Large aortic aneurysm and dissection in a patient with Marfan’s syndrome

Detalhes bibliográficos
Autor(a) principal: Pivatto Junior, Fernando
Data de Publicação: 2015
Outros Autores: Ramos, Leila Denise Cardoso, Foppa, Murilo, Torres, Felipe Soares
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Institucional da UFRGS
Texto Completo: http://hdl.handle.net/10183/158725
Resumo: Marfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately 1 in 5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive cardiac failure. In this report, we present a patient with a large symptomatic aortic aneurysm and chronic dissection, severe aortic regurgitation and cardiomegaly, treated successfully with resection of the proximal aorta and placement of a mechanic aortic valved graft.
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spelling Pivatto Junior, FernandoRamos, Leila Denise CardosoFoppa, MuriloTorres, Felipe Soares2017-05-30T02:37:08Z20152357-9730http://hdl.handle.net/10183/158725001013006Marfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately 1 in 5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive cardiac failure. In this report, we present a patient with a large symptomatic aortic aneurysm and chronic dissection, severe aortic regurgitation and cardiomegaly, treated successfully with resection of the proximal aorta and placement of a mechanic aortic valved graft.application/pdfengClinical and biomedical research. Porto Alegre. Vol. 35, n. 2, (2015), p. 112-115Síndrome de MarfanAneurisma aórticoDissecaçãoMarfan’s syndromeAortic aneurysmDissectionLarge aortic aneurysm and dissection in a patient with Marfan’s syndromeinfo:eu-repo/semantics/articleinfo:eu-repo/semantics/otherinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/openAccessreponame:Repositório Institucional da UFRGSinstname:Universidade Federal do Rio Grande do Sul (UFRGS)instacron:UFRGSORIGINAL001013006.pdf001013006.pdfTexto completo (inglês)application/pdf1355338http://www.lume.ufrgs.br/bitstream/10183/158725/1/001013006.pdf788a08e1197a255cd099ecc2f1427b72MD51TEXT001013006.pdf.txt001013006.pdf.txtExtracted Texttext/plain14857http://www.lume.ufrgs.br/bitstream/10183/158725/2/001013006.pdf.txt3f888a266ac0cf46329f2d1376e4557eMD5210183/1587252017-05-31 02:35:56.855249oai:www.lume.ufrgs.br:10183/158725Repositório de PublicaçõesPUBhttps://lume.ufrgs.br/oai/requestopendoar:2017-05-31T05:35:56Repositório Institucional da UFRGS - Universidade Federal do Rio Grande do Sul (UFRGS)false
dc.title.pt_BR.fl_str_mv Large aortic aneurysm and dissection in a patient with Marfan’s syndrome
title Large aortic aneurysm and dissection in a patient with Marfan’s syndrome
spellingShingle Large aortic aneurysm and dissection in a patient with Marfan’s syndrome
Pivatto Junior, Fernando
Síndrome de Marfan
Aneurisma aórtico
Dissecação
Marfan’s syndrome
Aortic aneurysm
Dissection
title_short Large aortic aneurysm and dissection in a patient with Marfan’s syndrome
title_full Large aortic aneurysm and dissection in a patient with Marfan’s syndrome
title_fullStr Large aortic aneurysm and dissection in a patient with Marfan’s syndrome
title_full_unstemmed Large aortic aneurysm and dissection in a patient with Marfan’s syndrome
title_sort Large aortic aneurysm and dissection in a patient with Marfan’s syndrome
author Pivatto Junior, Fernando
author_facet Pivatto Junior, Fernando
Ramos, Leila Denise Cardoso
Foppa, Murilo
Torres, Felipe Soares
author_role author
author2 Ramos, Leila Denise Cardoso
Foppa, Murilo
Torres, Felipe Soares
author2_role author
author
author
dc.contributor.author.fl_str_mv Pivatto Junior, Fernando
Ramos, Leila Denise Cardoso
Foppa, Murilo
Torres, Felipe Soares
dc.subject.por.fl_str_mv Síndrome de Marfan
Aneurisma aórtico
Dissecação
topic Síndrome de Marfan
Aneurisma aórtico
Dissecação
Marfan’s syndrome
Aortic aneurysm
Dissection
dc.subject.eng.fl_str_mv Marfan’s syndrome
Aortic aneurysm
Dissection
description Marfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately 1 in 5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive cardiac failure. In this report, we present a patient with a large symptomatic aortic aneurysm and chronic dissection, severe aortic regurgitation and cardiomegaly, treated successfully with resection of the proximal aorta and placement of a mechanic aortic valved graft.
publishDate 2015
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dc.relation.ispartof.pt_BR.fl_str_mv Clinical and biomedical research. Porto Alegre. Vol. 35, n. 2, (2015), p. 112-115
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