Idiopathic inflammatory myopathies : state of the art on clinical practice guidelines
| Autor(a) principal: | |
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| Data de Publicação: | 2019 |
| Outros Autores: | , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , , |
| Tipo de documento: | Artigo |
| Idioma: | eng |
| Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
| Texto Completo: | http://hdl.handle.net/10451/46782 |
Resumo: | © Author(s) (or their employer(s)) 2019. Re-use permitted under CC BY-NC. No commercial re-use. See rights and permissions. Published by BMJ |
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Idiopathic inflammatory myopathies : state of the art on clinical practice guidelines© Author(s) (or their employer(s)) 2019. Re-use permitted under CC BY-NC. No commercial re-use. See rights and permissions. Published by BMJThis article has been corrected since it first published. The authors would like to notify that title of the article has been changed to:Idiopathic inflammatory myopathies: state of the art on clinical practice guidelines. RMD Open 2019;5:e000784corr1. doi:10.1136/rmdopen-2018-000784corIdiopathic inflammatory myopathies (IIMs) encompass a heterogeneous group of rare autoimmune diseases characterised by muscle weakness and inflammation, but in antisynthetase syndrome arthritis and interstitial lung disease are more frequent and often inaugurate the disease. Clinical practice guidelines (CPGs) have been proposed for IIMs, but they are sparse and heterogeneous. This work aimed at identifying: i) current available CPGs for IIMs, ii) patients’ and clinicians’ unmet needs not covered by CPGs. It has been performed in the framework of the European Reference Network on rare and complex connective tissue and musculoskeletal diseases (ReCONNET), a network of centre of expertise and patients funded by the European Union’s Health Programme. Fourteen original CPGs were identified, notably recommending that: i) extra-muscular involvements should be assessed; ii) corticosteroids and methotrexate or azathioprine are first-line therapies of IIMs. iii) IVIG is a treatment of resistantDM that may be also used in other resistant-IIMs; iv) physical therapy and sun protection (in DM patients) are part of the treatment; v) tumour screening for patients with DM include imaging of chest, abdomen, pelvis and breast (in woman) along with colonoscopy (in patients over 50 years); vi) disease activity and damages should be monitor using standardised and validated tools. Yet, only half of these CPGs were evidence-based. Crucial unmet needs were identified both by patients and clinicians. In particular, there was a lack of large multidisciplinary working group and of patients’ preferences. The following fields were not or inappropriately targeted: diagnosis; management of extra-muscular involvements other than skin; co-morbidities and severe manifestations.This publication was funded by the European Union’s Health Programme (2014-2020), Framework Partnership Agreement number: 739531 – ERN ReCONNET. The content of this publication represents the views of the authors only and it is their sole responsibility; it cannot be considered to reflect the views of the European Commission and/or the Consumers, Health, Agriculture and Food Executive Agency (CHAFEA) or any other body of the European Union. The European Commission and the Agency do not accept any responsibility for use that may be made of the information it contains.BMJ Publishing Group, Ltd.Repositório da Universidade de LisboaMeyer, AlainScirè, Carlo AlbertoTalarico, RosariaAlexander, TobiasAmoura, ZahirAvcin, TadejBarsotti, SimoneBeretta, LorenzoBlagojevic, JelenaBurmester, GerdCavazzana, IlariaCherrin, PatrickDamian, LauraDoria, AndreaFonseca, João EuricoFurini, FedericaGaletti, IlariaHoussiau, FredericKrieg, ThomasLarosa, MaddalenaLaunay, DavidCampanilho-Marques, RaquelMartin, ThierryMatucci-Cerinic, MarcoMoinzadeh, PiaMontecucco, CarlomaurizioMoraes-Fontes, Maria FranciscaMouthon, LucNeri, RossellaPaolino, SabrinaPiette, YvesRednic, SimonaTamirou, FarahTincani, AngelaToplak, NatasaBombardieri, StefanoHachulla, EricMueller-Ladner, UlfSchneider, MatthiasSmith, VanessaVieira, AnaCutolo, MaurizioMosca, MartaCavagna, Lorenzo2021-03-10T16:32:25Z20192019-01-01T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttp://hdl.handle.net/10451/46782engRMD Open 2019;4:e00078410.1136/rmdopen-2018-0007842056-5933info:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2023-11-08T16:49:15Zoai:repositorio.ul.pt:10451/46782Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T21:58:51.936629Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
| dc.title.none.fl_str_mv |
Idiopathic inflammatory myopathies : state of the art on clinical practice guidelines |
| title |
Idiopathic inflammatory myopathies : state of the art on clinical practice guidelines |
| spellingShingle |
Idiopathic inflammatory myopathies : state of the art on clinical practice guidelines Meyer, Alain |
| title_short |
Idiopathic inflammatory myopathies : state of the art on clinical practice guidelines |
| title_full |
Idiopathic inflammatory myopathies : state of the art on clinical practice guidelines |
| title_fullStr |
Idiopathic inflammatory myopathies : state of the art on clinical practice guidelines |
| title_full_unstemmed |
Idiopathic inflammatory myopathies : state of the art on clinical practice guidelines |
| title_sort |
Idiopathic inflammatory myopathies : state of the art on clinical practice guidelines |
| author |
Meyer, Alain |
| author_facet |
Meyer, Alain Scirè, Carlo Alberto Talarico, Rosaria Alexander, Tobias Amoura, Zahir Avcin, Tadej Barsotti, Simone Beretta, Lorenzo Blagojevic, Jelena Burmester, Gerd Cavazzana, Ilaria Cherrin, Patrick Damian, Laura Doria, Andrea Fonseca, João Eurico Furini, Federica Galetti, Ilaria Houssiau, Frederic Krieg, Thomas Larosa, Maddalena Launay, David Campanilho-Marques, Raquel Martin, Thierry Matucci-Cerinic, Marco Moinzadeh, Pia Montecucco, Carlomaurizio Moraes-Fontes, Maria Francisca Mouthon, Luc Neri, Rossella Paolino, Sabrina Piette, Yves Rednic, Simona Tamirou, Farah Tincani, Angela Toplak, Natasa Bombardieri, Stefano Hachulla, Eric Mueller-Ladner, Ulf Schneider, Matthias Smith, Vanessa Vieira, Ana Cutolo, Maurizio Mosca, Marta Cavagna, Lorenzo |
| author_role |
author |
| author2 |
Scirè, Carlo Alberto Talarico, Rosaria Alexander, Tobias Amoura, Zahir Avcin, Tadej Barsotti, Simone Beretta, Lorenzo Blagojevic, Jelena Burmester, Gerd Cavazzana, Ilaria Cherrin, Patrick Damian, Laura Doria, Andrea Fonseca, João Eurico Furini, Federica Galetti, Ilaria Houssiau, Frederic Krieg, Thomas Larosa, Maddalena Launay, David Campanilho-Marques, Raquel Martin, Thierry Matucci-Cerinic, Marco Moinzadeh, Pia Montecucco, Carlomaurizio Moraes-Fontes, Maria Francisca Mouthon, Luc Neri, Rossella Paolino, Sabrina Piette, Yves Rednic, Simona Tamirou, Farah Tincani, Angela Toplak, Natasa Bombardieri, Stefano Hachulla, Eric Mueller-Ladner, Ulf Schneider, Matthias Smith, Vanessa Vieira, Ana Cutolo, Maurizio Mosca, Marta Cavagna, Lorenzo |
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author author author author author author author author author author author author author author author author author author author author author author author author author author author author author author author author author author author author author author author author author author author |
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Repositório da Universidade de Lisboa |
| dc.contributor.author.fl_str_mv |
Meyer, Alain Scirè, Carlo Alberto Talarico, Rosaria Alexander, Tobias Amoura, Zahir Avcin, Tadej Barsotti, Simone Beretta, Lorenzo Blagojevic, Jelena Burmester, Gerd Cavazzana, Ilaria Cherrin, Patrick Damian, Laura Doria, Andrea Fonseca, João Eurico Furini, Federica Galetti, Ilaria Houssiau, Frederic Krieg, Thomas Larosa, Maddalena Launay, David Campanilho-Marques, Raquel Martin, Thierry Matucci-Cerinic, Marco Moinzadeh, Pia Montecucco, Carlomaurizio Moraes-Fontes, Maria Francisca Mouthon, Luc Neri, Rossella Paolino, Sabrina Piette, Yves Rednic, Simona Tamirou, Farah Tincani, Angela Toplak, Natasa Bombardieri, Stefano Hachulla, Eric Mueller-Ladner, Ulf Schneider, Matthias Smith, Vanessa Vieira, Ana Cutolo, Maurizio Mosca, Marta Cavagna, Lorenzo |
| description |
© Author(s) (or their employer(s)) 2019. Re-use permitted under CC BY-NC. No commercial re-use. See rights and permissions. Published by BMJ |
| publishDate |
2019 |
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2019 2019-01-01T00:00:00Z 2021-03-10T16:32:25Z |
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info:eu-repo/semantics/publishedVersion |
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info:eu-repo/semantics/article |
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http://hdl.handle.net/10451/46782 |
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eng |
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eng |
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RMD Open 2019;4:e000784 10.1136/rmdopen-2018-000784 2056-5933 |
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BMJ Publishing Group, Ltd. |
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BMJ Publishing Group, Ltd. |
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