Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia
Autor(a) principal: | |
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Data de Publicação: | 2018 |
Outros Autores: | , , |
Tipo de documento: | Artigo |
Idioma: | por |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | https://doi.org/10.20344/amp.8802 |
Resumo: | Hereditary hemorrhagic telangiectasia is a rare multi-systemic autosomal dominant disorder characterized by dysplasia of the vascular connective tissue and recurrent bleeding tendency. Epistaxis is the most common and earliest symptom. It is usually mild to moderate, however, in some patients it can be severe with significant interference in quality of life. We report a case of a patient with hereditary hemorrhagic telangiectasia, in which an episode of refractory epistaxis was treated with radiofrequency and fibrin sealant. Control of acute bleeding and elimination of telangiectasia was possible with this technique. After six months follow-up, there was no epistaxis recurrence. Various treatments for epistaxis in this disease have been described in the literature, but there is no consensus about the gold-standard procedure. Radiofrequency ablation of telangiectasia is a recent technique that has shown to be safe, effective and well tolerated, even in patients who underwent other previous treatments. |
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Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasiaRadiofrequência no tratamento da epistaxis refractária na telangiectasia hemorrágica hereditáriaEpistaxisHereditary hemorrhagicRadiofrequencyTelangiectasiaMedicine(all)Hereditary hemorrhagic telangiectasia is a rare multi-systemic autosomal dominant disorder characterized by dysplasia of the vascular connective tissue and recurrent bleeding tendency. Epistaxis is the most common and earliest symptom. It is usually mild to moderate, however, in some patients it can be severe with significant interference in quality of life. We report a case of a patient with hereditary hemorrhagic telangiectasia, in which an episode of refractory epistaxis was treated with radiofrequency and fibrin sealant. Control of acute bleeding and elimination of telangiectasia was possible with this technique. After six months follow-up, there was no epistaxis recurrence. Various treatments for epistaxis in this disease have been described in the literature, but there is no consensus about the gold-standard procedure. Radiofrequency ablation of telangiectasia is a recent technique that has shown to be safe, effective and well tolerated, even in patients who underwent other previous treatments.NOVA Medical School|Faculdade de Ciências Médicas (NMS|FCM)RUNDonato, MarianaPimentel, JoãoCabral, RuiEscada, Pedro2018-02-20T23:18:34Z2018-012018-01-01T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/article4application/pdfhttps://doi.org/10.20344/amp.8802por0870-399XPURE: 3624925http://www.scopus.com/inward/record.url?scp=85041419052&partnerID=8YFLogxKhttps://doi.org/10.20344/amp.8802info:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2024-03-11T04:17:05Zoai:run.unl.pt:10362/30950Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-20T03:29:33.473411Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia Radiofrequência no tratamento da epistaxis refractária na telangiectasia hemorrágica hereditária |
title |
Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia |
spellingShingle |
Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia Donato, Mariana Epistaxis Hereditary hemorrhagic Radiofrequency Telangiectasia Medicine(all) |
title_short |
Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia |
title_full |
Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia |
title_fullStr |
Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia |
title_full_unstemmed |
Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia |
title_sort |
Radiofrequency for treatment of refractory epistaxis in hereditary hemorrhagic telangiectasia |
author |
Donato, Mariana |
author_facet |
Donato, Mariana Pimentel, João Cabral, Rui Escada, Pedro |
author_role |
author |
author2 |
Pimentel, João Cabral, Rui Escada, Pedro |
author2_role |
author author author |
dc.contributor.none.fl_str_mv |
NOVA Medical School|Faculdade de Ciências Médicas (NMS|FCM) RUN |
dc.contributor.author.fl_str_mv |
Donato, Mariana Pimentel, João Cabral, Rui Escada, Pedro |
dc.subject.por.fl_str_mv |
Epistaxis Hereditary hemorrhagic Radiofrequency Telangiectasia Medicine(all) |
topic |
Epistaxis Hereditary hemorrhagic Radiofrequency Telangiectasia Medicine(all) |
description |
Hereditary hemorrhagic telangiectasia is a rare multi-systemic autosomal dominant disorder characterized by dysplasia of the vascular connective tissue and recurrent bleeding tendency. Epistaxis is the most common and earliest symptom. It is usually mild to moderate, however, in some patients it can be severe with significant interference in quality of life. We report a case of a patient with hereditary hemorrhagic telangiectasia, in which an episode of refractory epistaxis was treated with radiofrequency and fibrin sealant. Control of acute bleeding and elimination of telangiectasia was possible with this technique. After six months follow-up, there was no epistaxis recurrence. Various treatments for epistaxis in this disease have been described in the literature, but there is no consensus about the gold-standard procedure. Radiofrequency ablation of telangiectasia is a recent technique that has shown to be safe, effective and well tolerated, even in patients who underwent other previous treatments. |
publishDate |
2018 |
dc.date.none.fl_str_mv |
2018-02-20T23:18:34Z 2018-01 2018-01-01T00:00:00Z |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://doi.org/10.20344/amp.8802 |
url |
https://doi.org/10.20344/amp.8802 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
0870-399X PURE: 3624925 http://www.scopus.com/inward/record.url?scp=85041419052&partnerID=8YFLogxK https://doi.org/10.20344/amp.8802 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
4 application/pdf |
dc.source.none.fl_str_mv |
reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
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Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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RCAAP |
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RCAAP |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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1799137921233584128 |