Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia

Detalhes bibliográficos
Autor(a) principal: Donato, Mariana
Data de Publicação: 2018
Outros Autores: Pimentel, João, Cabral, Rui, Escada, Pedro
Tipo de documento: Artigo
Idioma: por
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: https://doi.org/10.20344/amp.8802
Resumo: Hereditary hemorrhagic telangiectasia is a rare multi-systemic autosomal dominant disorder characterized by dysplasia of the vascular connective tissue and recurrent bleeding tendency. Epistaxis is the most common and earliest symptom. It is usually mild to moderate, however, in some patients it can be severe with significant interference in quality of life. We report a case of a patient with hereditary hemorrhagic telangiectasia, in which an episode of refractory epistaxis was treated with radiofrequency and fibrin sealant. Control of acute bleeding and elimination of telangiectasia was possible with this technique. After six months follow-up, there was no epistaxis recurrence. Various treatments for epistaxis in this disease have been described in the literature, but there is no consensus about the gold-standard procedure. Radiofrequency ablation of telangiectasia is a recent technique that has shown to be safe, effective and well tolerated, even in patients who underwent other previous treatments.
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spelling Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasiaRadiofrequência no tratamento da epistaxis refractária na telangiectasia hemorrágica hereditáriaEpistaxisHereditary hemorrhagicRadiofrequencyTelangiectasiaMedicine(all)Hereditary hemorrhagic telangiectasia is a rare multi-systemic autosomal dominant disorder characterized by dysplasia of the vascular connective tissue and recurrent bleeding tendency. Epistaxis is the most common and earliest symptom. It is usually mild to moderate, however, in some patients it can be severe with significant interference in quality of life. We report a case of a patient with hereditary hemorrhagic telangiectasia, in which an episode of refractory epistaxis was treated with radiofrequency and fibrin sealant. Control of acute bleeding and elimination of telangiectasia was possible with this technique. After six months follow-up, there was no epistaxis recurrence. Various treatments for epistaxis in this disease have been described in the literature, but there is no consensus about the gold-standard procedure. Radiofrequency ablation of telangiectasia is a recent technique that has shown to be safe, effective and well tolerated, even in patients who underwent other previous treatments.NOVA Medical School|Faculdade de Ciências Médicas (NMS|FCM)RUNDonato, MarianaPimentel, JoãoCabral, RuiEscada, Pedro2018-02-20T23:18:34Z2018-012018-01-01T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/article4application/pdfhttps://doi.org/10.20344/amp.8802por0870-399XPURE: 3624925http://www.scopus.com/inward/record.url?scp=85041419052&partnerID=8YFLogxKhttps://doi.org/10.20344/amp.8802info:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2024-03-11T04:17:05Zoai:run.unl.pt:10362/30950Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-20T03:29:33.473411Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia
Radiofrequência no tratamento da epistaxis refractária na telangiectasia hemorrágica hereditária
title Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia
spellingShingle Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia
Donato, Mariana
Epistaxis
Hereditary hemorrhagic
Radiofrequency
Telangiectasia
Medicine(all)
title_short Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia
title_full Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia
title_fullStr Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia
title_full_unstemmed Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia
title_sort Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia
author Donato, Mariana
author_facet Donato, Mariana
Pimentel, João
Cabral, Rui
Escada, Pedro
author_role author
author2 Pimentel, João
Cabral, Rui
Escada, Pedro
author2_role author
author
author
dc.contributor.none.fl_str_mv NOVA Medical School|Faculdade de Ciências Médicas (NMS|FCM)
RUN
dc.contributor.author.fl_str_mv Donato, Mariana
Pimentel, João
Cabral, Rui
Escada, Pedro
dc.subject.por.fl_str_mv Epistaxis
Hereditary hemorrhagic
Radiofrequency
Telangiectasia
Medicine(all)
topic Epistaxis
Hereditary hemorrhagic
Radiofrequency
Telangiectasia
Medicine(all)
description Hereditary hemorrhagic telangiectasia is a rare multi-systemic autosomal dominant disorder characterized by dysplasia of the vascular connective tissue and recurrent bleeding tendency. Epistaxis is the most common and earliest symptom. It is usually mild to moderate, however, in some patients it can be severe with significant interference in quality of life. We report a case of a patient with hereditary hemorrhagic telangiectasia, in which an episode of refractory epistaxis was treated with radiofrequency and fibrin sealant. Control of acute bleeding and elimination of telangiectasia was possible with this technique. After six months follow-up, there was no epistaxis recurrence. Various treatments for epistaxis in this disease have been described in the literature, but there is no consensus about the gold-standard procedure. Radiofrequency ablation of telangiectasia is a recent technique that has shown to be safe, effective and well tolerated, even in patients who underwent other previous treatments.
publishDate 2018
dc.date.none.fl_str_mv 2018-02-20T23:18:34Z
2018-01
2018-01-01T00:00:00Z
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url https://doi.org/10.20344/amp.8802
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv 0870-399X
PURE: 3624925
http://www.scopus.com/inward/record.url?scp=85041419052&partnerID=8YFLogxK
https://doi.org/10.20344/amp.8802
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