Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review

Detalhes bibliográficos
Autor(a) principal: Silveira, Inês
Data de Publicação: 2014
Outros Autores: Mota, Fernando, Ferreira, João Pedro, Dias, Renata, Leuschner, Pedro
Tipo de documento: Artigo
Idioma: por
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274
Resumo: Hepatic lesions represent a common finding in clinical practice. Bile ducts hamartomas, also known as Von Meyenburg complex, are benign hepatic malformations composed of small dilated cystic bile ducts lined by fibrous stroma. They represent a rare and asymptomatic clinic-pathological entity. Imagiological findings are variable, and may present as multiple small scattered lesions, or rarely as a single nodule. These findings may resemble secondary lesions and, although benign, there are cases of progression to colangiocarcinoma. Thus it is important to include this complex in the differential diagnoses of focal hepatic lesions, being necessary a detailed investigation for their differentiation. This case represents an atypical presentation of a rare and not frequently considered entity in clinical practice.
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spelling Von Meyenburg Complex or Liver Metastasis? Case Report and Literature ReviewComplexo de Von Meyenburg ou Metástases Hepáticas? Caso Clínico e Revisão da LiteraturaHepatic lesions represent a common finding in clinical practice. Bile ducts hamartomas, also known as Von Meyenburg complex, are benign hepatic malformations composed of small dilated cystic bile ducts lined by fibrous stroma. They represent a rare and asymptomatic clinic-pathological entity. Imagiological findings are variable, and may present as multiple small scattered lesions, or rarely as a single nodule. These findings may resemble secondary lesions and, although benign, there are cases of progression to colangiocarcinoma. Thus it is important to include this complex in the differential diagnoses of focal hepatic lesions, being necessary a detailed investigation for their differentiation. This case represents an atypical presentation of a rare and not frequently considered entity in clinical practice.As lesões hepáticas são achados comuns na prática clínica. Os hamartomas dos ductos biliares, vulgarmente conhecidos por complexo de Von Meyenburg, são malformações hepáticas benignas que se apresentam histologicamente como pequenas dilatações quísticas dos ductos biliares, revestidas por tecido fibroso. Representam uma entidade clinico-patológica rara, tipicamente assintomática e sem alterações nos parâmetros hepáticos. O aspeto imagiológico é variável, podendo apresentar-se como múltiplas pequenas lesões dispersas pelo fígado, ou mais raramente como nódulo isolado. Os achados imagiológicos podem mimetizar lesões secundárias e, apesar da aparente benignidade da patologia, estão descritos casos de progressão para colangiocarcinoma. É, por isso, importante incluir este complexo no diagnóstico diferencial das lesões hepáticas focais, sendo fundamental uma investigação minuciosa para a sua diferenciação. Os autores pretendem com este caso dar a conhecer uma apresentação atípica de uma entidade rara e pouco ponderada na prática clínica.Ordem dos Médicos2014-04-30info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfimage/jpegimage/jpegimage/jpegimage/jpegimage/jpegapplication/pdfhttps://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274oai:ojs.www.actamedicaportuguesa.com:article/4274Acta Médica Portuguesa; Vol. 27 No. 2 (2014): March-April; 271-273Acta Médica Portuguesa; Vol. 27 N.º 2 (2014): Março-Abril; 271-2731646-07580870-399Xreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPporhttps://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/3936https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/6924https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/6925https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/6926https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/6927https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/6928https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4274/7200Silveira, InêsMota, FernandoFerreira, João PedroDias, RenataLeuschner, Pedroinfo:eu-repo/semantics/openAccess2022-12-20T11:03:32Zoai:ojs.www.actamedicaportuguesa.com:article/4274Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T16:18:46.885053Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review
Complexo de Von Meyenburg ou Metástases Hepáticas? Caso Clínico e Revisão da Literatura
title Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review
spellingShingle Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review
Silveira, Inês
title_short Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review
title_full Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review
title_fullStr Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review
title_full_unstemmed Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review
title_sort Von Meyenburg Complex or Liver Metastasis? Case Report and Literature Review
author Silveira, Inês
author_facet Silveira, Inês
Mota, Fernando
Ferreira, João Pedro
Dias, Renata
Leuschner, Pedro
author_role author
author2 Mota, Fernando
Ferreira, João Pedro
Dias, Renata
Leuschner, Pedro
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Silveira, Inês
Mota, Fernando
Ferreira, João Pedro
Dias, Renata
Leuschner, Pedro
description Hepatic lesions represent a common finding in clinical practice. Bile ducts hamartomas, also known as Von Meyenburg complex, are benign hepatic malformations composed of small dilated cystic bile ducts lined by fibrous stroma. They represent a rare and asymptomatic clinic-pathological entity. Imagiological findings are variable, and may present as multiple small scattered lesions, or rarely as a single nodule. These findings may resemble secondary lesions and, although benign, there are cases of progression to colangiocarcinoma. Thus it is important to include this complex in the differential diagnoses of focal hepatic lesions, being necessary a detailed investigation for their differentiation. This case represents an atypical presentation of a rare and not frequently considered entity in clinical practice.
publishDate 2014
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dc.publisher.none.fl_str_mv Ordem dos Médicos
publisher.none.fl_str_mv Ordem dos Médicos
dc.source.none.fl_str_mv Acta Médica Portuguesa; Vol. 27 No. 2 (2014): March-April; 271-273
Acta Médica Portuguesa; Vol. 27 N.º 2 (2014): Março-Abril; 271-273
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