Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review
Autor(a) principal: | |
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Data de Publicação: | 2014 |
Outros Autores: | , , , |
Tipo de documento: | Artigo |
Idioma: | por |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274 |
Resumo: | Hepatic lesions represent a common finding in clinical practice. Bile ducts hamartomas, also known as Von Meyenburg complex, are benign hepatic malformations composed of small dilated cystic bile ducts lined by fibrous stroma. They represent a rare and asymptomatic clinic-pathological entity. Imagiological findings are variable, and may present as multiple small scattered lesions, or rarely as a single nodule. These findings may resemble secondary lesions and, although benign, there are cases of progression to colangiocarcinoma. Thus it is important to include this complex in the differential diagnoses of focal hepatic lesions, being necessary a detailed investigation for their differentiation. This case represents an atypical presentation of a rare and not frequently considered entity in clinical practice. |
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Von Meyenburg Complex or Liver Metastasis? Case Report and Literature ReviewComplexo de Von Meyenburg ou Metástases Hepáticas? Caso Clínico e Revisão da LiteraturaHepatic lesions represent a common finding in clinical practice. Bile ducts hamartomas, also known as Von Meyenburg complex, are benign hepatic malformations composed of small dilated cystic bile ducts lined by fibrous stroma. They represent a rare and asymptomatic clinic-pathological entity. Imagiological findings are variable, and may present as multiple small scattered lesions, or rarely as a single nodule. These findings may resemble secondary lesions and, although benign, there are cases of progression to colangiocarcinoma. Thus it is important to include this complex in the differential diagnoses of focal hepatic lesions, being necessary a detailed investigation for their differentiation. This case represents an atypical presentation of a rare and not frequently considered entity in clinical practice.As lesões hepáticas são achados comuns na prática clínica. Os hamartomas dos ductos biliares, vulgarmente conhecidos por complexo de Von Meyenburg, são malformações hepáticas benignas que se apresentam histologicamente como pequenas dilatações quísticas dos ductos biliares, revestidas por tecido fibroso. Representam uma entidade clinico-patológica rara, tipicamente assintomática e sem alterações nos parâmetros hepáticos. O aspeto imagiológico é variável, podendo apresentar-se como múltiplas pequenas lesões dispersas pelo fígado, ou mais raramente como nódulo isolado. Os achados imagiológicos podem mimetizar lesões secundárias e, apesar da aparente benignidade da patologia, estão descritos casos de progressão para colangiocarcinoma. É, por isso, importante incluir este complexo no diagnóstico diferencial das lesões hepáticas focais, sendo fundamental uma investigação minuciosa para a sua diferenciação. Os autores pretendem com este caso dar a conhecer uma apresentação atípica de uma entidade rara e pouco ponderada na prática clínica.Ordem dos Médicos2014-04-30info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfimage/jpegimage/jpegimage/jpegimage/jpegimage/jpegapplication/pdfhttps://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274oai:ojs.www.actamedicaportuguesa.com:article/4274Acta Médica Portuguesa; Vol. 27 No. 2 (2014): March-April; 271-273Acta Médica Portuguesa; Vol. 27 N.º 2 (2014): Março-Abril; 271-2731646-07580870-399Xreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPporhttps://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/3936https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/6924https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/6925https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/6926https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/6927https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/6928https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/7200Silveira, InêsMota, FernandoFerreira, João PedroDias, RenataLeuschner, Pedroinfo:eu-repo/semantics/openAccess2022-12-20T11:03:32Zoai:ojs.www.actamedicaportuguesa.com:article/4274Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T16:18:46.885053Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review Complexo de Von Meyenburg ou Metástases Hepáticas? Caso Clínico e Revisão da Literatura |
title |
Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review |
spellingShingle |
Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review Silveira, Inês |
title_short |
Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review |
title_full |
Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review |
title_fullStr |
Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review |
title_full_unstemmed |
Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review |
title_sort |
Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review |
author |
Silveira, Inês |
author_facet |
Silveira, Inês Mota, Fernando Ferreira, João Pedro Dias, Renata Leuschner, Pedro |
author_role |
author |
author2 |
Mota, Fernando Ferreira, João Pedro Dias, Renata Leuschner, Pedro |
author2_role |
author author author author |
dc.contributor.author.fl_str_mv |
Silveira, Inês Mota, Fernando Ferreira, João Pedro Dias, Renata Leuschner, Pedro |
description |
Hepatic lesions represent a common finding in clinical practice. Bile ducts hamartomas, also known as Von Meyenburg complex, are benign hepatic malformations composed of small dilated cystic bile ducts lined by fibrous stroma. They represent a rare and asymptomatic clinic-pathological entity. Imagiological findings are variable, and may present as multiple small scattered lesions, or rarely as a single nodule. These findings may resemble secondary lesions and, although benign, there are cases of progression to colangiocarcinoma. Thus it is important to include this complex in the differential diagnoses of focal hepatic lesions, being necessary a detailed investigation for their differentiation. This case represents an atypical presentation of a rare and not frequently considered entity in clinical practice. |
publishDate |
2014 |
dc.date.none.fl_str_mv |
2014-04-30 |
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info:eu-repo/semantics/article |
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https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274 oai:ojs.www.actamedicaportuguesa.com:article/4274 |
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https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274 |
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https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274 https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/3936 https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/6924 https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/6925 https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/6926 https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/6927 https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/6928 https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/7200 |
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Ordem dos Médicos |
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Ordem dos Médicos |
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Acta Médica Portuguesa; Vol. 27 No. 2 (2014): March-April; 271-273 Acta Médica Portuguesa; Vol. 27 N.º 2 (2014): Março-Abril; 271-273 1646-0758 0870-399X reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
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Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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