Adult onset sporadic ataxias: a diagnostic challenge
Autor(a) principal: | |
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Data de Publicação: | 2014 |
Outros Autores: | , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Arquivos de neuro-psiquiatria (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2014000300232 |
Resumo: | Patients with adult onset non-familial progressive ataxia are classified in sporadic ataxia group. There are several disease categories that may manifest with sporadic ataxia: toxic causes, immune-mediated ataxias, vitamin deficiency, infectious diseases, degenerative disorders and even genetic conditions. Considering heterogeneity in the clinical spectrum of sporadic ataxias, the correct diagnosis remains a clinical challenge. In this review, the different disease categories that lead to sporadic ataxia with adult onset are discussed with special emphasis on their clinical and neuroimaging features, and diagnostic criteria. |
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Adult onset sporadic ataxias: a diagnostic challengeataxiasporadic ataxiaclinical featuresdiagnostic criteriaPatients with adult onset non-familial progressive ataxia are classified in sporadic ataxia group. There are several disease categories that may manifest with sporadic ataxia: toxic causes, immune-mediated ataxias, vitamin deficiency, infectious diseases, degenerative disorders and even genetic conditions. Considering heterogeneity in the clinical spectrum of sporadic ataxias, the correct diagnosis remains a clinical challenge. In this review, the different disease categories that lead to sporadic ataxia with adult onset are discussed with special emphasis on their clinical and neuroimaging features, and diagnostic criteria.Academia Brasileira de Neurologia - ABNEURO2014-03-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2014000300232Arquivos de Neuro-Psiquiatria v.72 n.3 2014reponame:Arquivos de neuro-psiquiatria (Online)instname:Academia Brasileira de Neurologiainstacron:ABNEURO10.1590/0004-282X20130242info:eu-repo/semantics/openAccessBarsottini,Orlando Graziani PovoasAlbuquerque,Marcus Vinicius Cristino deBraga Neto,PedroPedroso,José Luizeng2014-03-28T00:00:00Zoai:scielo:S0004-282X2014000300232Revistahttp://www.scielo.br/anphttps://old.scielo.br/oai/scielo-oai.php||revista.arquivos@abneuro.org1678-42270004-282Xopendoar:2014-03-28T00:00Arquivos de neuro-psiquiatria (Online) - Academia Brasileira de Neurologiafalse |
dc.title.none.fl_str_mv |
Adult onset sporadic ataxias: a diagnostic challenge |
title |
Adult onset sporadic ataxias: a diagnostic challenge |
spellingShingle |
Adult onset sporadic ataxias: a diagnostic challenge Barsottini,Orlando Graziani Povoas ataxia sporadic ataxia clinical features diagnostic criteria |
title_short |
Adult onset sporadic ataxias: a diagnostic challenge |
title_full |
Adult onset sporadic ataxias: a diagnostic challenge |
title_fullStr |
Adult onset sporadic ataxias: a diagnostic challenge |
title_full_unstemmed |
Adult onset sporadic ataxias: a diagnostic challenge |
title_sort |
Adult onset sporadic ataxias: a diagnostic challenge |
author |
Barsottini,Orlando Graziani Povoas |
author_facet |
Barsottini,Orlando Graziani Povoas Albuquerque,Marcus Vinicius Cristino de Braga Neto,Pedro Pedroso,José Luiz |
author_role |
author |
author2 |
Albuquerque,Marcus Vinicius Cristino de Braga Neto,Pedro Pedroso,José Luiz |
author2_role |
author author author |
dc.contributor.author.fl_str_mv |
Barsottini,Orlando Graziani Povoas Albuquerque,Marcus Vinicius Cristino de Braga Neto,Pedro Pedroso,José Luiz |
dc.subject.por.fl_str_mv |
ataxia sporadic ataxia clinical features diagnostic criteria |
topic |
ataxia sporadic ataxia clinical features diagnostic criteria |
description |
Patients with adult onset non-familial progressive ataxia are classified in sporadic ataxia group. There are several disease categories that may manifest with sporadic ataxia: toxic causes, immune-mediated ataxias, vitamin deficiency, infectious diseases, degenerative disorders and even genetic conditions. Considering heterogeneity in the clinical spectrum of sporadic ataxias, the correct diagnosis remains a clinical challenge. In this review, the different disease categories that lead to sporadic ataxia with adult onset are discussed with special emphasis on their clinical and neuroimaging features, and diagnostic criteria. |
publishDate |
2014 |
dc.date.none.fl_str_mv |
2014-03-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2014000300232 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2014000300232 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/0004-282X20130242 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Academia Brasileira de Neurologia - ABNEURO |
publisher.none.fl_str_mv |
Academia Brasileira de Neurologia - ABNEURO |
dc.source.none.fl_str_mv |
Arquivos de Neuro-Psiquiatria v.72 n.3 2014 reponame:Arquivos de neuro-psiquiatria (Online) instname:Academia Brasileira de Neurologia instacron:ABNEURO |
instname_str |
Academia Brasileira de Neurologia |
instacron_str |
ABNEURO |
institution |
ABNEURO |
reponame_str |
Arquivos de neuro-psiquiatria (Online) |
collection |
Arquivos de neuro-psiquiatria (Online) |
repository.name.fl_str_mv |
Arquivos de neuro-psiquiatria (Online) - Academia Brasileira de Neurologia |
repository.mail.fl_str_mv |
||revista.arquivos@abneuro.org |
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1754212776131166208 |