Pregnancy in Marfan Syndrome – Two Case Reports
Autor(a) principal: | |
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Data de Publicação: | 2016 |
Outros Autores: | , |
Tipo de documento: | Artigo |
Idioma: | por |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | http://hdl.handle.net/10400.17/4154 |
Resumo: | Marfan syndrome is a connective tissue disorder, autosomal dominant, which affects multiple organ systems, namely the cardiovascular, ocular and skeletal. Morbidity and mortality result primarily from aortic and cardiac complications including dilatation, dissection and rupture of the aorta. As a result, pregnancy in women with the Marfan syndrome has an increased risk. Main causes of complications are related with hemodynamic and hormonal modifications caused by pregnancy. The approach to pregnancy in patients with this syndrome is challenging and deserves special care. A multidisciplinary surveillance plan should be developed with support from cardiology, maternal fetal medicine, anesthesiology, genetics and pediatrics. |
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Pregnancy in Marfan Syndrome – Two Case ReportsGravidez na Síndrome de Marfan – dois casos clínicosMarfan SyndromePregnancyAortic dilatationMAC OBSMarfan syndrome is a connective tissue disorder, autosomal dominant, which affects multiple organ systems, namely the cardiovascular, ocular and skeletal. Morbidity and mortality result primarily from aortic and cardiac complications including dilatation, dissection and rupture of the aorta. As a result, pregnancy in women with the Marfan syndrome has an increased risk. Main causes of complications are related with hemodynamic and hormonal modifications caused by pregnancy. The approach to pregnancy in patients with this syndrome is challenging and deserves special care. A multidisciplinary surveillance plan should be developed with support from cardiology, maternal fetal medicine, anesthesiology, genetics and pediatrics.Federação das Sociedades Portuguesas de Obstetrícia e GinecologiaRepositório do Centro Hospitalar Universitário de Lisboa Central, EPEIsidro Amaral, PCampos, APatrício, L2022-07-28T09:16:17Z20162016-01-01T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttp://hdl.handle.net/10400.17/4154porActa Obstet Ginecol Port 2016;10(1):74-77info:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2023-03-10T09:45:35Zoai:repositorio.chlc.min-saude.pt:10400.17/4154Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T17:21:29.575283Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
Pregnancy in Marfan Syndrome – Two Case Reports Gravidez na Síndrome de Marfan – dois casos clínicos |
title |
Pregnancy in Marfan Syndrome – Two Case Reports |
spellingShingle |
Pregnancy in Marfan Syndrome – Two Case Reports Isidro Amaral, P Marfan Syndrome Pregnancy Aortic dilatation MAC OBS |
title_short |
Pregnancy in Marfan Syndrome – Two Case Reports |
title_full |
Pregnancy in Marfan Syndrome – Two Case Reports |
title_fullStr |
Pregnancy in Marfan Syndrome – Two Case Reports |
title_full_unstemmed |
Pregnancy in Marfan Syndrome – Two Case Reports |
title_sort |
Pregnancy in Marfan Syndrome – Two Case Reports |
author |
Isidro Amaral, P |
author_facet |
Isidro Amaral, P Campos, A Patrício, L |
author_role |
author |
author2 |
Campos, A Patrício, L |
author2_role |
author author |
dc.contributor.none.fl_str_mv |
Repositório do Centro Hospitalar Universitário de Lisboa Central, EPE |
dc.contributor.author.fl_str_mv |
Isidro Amaral, P Campos, A Patrício, L |
dc.subject.por.fl_str_mv |
Marfan Syndrome Pregnancy Aortic dilatation MAC OBS |
topic |
Marfan Syndrome Pregnancy Aortic dilatation MAC OBS |
description |
Marfan syndrome is a connective tissue disorder, autosomal dominant, which affects multiple organ systems, namely the cardiovascular, ocular and skeletal. Morbidity and mortality result primarily from aortic and cardiac complications including dilatation, dissection and rupture of the aorta. As a result, pregnancy in women with the Marfan syndrome has an increased risk. Main causes of complications are related with hemodynamic and hormonal modifications caused by pregnancy. The approach to pregnancy in patients with this syndrome is challenging and deserves special care. A multidisciplinary surveillance plan should be developed with support from cardiology, maternal fetal medicine, anesthesiology, genetics and pediatrics. |
publishDate |
2016 |
dc.date.none.fl_str_mv |
2016 2016-01-01T00:00:00Z 2022-07-28T09:16:17Z |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://hdl.handle.net/10400.17/4154 |
url |
http://hdl.handle.net/10400.17/4154 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
Acta Obstet Ginecol Port 2016;10(1):74-77 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Federação das Sociedades Portuguesas de Obstetrícia e Ginecologia |
publisher.none.fl_str_mv |
Federação das Sociedades Portuguesas de Obstetrícia e Ginecologia |
dc.source.none.fl_str_mv |
reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
instname_str |
Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
instacron_str |
RCAAP |
institution |
RCAAP |
reponame_str |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
collection |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
repository.name.fl_str_mv |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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1799131310117093376 |