Cardiac amyloidosis a case report

Detalhes bibliográficos
Autor(a) principal: Destro, Cleonilce Rodrigues de Souza
Data de Publicação: 2020
Outros Autores: Santos, Alan Valladão dos, Rangel, Thiago Alfradique Rodrigues, Destro, Claudinei, Silva, Rose Mary Costa Rosa Andrade, Pereira, Eliane Ramos
Tipo de documento: Artigo
Idioma: por
Título da fonte: Research, Society and Development
Texto Completo: https://rsdjournal.org/index.php/rsd/article/view/2412
Resumo: The authors presented a case of amyloidosis with cardiac involvement in an elderly woman, with a previous history of arterial hypertension, permanent atrial fibrillation and acute heart failure of unknown etiology. The authors presented a case of amyloidosis with cardiac involvement in an elderly woman, with a previous history of arterial hypertension, permanent atrial fibrillation and acute heart failure of unknown etiology. Amyloidosis is a rare and heterogeneous group of diseases, characterized by the extracellular deposit of amyloid protein. There are several types of proteins identified. The most common are tranterritin (TTR) and light chain immunoglobulin (AL), amyloidosis AL, produced in excess by immune cells. Amyloid accumulation can be found anywhere in the body; such as the tongue, heart, adipose tissue, kidney among others. When no underlying disease (secondary amyloidosis) is identified, the term primary or systemic is used. In the latter, the involvement of the heart, with infiltration of the extracellular space by glycoproteins, is very frequent. This work aims to demonstrate the importance of the differential diagnosis of infiltrative cardiomyopathies, in amyloidosis with involvement in other sites such as tongue and cardiac manifestations of the disease, with the diagnosis of transthoracic echocardiography and tongue biopsy diagnosed in a patient at the Cardiology Service of  the Army's Central Hospital- Rio de Janeiro – RJ.
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spelling Cardiac amyloidosis a case reportAMILOIDOSIS CARDIACA UN INFORME DE CASOAmiloidose cardíaca um relato de casoAmiloidoseCardiomiopatia HipertróficaCardiomiopatia RestritivaInsuficiência Cardíaca.AmiloidosisCardiomiopatía HipertróficaCardiomiopatía RestrictivaInsuficiencia Cardíaca.AmyloidosisCardiomyopathyHypertrophicRestrictiveHeart Failure.The authors presented a case of amyloidosis with cardiac involvement in an elderly woman, with a previous history of arterial hypertension, permanent atrial fibrillation and acute heart failure of unknown etiology. The authors presented a case of amyloidosis with cardiac involvement in an elderly woman, with a previous history of arterial hypertension, permanent atrial fibrillation and acute heart failure of unknown etiology. Amyloidosis is a rare and heterogeneous group of diseases, characterized by the extracellular deposit of amyloid protein. There are several types of proteins identified. The most common are tranterritin (TTR) and light chain immunoglobulin (AL), amyloidosis AL, produced in excess by immune cells. Amyloid accumulation can be found anywhere in the body; such as the tongue, heart, adipose tissue, kidney among others. When no underlying disease (secondary amyloidosis) is identified, the term primary or systemic is used. In the latter, the involvement of the heart, with infiltration of the extracellular space by glycoproteins, is very frequent. This work aims to demonstrate the importance of the differential diagnosis of infiltrative cardiomyopathies, in amyloidosis with involvement in other sites such as tongue and cardiac manifestations of the disease, with the diagnosis of transthoracic echocardiography and tongue biopsy diagnosed in a patient at the Cardiology Service of  the Army's Central Hospital- Rio de Janeiro – RJ.Los autores presentan un caso de amiloidosis con afectación cardíaca en una mujer anciana, con antecedentes de hipertensión arterial, fibrilación auricular permanente e insuficiencia cardíaca aguda de etiología desconocida. La amiloidosis es un grupo raro y heterogéneo de enfermedades, caracterizado por el depósito extracelular de proteína amiloide. Hay varios tipos de proteínas identificadas. Las más comumes son la transterritina (TTR) e la inmunoglobulina de cadena ligera (AL), amiloidosis AL, producida en exceso por las células inmunes. La acumulación de amiloide se puede encontrar en cualquier parte del cuerpo; como la lengua, corazón, tejido adiposo, riñón entre otros. Cuando no se identifica una enfermedad subyacente (amiloidosis secundaria), se utiliza el término primario o sistémico. En este último, la participación del corazón, con infiltración del espacio extracelular por las glucoproteínas, es muy frecuente. El objetivo de este trabajo es demostrar la importancia del diagnóstico diferencial de las cardiomiopatías infiltrativas, en la amiloidosis con afectación en otros sitios como la lengua y las manifestaciones cardíacas de la enfermedad, con el diagnóstico de ecocardiografía transtorácica y biopsia de la lengua diagnosticada en un paciente del Servicio de Cardiología del Hospital Central del Ejército - Río de Janeiro – RJ.Os autores apresentam um caso de amiloidose com envolvimento cardíaco em uma mulher idosa, com antecedentes de hipertensão arterial, fibrilação atrial permanente e quadro de insuficiência cardíaca aguda de etiologia desconhecida. A amiloidose constitui um grupo heterogêneo de doenças, de ocorrência rara, caracterizado pelo depósito extracelular da proteína amiloide. Existem vários tipos de proteínas identificadas. As mais comuns são a trantirretina (TTR) e a imunoglobulina de cadeia leve (AL), amiloidose AL, produzida em excesso por células imunológicas. O acúmulo amiloide pode ser encontrado em qualquer local do organismo; como a língua, coração, tecido adiposo, rim entre outros. Quando não é identificada doença subjacente (amiloidose secundária), usa-se o termo primária ou sistêmica. Nesta última, o envolvimento do coração, com infiltração do espaço extracelular por glicoproteínas, é muito frequente. Este trabalho tem como objetivo demonstrar a importância do diagnóstico diferencial das cardiomiopatias infiltrativas, na amiloidose com acometimento em outros sítios como língua e manifestações cardíacas da doença tendo como diagnóstico o ecocardiograma transtorácico e a biopsia de língua diagnosticada em uma paciente do Serviço de Cardiologia do Hospital Central do Exército –Rio de Janeiro –RJ.Research, Society and Development2020-03-06info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://rsdjournal.org/index.php/rsd/article/view/241210.33448/rsd-v9i3.2412Research, Society and Development; Vol. 9 No. 3; e174932412Research, Society and Development; Vol. 9 Núm. 3; e174932412Research, Society and Development; v. 9 n. 3; e1749324122525-3409reponame:Research, Society and Developmentinstname:Universidade Federal de Itajubá (UNIFEI)instacron:UNIFEIporhttps://rsdjournal.org/index.php/rsd/article/view/2412/2053Copyright (c) 2019 Cleonilce Rodrigues de Souza Destro, Alan Valladão dos Santos, Thiago Alfradique Rodrigues Rangel, Claudinei Destro, Rose Mary Costa Rosa Andrade Silva, Eliane Ramos Pereirainfo:eu-repo/semantics/openAccessDestro, Cleonilce Rodrigues de SouzaSantos, Alan Valladão dosRangel, Thiago Alfradique RodriguesDestro, ClaudineiSilva, Rose Mary Costa Rosa AndradePereira, Eliane Ramos2020-08-20T18:07:57Zoai:ojs.pkp.sfu.ca:article/2412Revistahttps://rsdjournal.org/index.php/rsd/indexPUBhttps://rsdjournal.org/index.php/rsd/oairsd.articles@gmail.com2525-34092525-3409opendoar:2024-01-17T09:27:02.556728Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)false
dc.title.none.fl_str_mv Cardiac amyloidosis a case report
AMILOIDOSIS CARDIACA UN INFORME DE CASO
Amiloidose cardíaca um relato de caso
title Cardiac amyloidosis a case report
spellingShingle Cardiac amyloidosis a case report
Destro, Cleonilce Rodrigues de Souza
Amiloidose
Cardiomiopatia Hipertrófica
Cardiomiopatia Restritiva
Insuficiência Cardíaca.
Amiloidosis
Cardiomiopatía Hipertrófica
Cardiomiopatía Restrictiva
Insuficiencia Cardíaca.
Amyloidosis
Cardiomyopathy
Hypertrophic
Restrictive
Heart Failure.
title_short Cardiac amyloidosis a case report
title_full Cardiac amyloidosis a case report
title_fullStr Cardiac amyloidosis a case report
title_full_unstemmed Cardiac amyloidosis a case report
title_sort Cardiac amyloidosis a case report
author Destro, Cleonilce Rodrigues de Souza
author_facet Destro, Cleonilce Rodrigues de Souza
Santos, Alan Valladão dos
Rangel, Thiago Alfradique Rodrigues
Destro, Claudinei
Silva, Rose Mary Costa Rosa Andrade
Pereira, Eliane Ramos
author_role author
author2 Santos, Alan Valladão dos
Rangel, Thiago Alfradique Rodrigues
Destro, Claudinei
Silva, Rose Mary Costa Rosa Andrade
Pereira, Eliane Ramos
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Destro, Cleonilce Rodrigues de Souza
Santos, Alan Valladão dos
Rangel, Thiago Alfradique Rodrigues
Destro, Claudinei
Silva, Rose Mary Costa Rosa Andrade
Pereira, Eliane Ramos
dc.subject.por.fl_str_mv Amiloidose
Cardiomiopatia Hipertrófica
Cardiomiopatia Restritiva
Insuficiência Cardíaca.
Amiloidosis
Cardiomiopatía Hipertrófica
Cardiomiopatía Restrictiva
Insuficiencia Cardíaca.
Amyloidosis
Cardiomyopathy
Hypertrophic
Restrictive
Heart Failure.
topic Amiloidose
Cardiomiopatia Hipertrófica
Cardiomiopatia Restritiva
Insuficiência Cardíaca.
Amiloidosis
Cardiomiopatía Hipertrófica
Cardiomiopatía Restrictiva
Insuficiencia Cardíaca.
Amyloidosis
Cardiomyopathy
Hypertrophic
Restrictive
Heart Failure.
description The authors presented a case of amyloidosis with cardiac involvement in an elderly woman, with a previous history of arterial hypertension, permanent atrial fibrillation and acute heart failure of unknown etiology. The authors presented a case of amyloidosis with cardiac involvement in an elderly woman, with a previous history of arterial hypertension, permanent atrial fibrillation and acute heart failure of unknown etiology. Amyloidosis is a rare and heterogeneous group of diseases, characterized by the extracellular deposit of amyloid protein. There are several types of proteins identified. The most common are tranterritin (TTR) and light chain immunoglobulin (AL), amyloidosis AL, produced in excess by immune cells. Amyloid accumulation can be found anywhere in the body; such as the tongue, heart, adipose tissue, kidney among others. When no underlying disease (secondary amyloidosis) is identified, the term primary or systemic is used. In the latter, the involvement of the heart, with infiltration of the extracellular space by glycoproteins, is very frequent. This work aims to demonstrate the importance of the differential diagnosis of infiltrative cardiomyopathies, in amyloidosis with involvement in other sites such as tongue and cardiac manifestations of the disease, with the diagnosis of transthoracic echocardiography and tongue biopsy diagnosed in a patient at the Cardiology Service of  the Army's Central Hospital- Rio de Janeiro – RJ.
publishDate 2020
dc.date.none.fl_str_mv 2020-03-06
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://rsdjournal.org/index.php/rsd/article/view/2412
10.33448/rsd-v9i3.2412
url https://rsdjournal.org/index.php/rsd/article/view/2412
identifier_str_mv 10.33448/rsd-v9i3.2412
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://rsdjournal.org/index.php/rsd/article/view/2412/2053
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Research, Society and Development
publisher.none.fl_str_mv Research, Society and Development
dc.source.none.fl_str_mv Research, Society and Development; Vol. 9 No. 3; e174932412
Research, Society and Development; Vol. 9 Núm. 3; e174932412
Research, Society and Development; v. 9 n. 3; e174932412
2525-3409
reponame:Research, Society and Development
instname:Universidade Federal de Itajubá (UNIFEI)
instacron:UNIFEI
instname_str Universidade Federal de Itajubá (UNIFEI)
instacron_str UNIFEI
institution UNIFEI
reponame_str Research, Society and Development
collection Research, Society and Development
repository.name.fl_str_mv Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)
repository.mail.fl_str_mv rsd.articles@gmail.com
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