Sickle cell anemia: delayed diagnosis in Bahia, Brazil-a largely Afro-descendant population
| Autor(a) principal: | |
|---|---|
| Data de Publicação: | 2011 |
| Outros Autores: | , , , |
| Tipo de documento: | Artigo |
| Idioma: | eng |
| Título da fonte: | Repositório Institucional da FIOCRUZ (ARCA) |
| Texto Completo: | https://www.arca.fiocruz.br/handle/icict/19086 |
Resumo: | Hematology and Hemotherapy Center of Bahia. Salvador, BA, Brazil |
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Zanette, Angela Maria DiasGonçalves, Marilda de SouzaBahia, Regina Célia SantosNogueira, Luciana Vasconcelos AraujoArruda, Sérgio Marcos2017-06-01T16:11:58Z2017-06-01T16:11:58Z2011ZANETTE, A. M. D. et al. Sickle cell anemia: delayed diagnosis in Bahia, Brazil--a largely Afro-descendant population. Ethnicity & Disease, v. 21, n. 2, p. 243-247, 2011.1049-510Xhttps://www.arca.fiocruz.br/handle/icict/19086engInternational Society on Hypertension in BlacksAnemia falciformeDoença falciformeHemoglobinopatiaDiagnóstico atrasadoSickle Cell AnemiaSickle Cell DiseaseHemoglobinopathyDelayed DiagnosisAnemia falciformeDoença falciformeHemoglobinopatiasDiagnóstico tardioSickle cell anemia: delayed diagnosis in Bahia, Brazil-a largely Afro-descendant populationinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleHematology and Hemotherapy Center of Bahia. Salvador, BA, BrazilFundação Oswaldo Cruz. Centro de Pesquisas Gonçalo Moniz. Salvador, BA, BrasilHematology and Hemotherapy Center of Bahia. Salvador, BA, BrazilHematology and Hemotherapy Center of Bahia. Salvador, BA, BrazilFundação Oswaldo Cruz. Centro de Pesquisas Gonçalo Moniz. Salvador, BA, BrasilHemoglobinopathies are the most common genetic disorders in the world and include sickle cell anemia (SCA), which is a public health problem in Brazil. Nevertheless, the disease is highly unknown among health professionals, and delayed diagnosis constitutes an important cause of concern for caretakers of SCA patients. The purpose of this study was to compare the clinical and laboratory history of SCA patients whose diagnosis was established during the first year of life to those of other SCA patients who had delayed SCA diagnosis. Demographic, clinical, and laboratory data were all reviewed from 99 steady-state SCA patients who were followed in a public hematology and hemotherapy clinic in Salvador, Brazil. The patients were aged $12 years and attended the outpatient unit at least once from November 2008 to June 2009. The data were analyzed in 2010. For all patients, the mean age (6 SD) at diagnosis was 12.7(6 12.1) years, ranging from 0 to 47 years. Mean age was higher in patients whose SCA diagnosis was established after age 5 (32.9 6 11.9 years, P5.005). Increased unconjugated bilirubin, stroke and splenic sequestration were more prevalent in patients who were diagnosed in the first year of life (P5.043, .024 and .026 respectively).info:eu-repo/semantics/openAccessreponame:Repositório Institucional da FIOCRUZ (ARCA)instname:Fundação Oswaldo Cruz (FIOCRUZ)instacron:FIOCRUZLICENSElicense.txtlicense.txttext/plain; charset=utf-82991https://www.arca.fiocruz.br/bitstream/icict/19086/1/license.txt5a560609d32a3863062d77ff32785d58MD51ORIGINALZanette AM Sickle cell anemia....pdfZanette AM Sickle cell anemia....pdfapplication/pdf186145https://www.arca.fiocruz.br/bitstream/icict/19086/2/Zanette%20AM%20Sickle%20cell%20anemia....pdf86700d9dde1a04f35b2912dadd1e57eaMD52TEXTZanette AM Sickle cell anemia....pdf.txtZanette AM Sickle cell anemia....pdf.txtExtracted texttext/plain26269https://www.arca.fiocruz.br/bitstream/icict/19086/3/Zanette%20AM%20Sickle%20cell%20anemia....pdf.txtec45bdc53b6467b8d0277ba1f04991d4MD53icict/190862023-03-15 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| dc.title.pt_BR.fl_str_mv |
Sickle cell anemia: delayed diagnosis in Bahia, Brazil-a largely Afro-descendant population |
| title |
Sickle cell anemia: delayed diagnosis in Bahia, Brazil-a largely Afro-descendant population |
| spellingShingle |
Sickle cell anemia: delayed diagnosis in Bahia, Brazil-a largely Afro-descendant population Zanette, Angela Maria Dias Anemia falciforme Doença falciforme Hemoglobinopatia Diagnóstico atrasado Sickle Cell Anemia Sickle Cell Disease Hemoglobinopathy Delayed Diagnosis Anemia falciforme Doença falciforme Hemoglobinopatias Diagnóstico tardio |
| title_short |
Sickle cell anemia: delayed diagnosis in Bahia, Brazil-a largely Afro-descendant population |
| title_full |
Sickle cell anemia: delayed diagnosis in Bahia, Brazil-a largely Afro-descendant population |
| title_fullStr |
Sickle cell anemia: delayed diagnosis in Bahia, Brazil-a largely Afro-descendant population |
| title_full_unstemmed |
Sickle cell anemia: delayed diagnosis in Bahia, Brazil-a largely Afro-descendant population |
| title_sort |
Sickle cell anemia: delayed diagnosis in Bahia, Brazil-a largely Afro-descendant population |
| author |
Zanette, Angela Maria Dias |
| author_facet |
Zanette, Angela Maria Dias Gonçalves, Marilda de Souza Bahia, Regina Célia Santos Nogueira, Luciana Vasconcelos Araujo Arruda, Sérgio Marcos |
| author_role |
author |
| author2 |
Gonçalves, Marilda de Souza Bahia, Regina Célia Santos Nogueira, Luciana Vasconcelos Araujo Arruda, Sérgio Marcos |
| author2_role |
author author author author |
| dc.contributor.author.fl_str_mv |
Zanette, Angela Maria Dias Gonçalves, Marilda de Souza Bahia, Regina Célia Santos Nogueira, Luciana Vasconcelos Araujo Arruda, Sérgio Marcos |
| dc.subject.other.pt_BR.fl_str_mv |
Anemia falciforme Doença falciforme Hemoglobinopatia Diagnóstico atrasado |
| topic |
Anemia falciforme Doença falciforme Hemoglobinopatia Diagnóstico atrasado Sickle Cell Anemia Sickle Cell Disease Hemoglobinopathy Delayed Diagnosis Anemia falciforme Doença falciforme Hemoglobinopatias Diagnóstico tardio |
| dc.subject.en.pt_BR.fl_str_mv |
Sickle Cell Anemia Sickle Cell Disease Hemoglobinopathy Delayed Diagnosis |
| dc.subject.decs.pt_BR.fl_str_mv |
Anemia falciforme Doença falciforme Hemoglobinopatias Diagnóstico tardio |
| description |
Hematology and Hemotherapy Center of Bahia. Salvador, BA, Brazil |
| publishDate |
2011 |
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2011 |
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2017-06-01T16:11:58Z |
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2017-06-01T16:11:58Z |
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info:eu-repo/semantics/publishedVersion |
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info:eu-repo/semantics/article |
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article |
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ZANETTE, A. M. D. et al. Sickle cell anemia: delayed diagnosis in Bahia, Brazil--a largely Afro-descendant population. Ethnicity & Disease, v. 21, n. 2, p. 243-247, 2011. |
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https://www.arca.fiocruz.br/handle/icict/19086 |
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1049-510X |
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ZANETTE, A. M. D. et al. Sickle cell anemia: delayed diagnosis in Bahia, Brazil--a largely Afro-descendant population. Ethnicity & Disease, v. 21, n. 2, p. 243-247, 2011. 1049-510X |
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International Society on Hypertension in Blacks |
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International Society on Hypertension in Blacks |
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