Adult onset sporadic ataxias: a diagnostic challenge

Detalhes bibliográficos
Autor(a) principal: Barsottini,Orlando Graziani Povoas
Data de Publicação: 2014
Outros Autores: Albuquerque,Marcus Vinicius Cristino de, Braga Neto,Pedro, Pedroso,José Luiz
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Arquivos de neuro-psiquiatria (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2014000300232
Resumo: Patients with adult onset non-familial progressive ataxia are classified in sporadic ataxia group. There are several disease categories that may manifest with sporadic ataxia: toxic causes, immune-mediated ataxias, vitamin deficiency, infectious diseases, degenerative disorders and even genetic conditions. Considering heterogeneity in the clinical spectrum of sporadic ataxias, the correct diagnosis remains a clinical challenge. In this review, the different disease categories that lead to sporadic ataxia with adult onset are discussed with special emphasis on their clinical and neuroimaging features, and diagnostic criteria.
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spelling Adult onset sporadic ataxias: a diagnostic challengeataxiasporadic ataxiaclinical featuresdiagnostic criteriaPatients with adult onset non-familial progressive ataxia are classified in sporadic ataxia group. There are several disease categories that may manifest with sporadic ataxia: toxic causes, immune-mediated ataxias, vitamin deficiency, infectious diseases, degenerative disorders and even genetic conditions. Considering heterogeneity in the clinical spectrum of sporadic ataxias, the correct diagnosis remains a clinical challenge. In this review, the different disease categories that lead to sporadic ataxia with adult onset are discussed with special emphasis on their clinical and neuroimaging features, and diagnostic criteria.Academia Brasileira de Neurologia - ABNEURO2014-03-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2014000300232Arquivos de Neuro-Psiquiatria v.72 n.3 2014reponame:Arquivos de neuro-psiquiatria (Online)instname:Academia Brasileira de Neurologiainstacron:ABNEURO10.1590/0004-282X20130242info:eu-repo/semantics/openAccessBarsottini,Orlando Graziani PovoasAlbuquerque,Marcus Vinicius Cristino deBraga Neto,PedroPedroso,José Luizeng2014-03-28T00:00:00Zoai:scielo:S0004-282X2014000300232Revistahttp://www.scielo.br/anphttps://old.scielo.br/oai/scielo-oai.php||revista.arquivos@abneuro.org1678-42270004-282Xopendoar:2014-03-28T00:00Arquivos de neuro-psiquiatria (Online) - Academia Brasileira de Neurologiafalse
dc.title.none.fl_str_mv Adult onset sporadic ataxias: a diagnostic challenge
title Adult onset sporadic ataxias: a diagnostic challenge
spellingShingle Adult onset sporadic ataxias: a diagnostic challenge
Barsottini,Orlando Graziani Povoas
ataxia
sporadic ataxia
clinical features
diagnostic criteria
title_short Adult onset sporadic ataxias: a diagnostic challenge
title_full Adult onset sporadic ataxias: a diagnostic challenge
title_fullStr Adult onset sporadic ataxias: a diagnostic challenge
title_full_unstemmed Adult onset sporadic ataxias: a diagnostic challenge
title_sort Adult onset sporadic ataxias: a diagnostic challenge
author Barsottini,Orlando Graziani Povoas
author_facet Barsottini,Orlando Graziani Povoas
Albuquerque,Marcus Vinicius Cristino de
Braga Neto,Pedro
Pedroso,José Luiz
author_role author
author2 Albuquerque,Marcus Vinicius Cristino de
Braga Neto,Pedro
Pedroso,José Luiz
author2_role author
author
author
dc.contributor.author.fl_str_mv Barsottini,Orlando Graziani Povoas
Albuquerque,Marcus Vinicius Cristino de
Braga Neto,Pedro
Pedroso,José Luiz
dc.subject.por.fl_str_mv ataxia
sporadic ataxia
clinical features
diagnostic criteria
topic ataxia
sporadic ataxia
clinical features
diagnostic criteria
description Patients with adult onset non-familial progressive ataxia are classified in sporadic ataxia group. There are several disease categories that may manifest with sporadic ataxia: toxic causes, immune-mediated ataxias, vitamin deficiency, infectious diseases, degenerative disorders and even genetic conditions. Considering heterogeneity in the clinical spectrum of sporadic ataxias, the correct diagnosis remains a clinical challenge. In this review, the different disease categories that lead to sporadic ataxia with adult onset are discussed with special emphasis on their clinical and neuroimaging features, and diagnostic criteria.
publishDate 2014
dc.date.none.fl_str_mv 2014-03-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
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status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2014000300232
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2014000300232
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/0004-282X20130242
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Academia Brasileira de Neurologia - ABNEURO
publisher.none.fl_str_mv Academia Brasileira de Neurologia - ABNEURO
dc.source.none.fl_str_mv Arquivos de Neuro-Psiquiatria v.72 n.3 2014
reponame:Arquivos de neuro-psiquiatria (Online)
instname:Academia Brasileira de Neurologia
instacron:ABNEURO
instname_str Academia Brasileira de Neurologia
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reponame_str Arquivos de neuro-psiquiatria (Online)
collection Arquivos de neuro-psiquiatria (Online)
repository.name.fl_str_mv Arquivos de neuro-psiquiatria (Online) - Academia Brasileira de Neurologia
repository.mail.fl_str_mv ||revista.arquivos@abneuro.org
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