Blastic Plasmacytoid Dendritic cell neoplasm: Case report / Neoplasia de células Dendríticas Plasmocitóides Blásticas: Relato de caso

• Autor(a) principal: Sallum, Michel Hamui
• Data de Publicação: 2021
• Outros Autores: de Souza, Helio Moraes, de Vito, Fernanda Bernadelli, da Silva, Vanessa Afonso
• Tipo de documento: Artigo
• Idioma: por
• Título da fonte: Revista Veras
• Texto Completo: https://ojs.brazilianjournals.com.br/ojs/index.php/BRJD/article/view/30772
• topic: Blastic Plasmacytoid Dendritic Cell Neoplasm; Bone Marrow Cell Transplantation; Hematologic Malignancy.

Blastic plasmacytoid dendritic cell neoplasm is a rare neoplasm of hematopoietic origin with poor clinical evolution. Here we report a case of a patient who presented with blastic plamacytoid dendritic cell neoplasm with cutaneous and nodal involvement. The patient was successfully treated with polychemotherapy followed by allogeneic bone marrow transplantation. The case described reaches, until the moment of this publication, disease-free survival of 32 months, superior to that described in the literature, which is from 12 to 18 months. We also did a brief review of the literature on this disease, including aspects relevant to diagnosis, treatment and prognosis.