Turner Syndrome - an unusual cause for aortic dissection
Autor(a) principal: | |
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Data de Publicação: | 2020 |
Outros Autores: | , , , , , , , |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | http://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-706X2020000400322 |
Resumo: | Abstract Turner syndrome (TS) is a disorder of female development with cardinal features of short stature and congenital cardiovascular defects. Congenital or acquired cardiological problems occur commonly in TS, being potentially progressive and responsible for severe complications, such as aortic dissection in young women. Accordingly, we describe a case of type A aortic dissection occurring in a woman with TS, highlighting the need to prioritize investigation in those patients to avoid a catastrophic aortic scenario. |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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7160 |
spelling |
Turner Syndrome - an unusual cause for aortic dissectionTurner SyndromeAortic DissectionX ChromosomeBicuspid Aortic ValveCoarctationAbstract Turner syndrome (TS) is a disorder of female development with cardinal features of short stature and congenital cardiovascular defects. Congenital or acquired cardiological problems occur commonly in TS, being potentially progressive and responsible for severe complications, such as aortic dissection in young women. Accordingly, we describe a case of type A aortic dissection occurring in a woman with TS, highlighting the need to prioritize investigation in those patients to avoid a catastrophic aortic scenario.Sociedade Portuguesa de Angiologia e Cirurgia Vascular2020-12-01info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/reporttext/htmlhttp://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-706X2020000400322Angiologia e Cirurgia Vascular v.16 n.4 2020reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPenghttp://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-706X2020000400322Augusto,RitaCampos,JacintaCoelho,AndreiaCoelho,NunoPinto,EveliseSemião,CarolinaRibeiro,JoãoBrandão,DanielCanedo,Alexandrainfo:eu-repo/semantics/openAccess2024-02-06T17:23:00Zoai:scielo:S1646-706X2020000400322Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-20T02:29:27.984828Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
Turner Syndrome - an unusual cause for aortic dissection |
title |
Turner Syndrome - an unusual cause for aortic dissection |
spellingShingle |
Turner Syndrome - an unusual cause for aortic dissection Augusto,Rita Turner Syndrome Aortic Dissection X Chromosome Bicuspid Aortic Valve Coarctation |
title_short |
Turner Syndrome - an unusual cause for aortic dissection |
title_full |
Turner Syndrome - an unusual cause for aortic dissection |
title_fullStr |
Turner Syndrome - an unusual cause for aortic dissection |
title_full_unstemmed |
Turner Syndrome - an unusual cause for aortic dissection |
title_sort |
Turner Syndrome - an unusual cause for aortic dissection |
author |
Augusto,Rita |
author_facet |
Augusto,Rita Campos,Jacinta Coelho,Andreia Coelho,Nuno Pinto,Evelise Semião,Carolina Ribeiro,João Brandão,Daniel Canedo,Alexandra |
author_role |
author |
author2 |
Campos,Jacinta Coelho,Andreia Coelho,Nuno Pinto,Evelise Semião,Carolina Ribeiro,João Brandão,Daniel Canedo,Alexandra |
author2_role |
author author author author author author author author |
dc.contributor.author.fl_str_mv |
Augusto,Rita Campos,Jacinta Coelho,Andreia Coelho,Nuno Pinto,Evelise Semião,Carolina Ribeiro,João Brandão,Daniel Canedo,Alexandra |
dc.subject.por.fl_str_mv |
Turner Syndrome Aortic Dissection X Chromosome Bicuspid Aortic Valve Coarctation |
topic |
Turner Syndrome Aortic Dissection X Chromosome Bicuspid Aortic Valve Coarctation |
description |
Abstract Turner syndrome (TS) is a disorder of female development with cardinal features of short stature and congenital cardiovascular defects. Congenital or acquired cardiological problems occur commonly in TS, being potentially progressive and responsible for severe complications, such as aortic dissection in young women. Accordingly, we describe a case of type A aortic dissection occurring in a woman with TS, highlighting the need to prioritize investigation in those patients to avoid a catastrophic aortic scenario. |
publishDate |
2020 |
dc.date.none.fl_str_mv |
2020-12-01 |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-706X2020000400322 |
url |
http://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-706X2020000400322 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
http://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-706X2020000400322 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade Portuguesa de Angiologia e Cirurgia Vascular |
publisher.none.fl_str_mv |
Sociedade Portuguesa de Angiologia e Cirurgia Vascular |
dc.source.none.fl_str_mv |
Angiologia e Cirurgia Vascular v.16 n.4 2020 reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
instname_str |
Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
instacron_str |
RCAAP |
institution |
RCAAP |
reponame_str |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
collection |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
repository.name.fl_str_mv |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
repository.mail.fl_str_mv |
|
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1799137361713430528 |