Síndrome de Leigh: Relato de caso clínico

Detalhes bibliográficos
Autor(a) principal: Azevedo, Kayque Alves de
Data de Publicação: 2019
Tipo de documento: Trabalho de conclusão de curso
Idioma: por
Título da fonte: Repositório Institucional da UFU
Texto Completo: https://repositorio.ufu.br/handle/123456789/25458
Resumo: AIM: to describe the clinical case of a child diagnosed with Leigh Syndrome, its oral characteristics and to address the importance of dental monitoring, as well as behavioral management in face of the proposed treatment. CLINICAL CASE REPORT: The female patient, aged 7 years and 1 month, diagnosed with Leigh Syndrome, sought the Special Needs Patient Care Clinic for dental follow-up. The patient received the first dental care at 3 years and 6 months of age, being followed at the Dental Hospital of the Federal University of Uberlândia. At the general clinical examination it was observed that the child does not speak and does not walk, presents a tonicity of the muscles of the altered face to the clinical examination. The presence of a mixed dental dentition with the presence of a visible dental biofilm was also observed during the intraoral examination. In addition, it presented caries activity in deciduous and permanent teeth, as well as severe bruxism. The child presented a difficult behavior, requiring the use of active protective stabilization during the consultations. The proposed dental treatment was preventive sealants in healthy teeth, therapeutic sealant in decayed teeth at the level of enamel and restorative treatment in teeth with caries lesion in dentin. The control of the dental biofilm was enhanced in all the consultations, through oral hygiene orientation and supervised brushing with the mother. In relation to bruxism, there was an improvement in muscle hypotonia after initiation of medical treatment with botulinum toxin. CONCLUSION: The case of a child diagnosed with Leigh 's Syndrome was described, presenting the systemic characteristics, and with respect to the oral characteristics. The dental approach is complex in function of the clinical manifestations, the role of the dental surgeon is important in these cases to assist the maintenance of oral health.
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spelling Síndrome de Leigh: Relato de caso clínicoDoença de LeighDoenças do Sistema NervosoAssistência OdontológicaLeigh's DiseaseNervous System DiseasesDental CareCNPQ::CIENCIAS DA SAUDE::ODONTOLOGIA::ODONTOPEDIATRIAAIM: to describe the clinical case of a child diagnosed with Leigh Syndrome, its oral characteristics and to address the importance of dental monitoring, as well as behavioral management in face of the proposed treatment. CLINICAL CASE REPORT: The female patient, aged 7 years and 1 month, diagnosed with Leigh Syndrome, sought the Special Needs Patient Care Clinic for dental follow-up. The patient received the first dental care at 3 years and 6 months of age, being followed at the Dental Hospital of the Federal University of Uberlândia. At the general clinical examination it was observed that the child does not speak and does not walk, presents a tonicity of the muscles of the altered face to the clinical examination. The presence of a mixed dental dentition with the presence of a visible dental biofilm was also observed during the intraoral examination. In addition, it presented caries activity in deciduous and permanent teeth, as well as severe bruxism. The child presented a difficult behavior, requiring the use of active protective stabilization during the consultations. The proposed dental treatment was preventive sealants in healthy teeth, therapeutic sealant in decayed teeth at the level of enamel and restorative treatment in teeth with caries lesion in dentin. The control of the dental biofilm was enhanced in all the consultations, through oral hygiene orientation and supervised brushing with the mother. In relation to bruxism, there was an improvement in muscle hypotonia after initiation of medical treatment with botulinum toxin. CONCLUSION: The case of a child diagnosed with Leigh 's Syndrome was described, presenting the systemic characteristics, and with respect to the oral characteristics. The dental approach is complex in function of the clinical manifestations, the role of the dental surgeon is important in these cases to assist the maintenance of oral health.Trabalho de Conclusão de Curso (Graduação)OBJETIVO: descrever o caso clínico de uma criança diagnosticada com Síndrome de Leigh e abordar a importância do acompanhamento odontológico, bem como o gerenciamento comportamental frente ao tratamento proposto. RELATO DE CASO CLÍNICO: A paciente do sexo feminino com a idade de 7 anos e 1 mês diagnostica- da com a Síndrome de Leigh, procurou a Clínica de Atendimento de Pacientes com Necessidades Especiais para acompanhamento odontológico. A paciente recebeu o primeiro atendimento odontológico aos 3 anos e 6 meses de idade, sendo acompanhada no Hospital Odontológico da Universidade Federal de Uberlândia. Ao exame clínico geral foi observado que a criança não fala e não anda, apresenta tonicidade dos músculos da face alterada ao exame clínico. Ao exame clínico intrabucal verificou-se presença de dentadura mista, com presença de biofilme dental visível, além disso, apresentou atividade de cárie em dentes decíduos e permanentes, bem como bruxismo severo. A criança apresentou um comportamento difícil, sendo necessário o uso de estabilização protetora ativa durante as consultas. O tratamento odontológico proposto foi selantes preventivo em dentes hígidos e tratamento restaurador em dentes com lesão de cárie em dentina. O controle do biofilme dentário era realizado em todas as consultas, por meio de orientação de higiene bucal e escovação supervisionada com a mãe. Em relação ao bruxismo houve uma melhora no quadro de hipotonia muscular após o início de tratamento médico com uso de toxina botulínica. CONCLUSÃO: O caso de uma criança diagnosticada com a Síndrome de Leigh foi descrito, apresentando as característica sistêmicas. A abordagem odontológica é complexa em função das manifestações clínicas, o papel do cirurgião dentista é importante nesses casos para auxiliar a manutenção de saúde bucal.2021-05-29Universidade Federal de UberlândiaBrasilOdontologiaOliveira, Danielly Cunha Araújo Ferreira dehttp://lattes.cnpq.br/1476120663808129Martins, Laíza Fernandeshttp://lattes.cnpq.br/4533605387128081Simamoto Júnior, Paulo Cézarhttp://lattes.cnpq.br/3316615944784016Lima, Felipe Gomes Gonçalves Pereshttp://lattes.cnpq.br/2278821240247375Azevedo, Kayque Alves de2019-06-21T12:55:11Z2019-06-21T12:55:11Z2019-05-29info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/bachelorThesisapplication/pdfAZEVEDO, Kayque Alves de. Síndrome de Leigh: Relato De Caso Clínico. 2019. 20 f. Trabalho de Conclusão de Curso (Graduação em Odontologia) - Universidade Federal de Uberlândia, Uberlândia, 2019https://repositorio.ufu.br/handle/123456789/25458porinfo:eu-repo/semantics/openAccessreponame:Repositório Institucional da UFUinstname:Universidade Federal de Uberlândia (UFU)instacron:UFU2024-08-01T20:36:30Zoai:repositorio.ufu.br:123456789/25458Repositório InstitucionalONGhttp://repositorio.ufu.br/oai/requestdiinf@dirbi.ufu.bropendoar:2024-08-01T20:36:30Repositório Institucional da UFU - Universidade Federal de Uberlândia (UFU)false
dc.title.none.fl_str_mv Síndrome de Leigh: Relato de caso clínico
title Síndrome de Leigh: Relato de caso clínico
spellingShingle Síndrome de Leigh: Relato de caso clínico
Azevedo, Kayque Alves de
Doença de Leigh
Doenças do Sistema Nervoso
Assistência Odontológica
Leigh's Disease
Nervous System Diseases
Dental Care
CNPQ::CIENCIAS DA SAUDE::ODONTOLOGIA::ODONTOPEDIATRIA
title_short Síndrome de Leigh: Relato de caso clínico
title_full Síndrome de Leigh: Relato de caso clínico
title_fullStr Síndrome de Leigh: Relato de caso clínico
title_full_unstemmed Síndrome de Leigh: Relato de caso clínico
title_sort Síndrome de Leigh: Relato de caso clínico
author Azevedo, Kayque Alves de
author_facet Azevedo, Kayque Alves de
author_role author
dc.contributor.none.fl_str_mv Oliveira, Danielly Cunha Araújo Ferreira de
http://lattes.cnpq.br/1476120663808129
Martins, Laíza Fernandes
http://lattes.cnpq.br/4533605387128081
Simamoto Júnior, Paulo Cézar
http://lattes.cnpq.br/3316615944784016
Lima, Felipe Gomes Gonçalves Peres
http://lattes.cnpq.br/2278821240247375
dc.contributor.author.fl_str_mv Azevedo, Kayque Alves de
dc.subject.por.fl_str_mv Doença de Leigh
Doenças do Sistema Nervoso
Assistência Odontológica
Leigh's Disease
Nervous System Diseases
Dental Care
CNPQ::CIENCIAS DA SAUDE::ODONTOLOGIA::ODONTOPEDIATRIA
topic Doença de Leigh
Doenças do Sistema Nervoso
Assistência Odontológica
Leigh's Disease
Nervous System Diseases
Dental Care
CNPQ::CIENCIAS DA SAUDE::ODONTOLOGIA::ODONTOPEDIATRIA
description AIM: to describe the clinical case of a child diagnosed with Leigh Syndrome, its oral characteristics and to address the importance of dental monitoring, as well as behavioral management in face of the proposed treatment. CLINICAL CASE REPORT: The female patient, aged 7 years and 1 month, diagnosed with Leigh Syndrome, sought the Special Needs Patient Care Clinic for dental follow-up. The patient received the first dental care at 3 years and 6 months of age, being followed at the Dental Hospital of the Federal University of Uberlândia. At the general clinical examination it was observed that the child does not speak and does not walk, presents a tonicity of the muscles of the altered face to the clinical examination. The presence of a mixed dental dentition with the presence of a visible dental biofilm was also observed during the intraoral examination. In addition, it presented caries activity in deciduous and permanent teeth, as well as severe bruxism. The child presented a difficult behavior, requiring the use of active protective stabilization during the consultations. The proposed dental treatment was preventive sealants in healthy teeth, therapeutic sealant in decayed teeth at the level of enamel and restorative treatment in teeth with caries lesion in dentin. The control of the dental biofilm was enhanced in all the consultations, through oral hygiene orientation and supervised brushing with the mother. In relation to bruxism, there was an improvement in muscle hypotonia after initiation of medical treatment with botulinum toxin. CONCLUSION: The case of a child diagnosed with Leigh 's Syndrome was described, presenting the systemic characteristics, and with respect to the oral characteristics. The dental approach is complex in function of the clinical manifestations, the role of the dental surgeon is important in these cases to assist the maintenance of oral health.
publishDate 2019
dc.date.none.fl_str_mv 2019-06-21T12:55:11Z
2019-06-21T12:55:11Z
2019-05-29
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/bachelorThesis
format bachelorThesis
status_str publishedVersion
dc.identifier.uri.fl_str_mv AZEVEDO, Kayque Alves de. Síndrome de Leigh: Relato De Caso Clínico. 2019. 20 f. Trabalho de Conclusão de Curso (Graduação em Odontologia) - Universidade Federal de Uberlândia, Uberlândia, 2019
https://repositorio.ufu.br/handle/123456789/25458
identifier_str_mv AZEVEDO, Kayque Alves de. Síndrome de Leigh: Relato De Caso Clínico. 2019. 20 f. Trabalho de Conclusão de Curso (Graduação em Odontologia) - Universidade Federal de Uberlândia, Uberlândia, 2019
url https://repositorio.ufu.br/handle/123456789/25458
dc.language.iso.fl_str_mv por
language por
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Universidade Federal de Uberlândia
Brasil
Odontologia
publisher.none.fl_str_mv Universidade Federal de Uberlândia
Brasil
Odontologia
dc.source.none.fl_str_mv reponame:Repositório Institucional da UFU
instname:Universidade Federal de Uberlândia (UFU)
instacron:UFU
instname_str Universidade Federal de Uberlândia (UFU)
instacron_str UFU
institution UFU
reponame_str Repositório Institucional da UFU
collection Repositório Institucional da UFU
repository.name.fl_str_mv Repositório Institucional da UFU - Universidade Federal de Uberlândia (UFU)
repository.mail.fl_str_mv diinf@dirbi.ufu.br
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