Dermatomyositis with normal muscle enzymes and pulmonary involvement

• Autor(a) principal: Marques, Sandra
• Data de Publicação: 2003
• Outros Autores: Pacheco, Maria Helena, Martins Baptista, António, Freitas, Maria Graça, Malhado, José
• Tipo de documento: Artigo
• Idioma: por
• Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
• Texto Completo: https://revista.spmi.pt/index.php/rpmi/article/view/1831
• topic: Dermatomiosite amiopática; pneumonia intersticial aguda; lesão alveolar difusa; pulmonary interstitial disease; diffuse alveolar damage; Dermatomyositis sine myositis

Dermatomyositis (DM) is a rare autoimmune disease with inflammatory damage of muscles and skin. The survival rate is greater than 90% with current therapy. DM sine myositis is a particular form of this disease that may be associated with pulmonary damage. Prognosis is related to pulmonary interstitial damage.The authors report the case of a 42-year-old Indian woman with fever, cough, dyspneia and skin damage of three weeks duration, admitted in the emergency room. Clinical examination and laboratory analyses led to the diagnosis of DM with pulmonary damage. The clinical presentation and review of the literature on the subject is discussed.