Clinical and morphological aspects in children affected with hydranencephaly: an overview / Aspectos clínicos e morfológicos em crianças afetadas com hidranencefalia: uma visão geral
Autor(a) principal: | |
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Data de Publicação: | 2020 |
Outros Autores: | , , , , , , |
Tipo de documento: | Artigo |
Idioma: | por |
Título da fonte: | Brazilian Applied Science Review |
Texto Completo: | https://ojs.brazilianjournals.com.br/ojs/index.php/BASR/article/view/10581 |
Resumo: | Objective: To demonstrate a general view on the clinical and morphological aspects in children with Hydranencephaly. Methodology: This is a study that uses the systematic review as a method. Data collection took place in September 2019 through the SciELO and EBESCO databases with the following descriptors:”hemihydranencephaly”, '' Rare diseases '', 'malformation'. For the selection of articles, the following were used: inclusion criteria: articles in Portuguese, English, full articles that portray the theme related to the literature review and articles published and indexed in the referred databases in the period from 2007 to 2019. Results and Discussion: Hydranencephaly is a condition that in Most are lethal with exceptions, this malformation of the central nervous system occurs after the closure of the neural tube, defined as total or partial absence of cerebral hemispheres, the entire cortex that would be irrigated by the carotids is nonexistent. however, the brainstem, diencephalon and part of the occipital cortex, irrigated by the posterior cerebral arteries, are formed and may exhibit electrical activity. In some cases they have severe neurological sequelae, psychomotor disability, visual impairment, deafness and progressive macroencephaly. Conclusion: Patients with this rare condition are subjected to several surgeries and antibiotic therapies for prolonged periods in an attempt to provide the best survival for the patient. irrigated by the posterior cerebral arteries, are formed and may exhibit electrical activity. In some cases they have severe neurological sequelae, psychomotor disability, visual impairment, deafness and progressive macroencephaly. Conclusion: Patients with this rare condition are subjected to several surgeries and antibiotic therapies for prolonged periods in an attempt to provide the best survival for the patient. irrigated by the posterior cerebral arteries, are formed and may exhibit electrical activity. In some cases they have severe neurological sequelae, psychomotor disability, visual impairment, deafness and progressive macroencephaly. Conclusion: Patients with this rare condition are subjected to several surgeries and antibiotic therapies for prolonged periods in an attempt to provide the best survival for the patient. |
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Clinical and morphological aspects in children affected with hydranencephaly: an overview / Aspectos clínicos e morfológicos em crianças afetadas com hidranencefalia: uma visão geralhemihydrananencephalymalformationrare diseases.Objective: To demonstrate a general view on the clinical and morphological aspects in children with Hydranencephaly. Methodology: This is a study that uses the systematic review as a method. Data collection took place in September 2019 through the SciELO and EBESCO databases with the following descriptors:”hemihydranencephaly”, '' Rare diseases '', 'malformation'. For the selection of articles, the following were used: inclusion criteria: articles in Portuguese, English, full articles that portray the theme related to the literature review and articles published and indexed in the referred databases in the period from 2007 to 2019. Results and Discussion: Hydranencephaly is a condition that in Most are lethal with exceptions, this malformation of the central nervous system occurs after the closure of the neural tube, defined as total or partial absence of cerebral hemispheres, the entire cortex that would be irrigated by the carotids is nonexistent. however, the brainstem, diencephalon and part of the occipital cortex, irrigated by the posterior cerebral arteries, are formed and may exhibit electrical activity. In some cases they have severe neurological sequelae, psychomotor disability, visual impairment, deafness and progressive macroencephaly. Conclusion: Patients with this rare condition are subjected to several surgeries and antibiotic therapies for prolonged periods in an attempt to provide the best survival for the patient. irrigated by the posterior cerebral arteries, are formed and may exhibit electrical activity. In some cases they have severe neurological sequelae, psychomotor disability, visual impairment, deafness and progressive macroencephaly. Conclusion: Patients with this rare condition are subjected to several surgeries and antibiotic therapies for prolonged periods in an attempt to provide the best survival for the patient. irrigated by the posterior cerebral arteries, are formed and may exhibit electrical activity. In some cases they have severe neurological sequelae, psychomotor disability, visual impairment, deafness and progressive macroencephaly. Conclusion: Patients with this rare condition are subjected to several surgeries and antibiotic therapies for prolonged periods in an attempt to provide the best survival for the patient. Brazilian Journals Publicações de Periódicos e Editora Ltda.2020-05-25info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://ojs.brazilianjournals.com.br/ojs/index.php/BASR/article/view/1058110.34115/basrv4n3-056Brazilian Applied Science Review; Vol. 4 No. 3 (2020); 1458-1468Brazilian Applied Science Review; v. 4 n. 3 (2020); 1458-14682595-36212595-362110.34115/basr.v4i3reponame:Brazilian Applied Science Reviewinstname:Brazilian Journals Publicações de Periódicos e Editora Ltdainstacron:FIEPporhttps://ojs.brazilianjournals.com.br/ojs/index.php/BASR/article/view/10581/8840Copyright (c) 2020 Brazilian Applied Science Reviewinfo:eu-repo/semantics/openAccessSantos, Simone Martins dosBarbosa, Michael Gabriel AgustinhoSilva, Joas Francisco daSilva, Emanuela Ingridy DaSouza, Ana Paula Barbosa deSilva, Anderson José daCarvalho, Thays Wany SilvaLins, Tatiana Acioli2020-06-29T18:19:04Zoai:ojs2.ojs.brazilianjournals.com.br:article/10581Revistahttps://www.brazilianjournals.com/index.php/BASRPRIhttps://ojs.brazilianjournals.com.br/ojs/index.php/BASR/oaibrazilianasr@yahoo.com || brazilianasr@yahoo.com2595-36212595-3621opendoar:2020-06-29T18:19:04Brazilian Applied Science Review - Brazilian Journals Publicações de Periódicos e Editora Ltdafalse |
dc.title.none.fl_str_mv |
Clinical and morphological aspects in children affected with hydranencephaly: an overview / Aspectos clínicos e morfológicos em crianças afetadas com hidranencefalia: uma visão geral |
title |
Clinical and morphological aspects in children affected with hydranencephaly: an overview / Aspectos clínicos e morfológicos em crianças afetadas com hidranencefalia: uma visão geral |
spellingShingle |
Clinical and morphological aspects in children affected with hydranencephaly: an overview / Aspectos clínicos e morfológicos em crianças afetadas com hidranencefalia: uma visão geral Santos, Simone Martins dos hemihydrananencephaly malformation rare diseases. |
title_short |
Clinical and morphological aspects in children affected with hydranencephaly: an overview / Aspectos clínicos e morfológicos em crianças afetadas com hidranencefalia: uma visão geral |
title_full |
Clinical and morphological aspects in children affected with hydranencephaly: an overview / Aspectos clínicos e morfológicos em crianças afetadas com hidranencefalia: uma visão geral |
title_fullStr |
Clinical and morphological aspects in children affected with hydranencephaly: an overview / Aspectos clínicos e morfológicos em crianças afetadas com hidranencefalia: uma visão geral |
title_full_unstemmed |
Clinical and morphological aspects in children affected with hydranencephaly: an overview / Aspectos clínicos e morfológicos em crianças afetadas com hidranencefalia: uma visão geral |
title_sort |
Clinical and morphological aspects in children affected with hydranencephaly: an overview / Aspectos clínicos e morfológicos em crianças afetadas com hidranencefalia: uma visão geral |
author |
Santos, Simone Martins dos |
author_facet |
Santos, Simone Martins dos Barbosa, Michael Gabriel Agustinho Silva, Joas Francisco da Silva, Emanuela Ingridy Da Souza, Ana Paula Barbosa de Silva, Anderson José da Carvalho, Thays Wany Silva Lins, Tatiana Acioli |
author_role |
author |
author2 |
Barbosa, Michael Gabriel Agustinho Silva, Joas Francisco da Silva, Emanuela Ingridy Da Souza, Ana Paula Barbosa de Silva, Anderson José da Carvalho, Thays Wany Silva Lins, Tatiana Acioli |
author2_role |
author author author author author author author |
dc.contributor.author.fl_str_mv |
Santos, Simone Martins dos Barbosa, Michael Gabriel Agustinho Silva, Joas Francisco da Silva, Emanuela Ingridy Da Souza, Ana Paula Barbosa de Silva, Anderson José da Carvalho, Thays Wany Silva Lins, Tatiana Acioli |
dc.subject.por.fl_str_mv |
hemihydrananencephaly malformation rare diseases. |
topic |
hemihydrananencephaly malformation rare diseases. |
description |
Objective: To demonstrate a general view on the clinical and morphological aspects in children with Hydranencephaly. Methodology: This is a study that uses the systematic review as a method. Data collection took place in September 2019 through the SciELO and EBESCO databases with the following descriptors:”hemihydranencephaly”, '' Rare diseases '', 'malformation'. For the selection of articles, the following were used: inclusion criteria: articles in Portuguese, English, full articles that portray the theme related to the literature review and articles published and indexed in the referred databases in the period from 2007 to 2019. Results and Discussion: Hydranencephaly is a condition that in Most are lethal with exceptions, this malformation of the central nervous system occurs after the closure of the neural tube, defined as total or partial absence of cerebral hemispheres, the entire cortex that would be irrigated by the carotids is nonexistent. however, the brainstem, diencephalon and part of the occipital cortex, irrigated by the posterior cerebral arteries, are formed and may exhibit electrical activity. In some cases they have severe neurological sequelae, psychomotor disability, visual impairment, deafness and progressive macroencephaly. Conclusion: Patients with this rare condition are subjected to several surgeries and antibiotic therapies for prolonged periods in an attempt to provide the best survival for the patient. irrigated by the posterior cerebral arteries, are formed and may exhibit electrical activity. In some cases they have severe neurological sequelae, psychomotor disability, visual impairment, deafness and progressive macroencephaly. Conclusion: Patients with this rare condition are subjected to several surgeries and antibiotic therapies for prolonged periods in an attempt to provide the best survival for the patient. irrigated by the posterior cerebral arteries, are formed and may exhibit electrical activity. In some cases they have severe neurological sequelae, psychomotor disability, visual impairment, deafness and progressive macroencephaly. Conclusion: Patients with this rare condition are subjected to several surgeries and antibiotic therapies for prolonged periods in an attempt to provide the best survival for the patient. |
publishDate |
2020 |
dc.date.none.fl_str_mv |
2020-05-25 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://ojs.brazilianjournals.com.br/ojs/index.php/BASR/article/view/10581 10.34115/basrv4n3-056 |
url |
https://ojs.brazilianjournals.com.br/ojs/index.php/BASR/article/view/10581 |
identifier_str_mv |
10.34115/basrv4n3-056 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
https://ojs.brazilianjournals.com.br/ojs/index.php/BASR/article/view/10581/8840 |
dc.rights.driver.fl_str_mv |
Copyright (c) 2020 Brazilian Applied Science Review info:eu-repo/semantics/openAccess |
rights_invalid_str_mv |
Copyright (c) 2020 Brazilian Applied Science Review |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Brazilian Journals Publicações de Periódicos e Editora Ltda. |
publisher.none.fl_str_mv |
Brazilian Journals Publicações de Periódicos e Editora Ltda. |
dc.source.none.fl_str_mv |
Brazilian Applied Science Review; Vol. 4 No. 3 (2020); 1458-1468 Brazilian Applied Science Review; v. 4 n. 3 (2020); 1458-1468 2595-3621 2595-3621 10.34115/basr.v4i3 reponame:Brazilian Applied Science Review instname:Brazilian Journals Publicações de Periódicos e Editora Ltda instacron:FIEP |
instname_str |
Brazilian Journals Publicações de Periódicos e Editora Ltda |
instacron_str |
FIEP |
institution |
FIEP |
reponame_str |
Brazilian Applied Science Review |
collection |
Brazilian Applied Science Review |
repository.name.fl_str_mv |
Brazilian Applied Science Review - Brazilian Journals Publicações de Periódicos e Editora Ltda |
repository.mail.fl_str_mv |
brazilianasr@yahoo.com || brazilianasr@yahoo.com |
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1797240006718259200 |