Case for diagnosis

Detalhes bibliográficos
Autor(a) principal: Boza,Juliana Catucci
Data de Publicação: 2014
Outros Autores: Dorn,Timotio Volnei, Oliveira,Fabiana Bazanella de, Bakos,Renato Marchiori
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Anais brasileiros de dermatologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000600999
Resumo: The Osler-Weber-Rendu syndrome or Hereditary Hemorrhagic Telangiectasia (HHT) is a systemic fibrovascular dysplasia characterized by defects in the elastic and vascular walls of blood vessels, making them varicose and prone to disruptions. Lesions occur in different organs and can lead to hemorrhage in the lungs, digestive tract and brain. We describe the case of a patient with cutaneous manifestations and severe impairment of the digestive tract. It is important for the dermatologist to recognize this syndrome, since the cutaneous lesions may play a key role in diagnosis.
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spelling Case for diagnosisDiagnosisEpistaxisTelangiectasia, hereditary hemorrhagicTelangiectasisThe Osler-Weber-Rendu syndrome or Hereditary Hemorrhagic Telangiectasia (HHT) is a systemic fibrovascular dysplasia characterized by defects in the elastic and vascular walls of blood vessels, making them varicose and prone to disruptions. Lesions occur in different organs and can lead to hemorrhage in the lungs, digestive tract and brain. We describe the case of a patient with cutaneous manifestations and severe impairment of the digestive tract. It is important for the dermatologist to recognize this syndrome, since the cutaneous lesions may play a key role in diagnosis.Sociedade Brasileira de Dermatologia2014-12-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000600999Anais Brasileiros de Dermatologia v.89 n.6 2014reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20143232info:eu-repo/semantics/openAccessBoza,Juliana CatucciDorn,Timotio VolneiOliveira,Fabiana Bazanella deBakos,Renato Marchiorieng2015-03-25T00:00:00Zoai:scielo:S0365-05962014000600999Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2015-03-25T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false
dc.title.none.fl_str_mv Case for diagnosis
title Case for diagnosis
spellingShingle Case for diagnosis
Boza,Juliana Catucci
Diagnosis
Epistaxis
Telangiectasia, hereditary hemorrhagic
Telangiectasis
title_short Case for diagnosis
title_full Case for diagnosis
title_fullStr Case for diagnosis
title_full_unstemmed Case for diagnosis
title_sort Case for diagnosis
author Boza,Juliana Catucci
author_facet Boza,Juliana Catucci
Dorn,Timotio Volnei
Oliveira,Fabiana Bazanella de
Bakos,Renato Marchiori
author_role author
author2 Dorn,Timotio Volnei
Oliveira,Fabiana Bazanella de
Bakos,Renato Marchiori
author2_role author
author
author
dc.contributor.author.fl_str_mv Boza,Juliana Catucci
Dorn,Timotio Volnei
Oliveira,Fabiana Bazanella de
Bakos,Renato Marchiori
dc.subject.por.fl_str_mv Diagnosis
Epistaxis
Telangiectasia, hereditary hemorrhagic
Telangiectasis
topic Diagnosis
Epistaxis
Telangiectasia, hereditary hemorrhagic
Telangiectasis
description The Osler-Weber-Rendu syndrome or Hereditary Hemorrhagic Telangiectasia (HHT) is a systemic fibrovascular dysplasia characterized by defects in the elastic and vascular walls of blood vessels, making them varicose and prone to disruptions. Lesions occur in different organs and can lead to hemorrhage in the lungs, digestive tract and brain. We describe the case of a patient with cutaneous manifestations and severe impairment of the digestive tract. It is important for the dermatologist to recognize this syndrome, since the cutaneous lesions may play a key role in diagnosis.
publishDate 2014
dc.date.none.fl_str_mv 2014-12-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000600999
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000600999
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/abd1806-4841.20143232
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv Anais Brasileiros de Dermatologia v.89 n.6 2014
reponame:Anais brasileiros de dermatologia (Online)
instname:Sociedade Brasileira de Dermatologia (SBD)
instacron:SBD
instname_str Sociedade Brasileira de Dermatologia (SBD)
instacron_str SBD
institution SBD
reponame_str Anais brasileiros de dermatologia (Online)
collection Anais brasileiros de dermatologia (Online)
repository.name.fl_str_mv Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)
repository.mail.fl_str_mv abd@sbd.org.br||revista@sbd.org.br
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