Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report

Detalhes bibliográficos
Autor(a) principal: Oliveira, Daniela Silva
Data de Publicação: 2024
Outros Autores: Miranda, Carina Alves de Oliveira, Bertoldi, Anna Karolliny Costa, Santos, Mariana Aparecida dos, Araújo Junior, Reinaldo Ferreira de, Nascimento Neto, Antônio Félix do, Santo, Aline Soares Monte
Tipo de documento: Artigo
Idioma: por
Título da fonte: Research, Society and Development
Texto Completo: https://rsdjournal.org/index.php/rsd/article/view/44989
Resumo: Ectodermal dysplasia (ED) represents a rare genetic condition characterized by defects in the development of structures originating from the ectoderm. This can result in abnormalities such as the absence or underdevelopment of tissues such as skin, hair, nails, teeth and certain glands, including sebaceous and sweat glands. Often, teeth are sparse and have abnormal shapes in their crowns, and in rarer cases, a complete absence of teeth may occur. The diagnosis of this condition generally occurs in childhood, and dental management may involve the use of dental prostheses, whether partial or complete, and fixed or removable, adapted according to the patient's specific situation. This study aims to discuss the case of a four-year-old boy who was seen at the dental clinic at Universidade Tiradentes, presenting with anhidrotic ED. The application of a removable partial denture for both dental arches was recommended, accompanied by psychological support. The importance of early diagnosis is highlighted to prevent negative impacts on dental aesthetics and occlusion, which can significantly compromise the child's well-being. It is crucial that the dental professional has adequate knowledge about the variants of ED to ensure effective intervention and improve the patient's dental conditions.
id UNIFEI_3b5fef65bed153d6600e3fcba611138d
oai_identifier_str oai:ojs.pkp.sfu.ca:article/44989
network_acronym_str UNIFEI
network_name_str Research, Society and Development
repository_id_str
spelling Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case reportRehabilitación oral protésica en un paciente infantil con displasia ectodérmica: Reporte de casoReabilitação oral protética em paciente infantil com displasia ectodérmica: Relato de casoEctodermal dysplasiaDenture, partial, removablePediatric dentistry.Displasia ectodérmicaDentadura parcial removibleOdontología pediátrica.Displasia ectodérmicaPrótese parcial removívelOdontopediatria.Ectodermal dysplasia (ED) represents a rare genetic condition characterized by defects in the development of structures originating from the ectoderm. This can result in abnormalities such as the absence or underdevelopment of tissues such as skin, hair, nails, teeth and certain glands, including sebaceous and sweat glands. Often, teeth are sparse and have abnormal shapes in their crowns, and in rarer cases, a complete absence of teeth may occur. The diagnosis of this condition generally occurs in childhood, and dental management may involve the use of dental prostheses, whether partial or complete, and fixed or removable, adapted according to the patient's specific situation. This study aims to discuss the case of a four-year-old boy who was seen at the dental clinic at Universidade Tiradentes, presenting with anhidrotic ED. The application of a removable partial denture for both dental arches was recommended, accompanied by psychological support. The importance of early diagnosis is highlighted to prevent negative impacts on dental aesthetics and occlusion, which can significantly compromise the child's well-being. It is crucial that the dental professional has adequate knowledge about the variants of ED to ensure effective intervention and improve the patient's dental conditions.La displasia ectodérmica (DE) representa una rara condición genética caracterizada por defectos en el desarrollo de estructuras que se originan en el ectodermo. Esto puede provocar anomalías como la ausencia o el subdesarrollo de tejidos como la piel, el cabello, las uñas, los dientes y ciertas glándulas, incluidas las sebáceas y sudoríparas. A menudo, los dientes son escasos y tienen formas anormales en sus coronas y, en casos más raros, puede ocurrir una ausencia total de dientes. El diagnóstico de esta afección generalmente ocurre en la infancia, y el manejo odontológico puede implicar el uso de prótesis dentales, ya sean parciales o completas, fijas o removibles, adaptadas según la situación específica del paciente. Este estudio tiene como objetivo discutir el caso de un niño de cuatro años que fue atendido en la clínica dental de la Universidade Tiradentes, presentando DE anhidrótica. Se recomendó la aplicación de una prótesis parcial removible para ambas arcadas dentarias, acompañada de apoyo psicológico. Se destaca la importancia del diagnóstico precoz para prevenir impactos negativos en la estética y la oclusión dental, que pueden comprometer significativamente el bienestar del niño. Es crucial que el profesional odontológico tenga el conocimiento adecuado sobre las variantes de la DE para asegurar una intervención efectiva y mejorar las condiciones dentales del paciente.A displasia ectodérmica (DE) representa uma condição genética rara caracterizada por defeitos no desenvolvimento de estruturas originárias do ectoderma. Isso pode resultar em anormalidades como a ausência ou subdesenvolvimento de tecidos como pele, cabelo, unhas, dentes e certas glândulas, incluindo as sebáceas e sudoríparas. Frequentemente, os dentes são escassos e possuem formas anormais nas suas coroas, e em casos mais raros, pode ocorrer a completa ausência de dentes. O diagnóstico dessa condição geralmente ocorre na infância, e o manejo odontológico pode envolver o uso de próteses dentárias, sejam elas parciais ou totais, e fixas ou removíveis, adaptadas conforme a situação específica do paciente. Este estudo visa discutir o caso de um menino de quatro anos de idade que foi atendido na clínica odontológica da Universidade Tiradentes, apresentando DE anidrótica. Foi recomendada a aplicação de uma prótese parcial removível para as duas arcadas dentárias, acompanhada de suporte psicológico. Ressalta-se a importância do diagnóstico precoce para prevenir impactos negativos na estética dental e na oclusão, os quais podem comprometer significativamente o bem-estar da criança. É crucial que o profissional de odontologia possua conhecimento adequado sobre as variantes da DE para assegurar uma intervenção eficaz e melhorar as condições dentárias do paciente.Research, Society and Development2024-02-12info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://rsdjournal.org/index.php/rsd/article/view/4498910.33448/rsd-v13i2.44989Research, Society and Development; Vol. 13 No. 2; e4213244989Research, Society and Development; Vol. 13 Núm. 2; e4213244989Research, Society and Development; v. 13 n. 2; e42132449892525-3409reponame:Research, Society and Developmentinstname:Universidade Federal de Itajubá (UNIFEI)instacron:UNIFEIporhttps://rsdjournal.org/index.php/rsd/article/view/44989/35922Copyright (c) 2024 Daniela Silva Oliveira; Carina Alves de Oliveira Miranda; Anna Karolliny Costa Bertoldi; Mariana Aparecida dos Santos; Reinaldo Ferreira de Araújo Junior; Antônio Félix do Nascimento Neto; Aline Soares Monte Santohttps://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessOliveira, Daniela Silva Miranda, Carina Alves de Oliveira Bertoldi, Anna Karolliny Costa Santos, Mariana Aparecida dos Araújo Junior, Reinaldo Ferreira de Nascimento Neto, Antônio Félix do Santo, Aline Soares Monte 2024-03-04T09:47:20Zoai:ojs.pkp.sfu.ca:article/44989Revistahttps://rsdjournal.org/index.php/rsd/indexPUBhttps://rsdjournal.org/index.php/rsd/oairsd.articles@gmail.com2525-34092525-3409opendoar:2024-03-04T09:47:20Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)false
dc.title.none.fl_str_mv Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report
Rehabilitación oral protésica en un paciente infantil con displasia ectodérmica: Reporte de caso
Reabilitação oral protética em paciente infantil com displasia ectodérmica: Relato de caso
title Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report
spellingShingle Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report
Oliveira, Daniela Silva
Ectodermal dysplasia
Denture, partial, removable
Pediatric dentistry.
Displasia ectodérmica
Dentadura parcial removible
Odontología pediátrica.
Displasia ectodérmica
Prótese parcial removível
Odontopediatria.
title_short Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report
title_full Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report
title_fullStr Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report
title_full_unstemmed Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report
title_sort Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report
author Oliveira, Daniela Silva
author_facet Oliveira, Daniela Silva
Miranda, Carina Alves de Oliveira
Bertoldi, Anna Karolliny Costa
Santos, Mariana Aparecida dos
Araújo Junior, Reinaldo Ferreira de
Nascimento Neto, Antônio Félix do
Santo, Aline Soares Monte
author_role author
author2 Miranda, Carina Alves de Oliveira
Bertoldi, Anna Karolliny Costa
Santos, Mariana Aparecida dos
Araújo Junior, Reinaldo Ferreira de
Nascimento Neto, Antônio Félix do
Santo, Aline Soares Monte
author2_role author
author
author
author
author
author
dc.contributor.author.fl_str_mv Oliveira, Daniela Silva
Miranda, Carina Alves de Oliveira
Bertoldi, Anna Karolliny Costa
Santos, Mariana Aparecida dos
Araújo Junior, Reinaldo Ferreira de
Nascimento Neto, Antônio Félix do
Santo, Aline Soares Monte
dc.subject.por.fl_str_mv Ectodermal dysplasia
Denture, partial, removable
Pediatric dentistry.
Displasia ectodérmica
Dentadura parcial removible
Odontología pediátrica.
Displasia ectodérmica
Prótese parcial removível
Odontopediatria.
topic Ectodermal dysplasia
Denture, partial, removable
Pediatric dentistry.
Displasia ectodérmica
Dentadura parcial removible
Odontología pediátrica.
Displasia ectodérmica
Prótese parcial removível
Odontopediatria.
description Ectodermal dysplasia (ED) represents a rare genetic condition characterized by defects in the development of structures originating from the ectoderm. This can result in abnormalities such as the absence or underdevelopment of tissues such as skin, hair, nails, teeth and certain glands, including sebaceous and sweat glands. Often, teeth are sparse and have abnormal shapes in their crowns, and in rarer cases, a complete absence of teeth may occur. The diagnosis of this condition generally occurs in childhood, and dental management may involve the use of dental prostheses, whether partial or complete, and fixed or removable, adapted according to the patient's specific situation. This study aims to discuss the case of a four-year-old boy who was seen at the dental clinic at Universidade Tiradentes, presenting with anhidrotic ED. The application of a removable partial denture for both dental arches was recommended, accompanied by psychological support. The importance of early diagnosis is highlighted to prevent negative impacts on dental aesthetics and occlusion, which can significantly compromise the child's well-being. It is crucial that the dental professional has adequate knowledge about the variants of ED to ensure effective intervention and improve the patient's dental conditions.
publishDate 2024
dc.date.none.fl_str_mv 2024-02-12
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://rsdjournal.org/index.php/rsd/article/view/44989
10.33448/rsd-v13i2.44989
url https://rsdjournal.org/index.php/rsd/article/view/44989
identifier_str_mv 10.33448/rsd-v13i2.44989
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://rsdjournal.org/index.php/rsd/article/view/44989/35922
dc.rights.driver.fl_str_mv https://creativecommons.org/licenses/by/4.0
info:eu-repo/semantics/openAccess
rights_invalid_str_mv https://creativecommons.org/licenses/by/4.0
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Research, Society and Development
publisher.none.fl_str_mv Research, Society and Development
dc.source.none.fl_str_mv Research, Society and Development; Vol. 13 No. 2; e4213244989
Research, Society and Development; Vol. 13 Núm. 2; e4213244989
Research, Society and Development; v. 13 n. 2; e4213244989
2525-3409
reponame:Research, Society and Development
instname:Universidade Federal de Itajubá (UNIFEI)
instacron:UNIFEI
instname_str Universidade Federal de Itajubá (UNIFEI)
instacron_str UNIFEI
institution UNIFEI
reponame_str Research, Society and Development
collection Research, Society and Development
repository.name.fl_str_mv Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)
repository.mail.fl_str_mv rsd.articles@gmail.com
_version_ 1797052638069522432