Cardiac amyloidosis a case report
Autor(a) principal: | |
---|---|
Data de Publicação: | 2020 |
Outros Autores: | , , , , |
Tipo de documento: | Artigo |
Idioma: | por |
Título da fonte: | Research, Society and Development |
Texto Completo: | https://rsdjournal.org/index.php/rsd/article/view/2412 |
Resumo: | The authors presented a case of amyloidosis with cardiac involvement in an elderly woman, with a previous history of arterial hypertension, permanent atrial fibrillation and acute heart failure of unknown etiology. The authors presented a case of amyloidosis with cardiac involvement in an elderly woman, with a previous history of arterial hypertension, permanent atrial fibrillation and acute heart failure of unknown etiology. Amyloidosis is a rare and heterogeneous group of diseases, characterized by the extracellular deposit of amyloid protein. There are several types of proteins identified. The most common are tranterritin (TTR) and light chain immunoglobulin (AL), amyloidosis AL, produced in excess by immune cells. Amyloid accumulation can be found anywhere in the body; such as the tongue, heart, adipose tissue, kidney among others. When no underlying disease (secondary amyloidosis) is identified, the term primary or systemic is used. In the latter, the involvement of the heart, with infiltration of the extracellular space by glycoproteins, is very frequent. This work aims to demonstrate the importance of the differential diagnosis of infiltrative cardiomyopathies, in amyloidosis with involvement in other sites such as tongue and cardiac manifestations of the disease, with the diagnosis of transthoracic echocardiography and tongue biopsy diagnosed in a patient at the Cardiology Service of the Army's Central Hospital- Rio de Janeiro – RJ. |
id |
UNIFEI_d583a76ae5b87959cec56a4073d536a0 |
---|---|
oai_identifier_str |
oai:ojs.pkp.sfu.ca:article/2412 |
network_acronym_str |
UNIFEI |
network_name_str |
Research, Society and Development |
repository_id_str |
|
spelling |
Cardiac amyloidosis a case reportAMILOIDOSIS CARDIACA UN INFORME DE CASOAmiloidose cardíaca um relato de casoAmiloidoseCardiomiopatia HipertróficaCardiomiopatia RestritivaInsuficiência Cardíaca.AmiloidosisCardiomiopatía HipertróficaCardiomiopatía RestrictivaInsuficiencia Cardíaca.AmyloidosisCardiomyopathyHypertrophicRestrictiveHeart Failure.The authors presented a case of amyloidosis with cardiac involvement in an elderly woman, with a previous history of arterial hypertension, permanent atrial fibrillation and acute heart failure of unknown etiology. The authors presented a case of amyloidosis with cardiac involvement in an elderly woman, with a previous history of arterial hypertension, permanent atrial fibrillation and acute heart failure of unknown etiology. Amyloidosis is a rare and heterogeneous group of diseases, characterized by the extracellular deposit of amyloid protein. There are several types of proteins identified. The most common are tranterritin (TTR) and light chain immunoglobulin (AL), amyloidosis AL, produced in excess by immune cells. Amyloid accumulation can be found anywhere in the body; such as the tongue, heart, adipose tissue, kidney among others. When no underlying disease (secondary amyloidosis) is identified, the term primary or systemic is used. In the latter, the involvement of the heart, with infiltration of the extracellular space by glycoproteins, is very frequent. This work aims to demonstrate the importance of the differential diagnosis of infiltrative cardiomyopathies, in amyloidosis with involvement in other sites such as tongue and cardiac manifestations of the disease, with the diagnosis of transthoracic echocardiography and tongue biopsy diagnosed in a patient at the Cardiology Service of the Army's Central Hospital- Rio de Janeiro – RJ.Los autores presentan un caso de amiloidosis con afectación cardíaca en una mujer anciana, con antecedentes de hipertensión arterial, fibrilación auricular permanente e insuficiencia cardíaca aguda de etiología desconocida. La amiloidosis es un grupo raro y heterogéneo de enfermedades, caracterizado por el depósito extracelular de proteína amiloide. Hay varios tipos de proteínas identificadas. Las más comumes son la transterritina (TTR) e la inmunoglobulina de cadena ligera (AL), amiloidosis AL, producida en exceso por las células inmunes. La acumulación de amiloide se puede encontrar en cualquier parte del cuerpo; como la lengua, corazón, tejido adiposo, riñón entre otros. Cuando no se identifica una enfermedad subyacente (amiloidosis secundaria), se utiliza el término primario o sistémico. En este último, la participación del corazón, con infiltración del espacio extracelular por las glucoproteínas, es muy frecuente. El objetivo de este trabajo es demostrar la importancia del diagnóstico diferencial de las cardiomiopatías infiltrativas, en la amiloidosis con afectación en otros sitios como la lengua y las manifestaciones cardíacas de la enfermedad, con el diagnóstico de ecocardiografía transtorácica y biopsia de la lengua diagnosticada en un paciente del Servicio de Cardiología del Hospital Central del Ejército - Río de Janeiro – RJ.Os autores apresentam um caso de amiloidose com envolvimento cardíaco em uma mulher idosa, com antecedentes de hipertensão arterial, fibrilação atrial permanente e quadro de insuficiência cardíaca aguda de etiologia desconhecida. A amiloidose constitui um grupo heterogêneo de doenças, de ocorrência rara, caracterizado pelo depósito extracelular da proteína amiloide. Existem vários tipos de proteínas identificadas. As mais comuns são a trantirretina (TTR) e a imunoglobulina de cadeia leve (AL), amiloidose AL, produzida em excesso por células imunológicas. O acúmulo amiloide pode ser encontrado em qualquer local do organismo; como a língua, coração, tecido adiposo, rim entre outros. Quando não é identificada doença subjacente (amiloidose secundária), usa-se o termo primária ou sistêmica. Nesta última, o envolvimento do coração, com infiltração do espaço extracelular por glicoproteínas, é muito frequente. Este trabalho tem como objetivo demonstrar a importância do diagnóstico diferencial das cardiomiopatias infiltrativas, na amiloidose com acometimento em outros sítios como língua e manifestações cardíacas da doença tendo como diagnóstico o ecocardiograma transtorácico e a biopsia de língua diagnosticada em uma paciente do Serviço de Cardiologia do Hospital Central do Exército –Rio de Janeiro –RJ.Research, Society and Development2020-03-06info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://rsdjournal.org/index.php/rsd/article/view/241210.33448/rsd-v9i3.2412Research, Society and Development; Vol. 9 No. 3; e174932412Research, Society and Development; Vol. 9 Núm. 3; e174932412Research, Society and Development; v. 9 n. 3; e1749324122525-3409reponame:Research, Society and Developmentinstname:Universidade Federal de Itajubá (UNIFEI)instacron:UNIFEIporhttps://rsdjournal.org/index.php/rsd/article/view/2412/2053Copyright (c) 2019 Cleonilce Rodrigues de Souza Destro, Alan Valladão dos Santos, Thiago Alfradique Rodrigues Rangel, Claudinei Destro, Rose Mary Costa Rosa Andrade Silva, Eliane Ramos Pereirainfo:eu-repo/semantics/openAccessDestro, Cleonilce Rodrigues de SouzaSantos, Alan Valladão dosRangel, Thiago Alfradique RodriguesDestro, ClaudineiSilva, Rose Mary Costa Rosa AndradePereira, Eliane Ramos2020-08-20T18:07:57Zoai:ojs.pkp.sfu.ca:article/2412Revistahttps://rsdjournal.org/index.php/rsd/indexPUBhttps://rsdjournal.org/index.php/rsd/oairsd.articles@gmail.com2525-34092525-3409opendoar:2024-01-17T09:27:02.556728Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)false |
dc.title.none.fl_str_mv |
Cardiac amyloidosis a case report AMILOIDOSIS CARDIACA UN INFORME DE CASO Amiloidose cardíaca um relato de caso |
title |
Cardiac amyloidosis a case report |
spellingShingle |
Cardiac amyloidosis a case report Destro, Cleonilce Rodrigues de Souza Amiloidose Cardiomiopatia Hipertrófica Cardiomiopatia Restritiva Insuficiência Cardíaca. Amiloidosis Cardiomiopatía Hipertrófica Cardiomiopatía Restrictiva Insuficiencia Cardíaca. Amyloidosis Cardiomyopathy Hypertrophic Restrictive Heart Failure. |
title_short |
Cardiac amyloidosis a case report |
title_full |
Cardiac amyloidosis a case report |
title_fullStr |
Cardiac amyloidosis a case report |
title_full_unstemmed |
Cardiac amyloidosis a case report |
title_sort |
Cardiac amyloidosis a case report |
author |
Destro, Cleonilce Rodrigues de Souza |
author_facet |
Destro, Cleonilce Rodrigues de Souza Santos, Alan Valladão dos Rangel, Thiago Alfradique Rodrigues Destro, Claudinei Silva, Rose Mary Costa Rosa Andrade Pereira, Eliane Ramos |
author_role |
author |
author2 |
Santos, Alan Valladão dos Rangel, Thiago Alfradique Rodrigues Destro, Claudinei Silva, Rose Mary Costa Rosa Andrade Pereira, Eliane Ramos |
author2_role |
author author author author author |
dc.contributor.author.fl_str_mv |
Destro, Cleonilce Rodrigues de Souza Santos, Alan Valladão dos Rangel, Thiago Alfradique Rodrigues Destro, Claudinei Silva, Rose Mary Costa Rosa Andrade Pereira, Eliane Ramos |
dc.subject.por.fl_str_mv |
Amiloidose Cardiomiopatia Hipertrófica Cardiomiopatia Restritiva Insuficiência Cardíaca. Amiloidosis Cardiomiopatía Hipertrófica Cardiomiopatía Restrictiva Insuficiencia Cardíaca. Amyloidosis Cardiomyopathy Hypertrophic Restrictive Heart Failure. |
topic |
Amiloidose Cardiomiopatia Hipertrófica Cardiomiopatia Restritiva Insuficiência Cardíaca. Amiloidosis Cardiomiopatía Hipertrófica Cardiomiopatía Restrictiva Insuficiencia Cardíaca. Amyloidosis Cardiomyopathy Hypertrophic Restrictive Heart Failure. |
description |
The authors presented a case of amyloidosis with cardiac involvement in an elderly woman, with a previous history of arterial hypertension, permanent atrial fibrillation and acute heart failure of unknown etiology. The authors presented a case of amyloidosis with cardiac involvement in an elderly woman, with a previous history of arterial hypertension, permanent atrial fibrillation and acute heart failure of unknown etiology. Amyloidosis is a rare and heterogeneous group of diseases, characterized by the extracellular deposit of amyloid protein. There are several types of proteins identified. The most common are tranterritin (TTR) and light chain immunoglobulin (AL), amyloidosis AL, produced in excess by immune cells. Amyloid accumulation can be found anywhere in the body; such as the tongue, heart, adipose tissue, kidney among others. When no underlying disease (secondary amyloidosis) is identified, the term primary or systemic is used. In the latter, the involvement of the heart, with infiltration of the extracellular space by glycoproteins, is very frequent. This work aims to demonstrate the importance of the differential diagnosis of infiltrative cardiomyopathies, in amyloidosis with involvement in other sites such as tongue and cardiac manifestations of the disease, with the diagnosis of transthoracic echocardiography and tongue biopsy diagnosed in a patient at the Cardiology Service of the Army's Central Hospital- Rio de Janeiro – RJ. |
publishDate |
2020 |
dc.date.none.fl_str_mv |
2020-03-06 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://rsdjournal.org/index.php/rsd/article/view/2412 10.33448/rsd-v9i3.2412 |
url |
https://rsdjournal.org/index.php/rsd/article/view/2412 |
identifier_str_mv |
10.33448/rsd-v9i3.2412 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
https://rsdjournal.org/index.php/rsd/article/view/2412/2053 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Research, Society and Development |
publisher.none.fl_str_mv |
Research, Society and Development |
dc.source.none.fl_str_mv |
Research, Society and Development; Vol. 9 No. 3; e174932412 Research, Society and Development; Vol. 9 Núm. 3; e174932412 Research, Society and Development; v. 9 n. 3; e174932412 2525-3409 reponame:Research, Society and Development instname:Universidade Federal de Itajubá (UNIFEI) instacron:UNIFEI |
instname_str |
Universidade Federal de Itajubá (UNIFEI) |
instacron_str |
UNIFEI |
institution |
UNIFEI |
reponame_str |
Research, Society and Development |
collection |
Research, Society and Development |
repository.name.fl_str_mv |
Research, Society and Development - Universidade Federal de Itajubá (UNIFEI) |
repository.mail.fl_str_mv |
rsd.articles@gmail.com |
_version_ |
1797052640396312576 |