Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report
Autor(a) principal: | |
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Data de Publicação: | 2024 |
Outros Autores: | , , , , , |
Tipo de documento: | Artigo |
Idioma: | por |
Título da fonte: | Research, Society and Development |
Texto Completo: | https://rsdjournal.org/index.php/rsd/article/view/44989 |
Resumo: | Ectodermal dysplasia (ED) represents a rare genetic condition characterized by defects in the development of structures originating from the ectoderm. This can result in abnormalities such as the absence or underdevelopment of tissues such as skin, hair, nails, teeth and certain glands, including sebaceous and sweat glands. Often, teeth are sparse and have abnormal shapes in their crowns, and in rarer cases, a complete absence of teeth may occur. The diagnosis of this condition generally occurs in childhood, and dental management may involve the use of dental prostheses, whether partial or complete, and fixed or removable, adapted according to the patient's specific situation. This study aims to discuss the case of a four-year-old boy who was seen at the dental clinic at Universidade Tiradentes, presenting with anhidrotic ED. The application of a removable partial denture for both dental arches was recommended, accompanied by psychological support. The importance of early diagnosis is highlighted to prevent negative impacts on dental aesthetics and occlusion, which can significantly compromise the child's well-being. It is crucial that the dental professional has adequate knowledge about the variants of ED to ensure effective intervention and improve the patient's dental conditions. |
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Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case reportRehabilitación oral protésica en un paciente infantil con displasia ectodérmica: Reporte de casoReabilitação oral protética em paciente infantil com displasia ectodérmica: Relato de casoEctodermal dysplasiaDenture, partial, removablePediatric dentistry.Displasia ectodérmicaDentadura parcial removibleOdontología pediátrica.Displasia ectodérmicaPrótese parcial removívelOdontopediatria.Ectodermal dysplasia (ED) represents a rare genetic condition characterized by defects in the development of structures originating from the ectoderm. This can result in abnormalities such as the absence or underdevelopment of tissues such as skin, hair, nails, teeth and certain glands, including sebaceous and sweat glands. Often, teeth are sparse and have abnormal shapes in their crowns, and in rarer cases, a complete absence of teeth may occur. The diagnosis of this condition generally occurs in childhood, and dental management may involve the use of dental prostheses, whether partial or complete, and fixed or removable, adapted according to the patient's specific situation. This study aims to discuss the case of a four-year-old boy who was seen at the dental clinic at Universidade Tiradentes, presenting with anhidrotic ED. The application of a removable partial denture for both dental arches was recommended, accompanied by psychological support. The importance of early diagnosis is highlighted to prevent negative impacts on dental aesthetics and occlusion, which can significantly compromise the child's well-being. It is crucial that the dental professional has adequate knowledge about the variants of ED to ensure effective intervention and improve the patient's dental conditions.La displasia ectodérmica (DE) representa una rara condición genética caracterizada por defectos en el desarrollo de estructuras que se originan en el ectodermo. Esto puede provocar anomalías como la ausencia o el subdesarrollo de tejidos como la piel, el cabello, las uñas, los dientes y ciertas glándulas, incluidas las sebáceas y sudoríparas. A menudo, los dientes son escasos y tienen formas anormales en sus coronas y, en casos más raros, puede ocurrir una ausencia total de dientes. El diagnóstico de esta afección generalmente ocurre en la infancia, y el manejo odontológico puede implicar el uso de prótesis dentales, ya sean parciales o completas, fijas o removibles, adaptadas según la situación específica del paciente. Este estudio tiene como objetivo discutir el caso de un niño de cuatro años que fue atendido en la clínica dental de la Universidade Tiradentes, presentando DE anhidrótica. Se recomendó la aplicación de una prótesis parcial removible para ambas arcadas dentarias, acompañada de apoyo psicológico. Se destaca la importancia del diagnóstico precoz para prevenir impactos negativos en la estética y la oclusión dental, que pueden comprometer significativamente el bienestar del niño. Es crucial que el profesional odontológico tenga el conocimiento adecuado sobre las variantes de la DE para asegurar una intervención efectiva y mejorar las condiciones dentales del paciente.A displasia ectodérmica (DE) representa uma condição genética rara caracterizada por defeitos no desenvolvimento de estruturas originárias do ectoderma. Isso pode resultar em anormalidades como a ausência ou subdesenvolvimento de tecidos como pele, cabelo, unhas, dentes e certas glândulas, incluindo as sebáceas e sudoríparas. Frequentemente, os dentes são escassos e possuem formas anormais nas suas coroas, e em casos mais raros, pode ocorrer a completa ausência de dentes. O diagnóstico dessa condição geralmente ocorre na infância, e o manejo odontológico pode envolver o uso de próteses dentárias, sejam elas parciais ou totais, e fixas ou removíveis, adaptadas conforme a situação específica do paciente. Este estudo visa discutir o caso de um menino de quatro anos de idade que foi atendido na clínica odontológica da Universidade Tiradentes, apresentando DE anidrótica. Foi recomendada a aplicação de uma prótese parcial removível para as duas arcadas dentárias, acompanhada de suporte psicológico. Ressalta-se a importância do diagnóstico precoce para prevenir impactos negativos na estética dental e na oclusão, os quais podem comprometer significativamente o bem-estar da criança. É crucial que o profissional de odontologia possua conhecimento adequado sobre as variantes da DE para assegurar uma intervenção eficaz e melhorar as condições dentárias do paciente.Research, Society and Development2024-02-12info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://rsdjournal.org/index.php/rsd/article/view/4498910.33448/rsd-v13i2.44989Research, Society and Development; Vol. 13 No. 2; e4213244989Research, Society and Development; Vol. 13 Núm. 2; e4213244989Research, Society and Development; v. 13 n. 2; e42132449892525-3409reponame:Research, Society and Developmentinstname:Universidade Federal de Itajubá (UNIFEI)instacron:UNIFEIporhttps://rsdjournal.org/index.php/rsd/article/view/44989/35922Copyright (c) 2024 Daniela Silva Oliveira; Carina Alves de Oliveira Miranda; Anna Karolliny Costa Bertoldi; Mariana Aparecida dos Santos; Reinaldo Ferreira de Araújo Junior; Antônio Félix do Nascimento Neto; Aline Soares Monte Santohttps://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessOliveira, Daniela Silva Miranda, Carina Alves de Oliveira Bertoldi, Anna Karolliny Costa Santos, Mariana Aparecida dos Araújo Junior, Reinaldo Ferreira de Nascimento Neto, Antônio Félix do Santo, Aline Soares Monte 2024-03-04T09:47:20Zoai:ojs.pkp.sfu.ca:article/44989Revistahttps://rsdjournal.org/index.php/rsd/indexPUBhttps://rsdjournal.org/index.php/rsd/oairsd.articles@gmail.com2525-34092525-3409opendoar:2024-03-04T09:47:20Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)false |
dc.title.none.fl_str_mv |
Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report Rehabilitación oral protésica en un paciente infantil con displasia ectodérmica: Reporte de caso Reabilitação oral protética em paciente infantil com displasia ectodérmica: Relato de caso |
title |
Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report |
spellingShingle |
Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report Oliveira, Daniela Silva Ectodermal dysplasia Denture, partial, removable Pediatric dentistry. Displasia ectodérmica Dentadura parcial removible Odontología pediátrica. Displasia ectodérmica Prótese parcial removível Odontopediatria. |
title_short |
Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report |
title_full |
Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report |
title_fullStr |
Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report |
title_full_unstemmed |
Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report |
title_sort |
Prosthetic oral rehabilitation in a child patient with ectodermal dysplasia: Case report |
author |
Oliveira, Daniela Silva |
author_facet |
Oliveira, Daniela Silva Miranda, Carina Alves de Oliveira Bertoldi, Anna Karolliny Costa Santos, Mariana Aparecida dos Araújo Junior, Reinaldo Ferreira de Nascimento Neto, Antônio Félix do Santo, Aline Soares Monte |
author_role |
author |
author2 |
Miranda, Carina Alves de Oliveira Bertoldi, Anna Karolliny Costa Santos, Mariana Aparecida dos Araújo Junior, Reinaldo Ferreira de Nascimento Neto, Antônio Félix do Santo, Aline Soares Monte |
author2_role |
author author author author author author |
dc.contributor.author.fl_str_mv |
Oliveira, Daniela Silva Miranda, Carina Alves de Oliveira Bertoldi, Anna Karolliny Costa Santos, Mariana Aparecida dos Araújo Junior, Reinaldo Ferreira de Nascimento Neto, Antônio Félix do Santo, Aline Soares Monte |
dc.subject.por.fl_str_mv |
Ectodermal dysplasia Denture, partial, removable Pediatric dentistry. Displasia ectodérmica Dentadura parcial removible Odontología pediátrica. Displasia ectodérmica Prótese parcial removível Odontopediatria. |
topic |
Ectodermal dysplasia Denture, partial, removable Pediatric dentistry. Displasia ectodérmica Dentadura parcial removible Odontología pediátrica. Displasia ectodérmica Prótese parcial removível Odontopediatria. |
description |
Ectodermal dysplasia (ED) represents a rare genetic condition characterized by defects in the development of structures originating from the ectoderm. This can result in abnormalities such as the absence or underdevelopment of tissues such as skin, hair, nails, teeth and certain glands, including sebaceous and sweat glands. Often, teeth are sparse and have abnormal shapes in their crowns, and in rarer cases, a complete absence of teeth may occur. The diagnosis of this condition generally occurs in childhood, and dental management may involve the use of dental prostheses, whether partial or complete, and fixed or removable, adapted according to the patient's specific situation. This study aims to discuss the case of a four-year-old boy who was seen at the dental clinic at Universidade Tiradentes, presenting with anhidrotic ED. The application of a removable partial denture for both dental arches was recommended, accompanied by psychological support. The importance of early diagnosis is highlighted to prevent negative impacts on dental aesthetics and occlusion, which can significantly compromise the child's well-being. It is crucial that the dental professional has adequate knowledge about the variants of ED to ensure effective intervention and improve the patient's dental conditions. |
publishDate |
2024 |
dc.date.none.fl_str_mv |
2024-02-12 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://rsdjournal.org/index.php/rsd/article/view/44989 10.33448/rsd-v13i2.44989 |
url |
https://rsdjournal.org/index.php/rsd/article/view/44989 |
identifier_str_mv |
10.33448/rsd-v13i2.44989 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
https://rsdjournal.org/index.php/rsd/article/view/44989/35922 |
dc.rights.driver.fl_str_mv |
https://creativecommons.org/licenses/by/4.0 info:eu-repo/semantics/openAccess |
rights_invalid_str_mv |
https://creativecommons.org/licenses/by/4.0 |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Research, Society and Development |
publisher.none.fl_str_mv |
Research, Society and Development |
dc.source.none.fl_str_mv |
Research, Society and Development; Vol. 13 No. 2; e4213244989 Research, Society and Development; Vol. 13 Núm. 2; e4213244989 Research, Society and Development; v. 13 n. 2; e4213244989 2525-3409 reponame:Research, Society and Development instname:Universidade Federal de Itajubá (UNIFEI) instacron:UNIFEI |
instname_str |
Universidade Federal de Itajubá (UNIFEI) |
instacron_str |
UNIFEI |
institution |
UNIFEI |
reponame_str |
Research, Society and Development |
collection |
Research, Society and Development |
repository.name.fl_str_mv |
Research, Society and Development - Universidade Federal de Itajubá (UNIFEI) |
repository.mail.fl_str_mv |
rsd.articles@gmail.com |
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1797052638069522432 |