Pulmonary alveolar proteinosis and paraneoplastic syndromes: manifestação paraneoplásica?

Detalhes bibliográficos
Autor(a) principal: Pressi, Alexandre
Data de Publicação: 2022
Outros Autores: D. Furtado, André, Chachamovich, Régis, Henn, Lucélia, M. Barreto, Sérgio
Tipo de documento: Artigo
Idioma: por
Título da fonte: Clinical and Biomedical Research
Texto Completo: https://seer.ufrgs.br/index.php/hcpa/article/view/125272
Resumo: Pulmonary alveolar proteinosis (PAP) is a rare condition of unknown etiology. It hasbeen described as the presence of periodic acid-Schiff-positive proteinaceous material(rich in lipids) in the alveoli. Its pathogenesis is believed to consist of an overproductionor surfactant removal defect at the lung. The association of PAP with respiratorydiseases, silicosis, exposure to aluminium or titanium, and hematological neoplasiashas been reported. Here we report two cases of pulmonary alveolar proteinosis andneoplasm diagnosed at the PulmonaryDepartment at Hospital de Clínicas de PortoAlegre.
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spelling Pulmonary alveolar proteinosis and paraneoplastic syndromes: manifestação paraneoplásica?Proteinose alveolar: manifestação paraneoplásica?Proteinose alveolarparaneoplásicapulmonary alveolar proteinosisparaneoplasticPulmonary alveolar proteinosis (PAP) is a rare condition of unknown etiology. It hasbeen described as the presence of periodic acid-Schiff-positive proteinaceous material(rich in lipids) in the alveoli. Its pathogenesis is believed to consist of an overproductionor surfactant removal defect at the lung. The association of PAP with respiratorydiseases, silicosis, exposure to aluminium or titanium, and hematological neoplasiashas been reported. Here we report two cases of pulmonary alveolar proteinosis andneoplasm diagnosed at the PulmonaryDepartment at Hospital de Clínicas de PortoAlegre.A proteinose alveolar (PA) é uma doença rara, de etiologia desconhecida, caracterizadapelo acúmulo alveolar de material proteináceo PAS + (ácido-periódico de Schiff), ricoem fosfolipídios. Acredita-se que a patogênese consiste na superprodução ou defeitona remoção do surfactante ao nível do epitélio pulmonar (10). A PA pode estar associadaa infecções respiratórias (1,2), silicose (3), exposição ao alumínio (4), titânio (5) e aneoplasias hematológicas (6-8). Neste presente artigo, serão apresentados dois relatosde casos de proteinose alveolar e carcinomas diagnosticados no Serviço de Pneumologiado Hospital de Clínicas de Porto Alegre.HCPA/FAMED/UFRGS2022-06-15info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionPeer-reviewed ArticleAvaliado por paresapplication/pdfhttps://seer.ufrgs.br/index.php/hcpa/article/view/125272Clinical & Biomedical Research; Vol. 20 No. 1 (2000): Revista HCPAClinical and Biomedical Research; v. 20 n. 1 (2000): Revista HCPA2357-9730reponame:Clinical and Biomedical Researchinstname:Universidade Federal do Rio Grande do Sul (UFRGS)instacron:UFRGSporhttps://seer.ufrgs.br/index.php/hcpa/article/view/125272/85197http://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessPressi, Alexandre D. Furtado, André Chachamovich, Régis Henn, Lucélia M. Barreto, Sérgio 2022-09-16T16:33:00Zoai:seer.ufrgs.br:article/125272Revistahttps://www.seer.ufrgs.br/index.php/hcpaPUBhttps://seer.ufrgs.br/index.php/hcpa/oai||cbr@hcpa.edu.br2357-97302357-9730opendoar:2022-09-16T16:33Clinical and Biomedical Research - Universidade Federal do Rio Grande do Sul (UFRGS)false
dc.title.none.fl_str_mv Pulmonary alveolar proteinosis and paraneoplastic syndromes: manifestação paraneoplásica?
Proteinose alveolar: manifestação paraneoplásica?
title Pulmonary alveolar proteinosis and paraneoplastic syndromes: manifestação paraneoplásica?
spellingShingle Pulmonary alveolar proteinosis and paraneoplastic syndromes: manifestação paraneoplásica?
Pressi, Alexandre
Proteinose alveolar
paraneoplásica
pulmonary alveolar proteinosis
paraneoplastic
title_short Pulmonary alveolar proteinosis and paraneoplastic syndromes: manifestação paraneoplásica?
title_full Pulmonary alveolar proteinosis and paraneoplastic syndromes: manifestação paraneoplásica?
title_fullStr Pulmonary alveolar proteinosis and paraneoplastic syndromes: manifestação paraneoplásica?
title_full_unstemmed Pulmonary alveolar proteinosis and paraneoplastic syndromes: manifestação paraneoplásica?
title_sort Pulmonary alveolar proteinosis and paraneoplastic syndromes: manifestação paraneoplásica?
author Pressi, Alexandre
author_facet Pressi, Alexandre
D. Furtado, André
Chachamovich, Régis
Henn, Lucélia
M. Barreto, Sérgio
author_role author
author2 D. Furtado, André
Chachamovich, Régis
Henn, Lucélia
M. Barreto, Sérgio
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Pressi, Alexandre
D. Furtado, André
Chachamovich, Régis
Henn, Lucélia
M. Barreto, Sérgio
dc.subject.por.fl_str_mv Proteinose alveolar
paraneoplásica
pulmonary alveolar proteinosis
paraneoplastic
topic Proteinose alveolar
paraneoplásica
pulmonary alveolar proteinosis
paraneoplastic
description Pulmonary alveolar proteinosis (PAP) is a rare condition of unknown etiology. It hasbeen described as the presence of periodic acid-Schiff-positive proteinaceous material(rich in lipids) in the alveoli. Its pathogenesis is believed to consist of an overproductionor surfactant removal defect at the lung. The association of PAP with respiratorydiseases, silicosis, exposure to aluminium or titanium, and hematological neoplasiashas been reported. Here we report two cases of pulmonary alveolar proteinosis andneoplasm diagnosed at the PulmonaryDepartment at Hospital de Clínicas de PortoAlegre.
publishDate 2022
dc.date.none.fl_str_mv 2022-06-15
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
Peer-reviewed Article
Avaliado por pares
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://seer.ufrgs.br/index.php/hcpa/article/view/125272
url https://seer.ufrgs.br/index.php/hcpa/article/view/125272
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://seer.ufrgs.br/index.php/hcpa/article/view/125272/85197
dc.rights.driver.fl_str_mv http://creativecommons.org/licenses/by/4.0
info:eu-repo/semantics/openAccess
rights_invalid_str_mv http://creativecommons.org/licenses/by/4.0
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv HCPA/FAMED/UFRGS
publisher.none.fl_str_mv HCPA/FAMED/UFRGS
dc.source.none.fl_str_mv Clinical & Biomedical Research; Vol. 20 No. 1 (2000): Revista HCPA
Clinical and Biomedical Research; v. 20 n. 1 (2000): Revista HCPA
2357-9730
reponame:Clinical and Biomedical Research
instname:Universidade Federal do Rio Grande do Sul (UFRGS)
instacron:UFRGS
instname_str Universidade Federal do Rio Grande do Sul (UFRGS)
instacron_str UFRGS
institution UFRGS
reponame_str Clinical and Biomedical Research
collection Clinical and Biomedical Research
repository.name.fl_str_mv Clinical and Biomedical Research - Universidade Federal do Rio Grande do Sul (UFRGS)
repository.mail.fl_str_mv ||cbr@hcpa.edu.br
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