Case for diagnosis
Autor(a) principal: | |
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Data de Publicação: | 2014 |
Outros Autores: | , , |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | Anais brasileiros de dermatologia (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000600999 |
Resumo: | The Osler-Weber-Rendu syndrome or Hereditary Hemorrhagic Telangiectasia (HHT) is a systemic fibrovascular dysplasia characterized by defects in the elastic and vascular walls of blood vessels, making them varicose and prone to disruptions. Lesions occur in different organs and can lead to hemorrhage in the lungs, digestive tract and brain. We describe the case of a patient with cutaneous manifestations and severe impairment of the digestive tract. It is important for the dermatologist to recognize this syndrome, since the cutaneous lesions may play a key role in diagnosis. |
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Anais brasileiros de dermatologia (Online) |
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Case for diagnosisDiagnosisEpistaxisTelangiectasia, hereditary hemorrhagicTelangiectasisThe Osler-Weber-Rendu syndrome or Hereditary Hemorrhagic Telangiectasia (HHT) is a systemic fibrovascular dysplasia characterized by defects in the elastic and vascular walls of blood vessels, making them varicose and prone to disruptions. Lesions occur in different organs and can lead to hemorrhage in the lungs, digestive tract and brain. We describe the case of a patient with cutaneous manifestations and severe impairment of the digestive tract. It is important for the dermatologist to recognize this syndrome, since the cutaneous lesions may play a key role in diagnosis.Sociedade Brasileira de Dermatologia2014-12-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000600999Anais Brasileiros de Dermatologia v.89 n.6 2014reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20143232info:eu-repo/semantics/openAccessBoza,Juliana CatucciDorn,Timotio VolneiOliveira,Fabiana Bazanella deBakos,Renato Marchiorieng2015-03-25T00:00:00Zoai:scielo:S0365-05962014000600999Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2015-03-25T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false |
dc.title.none.fl_str_mv |
Case for diagnosis |
title |
Case for diagnosis |
spellingShingle |
Case for diagnosis Boza,Juliana Catucci Diagnosis Epistaxis Telangiectasia, hereditary hemorrhagic Telangiectasis |
title_short |
Case for diagnosis |
title_full |
Case for diagnosis |
title_fullStr |
Case for diagnosis |
title_full_unstemmed |
Case for diagnosis |
title_sort |
Case for diagnosis |
author |
Boza,Juliana Catucci |
author_facet |
Boza,Juliana Catucci Dorn,Timotio Volnei Oliveira,Fabiana Bazanella de Bakos,Renato Marchiori |
author_role |
author |
author2 |
Dorn,Timotio Volnei Oliveira,Fabiana Bazanella de Bakos,Renato Marchiori |
author2_role |
author author author |
dc.contributor.author.fl_str_mv |
Boza,Juliana Catucci Dorn,Timotio Volnei Oliveira,Fabiana Bazanella de Bakos,Renato Marchiori |
dc.subject.por.fl_str_mv |
Diagnosis Epistaxis Telangiectasia, hereditary hemorrhagic Telangiectasis |
topic |
Diagnosis Epistaxis Telangiectasia, hereditary hemorrhagic Telangiectasis |
description |
The Osler-Weber-Rendu syndrome or Hereditary Hemorrhagic Telangiectasia (HHT) is a systemic fibrovascular dysplasia characterized by defects in the elastic and vascular walls of blood vessels, making them varicose and prone to disruptions. Lesions occur in different organs and can lead to hemorrhage in the lungs, digestive tract and brain. We describe the case of a patient with cutaneous manifestations and severe impairment of the digestive tract. It is important for the dermatologist to recognize this syndrome, since the cutaneous lesions may play a key role in diagnosis. |
publishDate |
2014 |
dc.date.none.fl_str_mv |
2014-12-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000600999 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000600999 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/abd1806-4841.20143232 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
dc.source.none.fl_str_mv |
Anais Brasileiros de Dermatologia v.89 n.6 2014 reponame:Anais brasileiros de dermatologia (Online) instname:Sociedade Brasileira de Dermatologia (SBD) instacron:SBD |
instname_str |
Sociedade Brasileira de Dermatologia (SBD) |
instacron_str |
SBD |
institution |
SBD |
reponame_str |
Anais brasileiros de dermatologia (Online) |
collection |
Anais brasileiros de dermatologia (Online) |
repository.name.fl_str_mv |
Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD) |
repository.mail.fl_str_mv |
abd@sbd.org.br||revista@sbd.org.br |
_version_ |
1752126420167950336 |