proliferation, it predominates in childhood which may affect any organ of the body. The case reports of a female patient, aged 44, presentingthick plates with scales adhering to the hairs, scalp located, similar to seborrheic dermatitis, besides fistulas in axillas, inguinal and infra mammary regions. The hypothesis of Langerhans cell histiocytosis was confirmed by cutaneous biopsy and immunohistochemistry. Systemical investigation accused pulmonary involvement. Until now are few publications about adult cutaneous cases, so none treatment protocols are avaible for them. More specific studies are demanded for better management of these patients.
publishDate 2018
dc.date.none.fl_str_mv 2018-10-15
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10.34019/1982-8047.2017.v43.2892
url https://periodicos.ufjf.br/index.php/hurevista/article/view/2892
identifier_str_mv 10.34019/1982-8047.2017.v43.2892
dc.language.iso.fl_str_mv por
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dc.relation.none.fl_str_mv https://periodicos.ufjf.br/index.php/hurevista/article/view/2892/pdf
https://periodicos.ufjf.br/index.php/hurevista/article/view/2892/16124
https://periodicos.ufjf.br/index.php/hurevista/article/view/2892/16125
https://periodicos.ufjf.br/index.php/hurevista/article/view/2892/16129
https://periodicos.ufjf.br/index.php/hurevista/article/view/2892/16130
https://periodicos.ufjf.br/index.php/hurevista/article/view/2892/16131
https://periodicos.ufjf.br/index.php/hurevista/article/view/2892/16137
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dc.publisher.none.fl_str_mv Editora UFJF
publisher.none.fl_str_mv Editora UFJF
dc.source.none.fl_str_mv HU Revista; v. 43 n. 3 (2017); 301 - 304
1982-8047
0103-3123
reponame:HU Revista (Online)
instname:Universidade Federal de Juiz de Fora (UFJF)
instacron:UFJF
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instacron_str UFJF
institution UFJF
reponame_str HU Revista (Online)
collection HU Revista (Online)
repository.name.fl_str_mv HU Revista (Online) - Universidade Federal de Juiz de Fora (UFJF)
repository.mail.fl_str_mv revista.hurevista@ufjf.edu.br
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