Large aortic aneurysm and dissection in a patient with Marfan's syndrome

Detalhes bibliográficos
Autor(a) principal: Pivatto Júnior, Fernando
Data de Publicação: 2015
Outros Autores: Ramos, Leila Denise Cardoso, Foppa, Murilo, Torres, Felipe Soares
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Clinical and Biomedical Research
Texto Completo: https://seer.ufrgs.br/index.php/hcpa/article/view/52524
Resumo: Marfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive cardiac failure. In this report, we present a patient with a large symptomatic aortic aneurysm and chronic dissection, severe aortic regurgitation and cardiomegaly, treated successfully with resection of the proximal aorta and placement of a mechanic aortic valved graft. 
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spelling Large aortic aneurysm and dissection in a patient with Marfan's syndromeMarfan’s syndromeaortic aneurysmdissectionMarfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive cardiac failure. In this report, we present a patient with a large symptomatic aortic aneurysm and chronic dissection, severe aortic regurgitation and cardiomegaly, treated successfully with resection of the proximal aorta and placement of a mechanic aortic valved graft. HCPA/FAMED/UFRGS2015-04-28info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionPeer-reviewed ArticleAvaliado por paresapplication/pdfhttps://seer.ufrgs.br/index.php/hcpa/article/view/52524Clinical & Biomedical Research; Vol. 35 No. 2 (2015): Clinical and Biomedical ResearchClinical and Biomedical Research; v. 35 n. 2 (2015): Clinical and Biomedical Research2357-9730reponame:Clinical and Biomedical Researchinstname:Universidade Federal do Rio Grande do Sul (UFRGS)instacron:UFRGSenghttps://seer.ufrgs.br/index.php/hcpa/article/view/52524/pdf_10Pivatto Júnior, FernandoRamos, Leila Denise CardosoFoppa, MuriloTorres, Felipe Soaresinfo:eu-repo/semantics/openAccess2024-01-19T14:26:26Zoai:seer.ufrgs.br:article/52524Revistahttps://www.seer.ufrgs.br/index.php/hcpaPUBhttps://seer.ufrgs.br/index.php/hcpa/oai||cbr@hcpa.edu.br2357-97302357-9730opendoar:2024-01-19T14:26:26Clinical and Biomedical Research - Universidade Federal do Rio Grande do Sul (UFRGS)false
dc.title.none.fl_str_mv Large aortic aneurysm and dissection in a patient with Marfan's syndrome
title Large aortic aneurysm and dissection in a patient with Marfan's syndrome
spellingShingle Large aortic aneurysm and dissection in a patient with Marfan's syndrome
Pivatto Júnior, Fernando
Marfan’s syndrome
aortic aneurysm
dissection
title_short Large aortic aneurysm and dissection in a patient with Marfan's syndrome
title_full Large aortic aneurysm and dissection in a patient with Marfan's syndrome
title_fullStr Large aortic aneurysm and dissection in a patient with Marfan's syndrome
title_full_unstemmed Large aortic aneurysm and dissection in a patient with Marfan's syndrome
title_sort Large aortic aneurysm and dissection in a patient with Marfan's syndrome
author Pivatto Júnior, Fernando
author_facet Pivatto Júnior, Fernando
Ramos, Leila Denise Cardoso
Foppa, Murilo
Torres, Felipe Soares
author_role author
author2 Ramos, Leila Denise Cardoso
Foppa, Murilo
Torres, Felipe Soares
author2_role author
author
author
dc.contributor.author.fl_str_mv Pivatto Júnior, Fernando
Ramos, Leila Denise Cardoso
Foppa, Murilo
Torres, Felipe Soares
dc.subject.por.fl_str_mv Marfan’s syndrome
aortic aneurysm
dissection
topic Marfan’s syndrome
aortic aneurysm
dissection
description Marfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive cardiac failure. In this report, we present a patient with a large symptomatic aortic aneurysm and chronic dissection, severe aortic regurgitation and cardiomegaly, treated successfully with resection of the proximal aorta and placement of a mechanic aortic valved graft. 
publishDate 2015
dc.date.none.fl_str_mv 2015-04-28
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
Peer-reviewed Article
Avaliado por pares
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://seer.ufrgs.br/index.php/hcpa/article/view/52524
url https://seer.ufrgs.br/index.php/hcpa/article/view/52524
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv https://seer.ufrgs.br/index.php/hcpa/article/view/52524/pdf_10
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv HCPA/FAMED/UFRGS
publisher.none.fl_str_mv HCPA/FAMED/UFRGS
dc.source.none.fl_str_mv Clinical & Biomedical Research; Vol. 35 No. 2 (2015): Clinical and Biomedical Research
Clinical and Biomedical Research; v. 35 n. 2 (2015): Clinical and Biomedical Research
2357-9730
reponame:Clinical and Biomedical Research
instname:Universidade Federal do Rio Grande do Sul (UFRGS)
instacron:UFRGS
instname_str Universidade Federal do Rio Grande do Sul (UFRGS)
instacron_str UFRGS
institution UFRGS
reponame_str Clinical and Biomedical Research
collection Clinical and Biomedical Research
repository.name.fl_str_mv Clinical and Biomedical Research - Universidade Federal do Rio Grande do Sul (UFRGS)
repository.mail.fl_str_mv ||cbr@hcpa.edu.br
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