Case for diagnosis. Diffuse ulcerated nodular lesions
Autor(a) principal: | |
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Data de Publicação: | 2019 |
Outros Autores: | , , |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | Anais brasileiros de dermatologia (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962019000500615 |
Resumo: | Abstract Langerhans cell histiocytosis is a rare clonal proliferative disease, characterized by the infiltration of one or multiple organs by histiocytes. Due to the diversity of signs and symptoms, the diagnosis of this disease is often late. The estimated incidence in adults is one to two cases per million, but the disease is probably underdiagnosed in this population. This report presents a case of disseminated Langerhans cell histiocytosis. The authors highlight the most characteristic aspects of this rare and heterogeneous disease, which usually presents as a challenging clinical diagnosis. |
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Case for diagnosis. Diffuse ulcerated nodular lesionsHistiocytosisInflammationNeoplasmsAbstract Langerhans cell histiocytosis is a rare clonal proliferative disease, characterized by the infiltration of one or multiple organs by histiocytes. Due to the diversity of signs and symptoms, the diagnosis of this disease is often late. The estimated incidence in adults is one to two cases per million, but the disease is probably underdiagnosed in this population. This report presents a case of disseminated Langerhans cell histiocytosis. The authors highlight the most characteristic aspects of this rare and heterogeneous disease, which usually presents as a challenging clinical diagnosis.Sociedade Brasileira de Dermatologia2019-10-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962019000500615Anais Brasileiros de Dermatologia v.94 n.5 2019reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1016/j.abd.2019.09.021info:eu-repo/semantics/openAccessMartins,Paulo Henrique TeixeiraDallagnese,GabrielaLuzzatto,LauraDantas,Manuela Limaeng2019-12-05T00:00:00Zoai:scielo:S0365-05962019000500615Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2019-12-05T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false |
dc.title.none.fl_str_mv |
Case for diagnosis. Diffuse ulcerated nodular lesions |
title |
Case for diagnosis. Diffuse ulcerated nodular lesions |
spellingShingle |
Case for diagnosis. Diffuse ulcerated nodular lesions Martins,Paulo Henrique Teixeira Histiocytosis Inflammation Neoplasms |
title_short |
Case for diagnosis. Diffuse ulcerated nodular lesions |
title_full |
Case for diagnosis. Diffuse ulcerated nodular lesions |
title_fullStr |
Case for diagnosis. Diffuse ulcerated nodular lesions |
title_full_unstemmed |
Case for diagnosis. Diffuse ulcerated nodular lesions |
title_sort |
Case for diagnosis. Diffuse ulcerated nodular lesions |
author |
Martins,Paulo Henrique Teixeira |
author_facet |
Martins,Paulo Henrique Teixeira Dallagnese,Gabriela Luzzatto,Laura Dantas,Manuela Lima |
author_role |
author |
author2 |
Dallagnese,Gabriela Luzzatto,Laura Dantas,Manuela Lima |
author2_role |
author author author |
dc.contributor.author.fl_str_mv |
Martins,Paulo Henrique Teixeira Dallagnese,Gabriela Luzzatto,Laura Dantas,Manuela Lima |
dc.subject.por.fl_str_mv |
Histiocytosis Inflammation Neoplasms |
topic |
Histiocytosis Inflammation Neoplasms |
description |
Abstract Langerhans cell histiocytosis is a rare clonal proliferative disease, characterized by the infiltration of one or multiple organs by histiocytes. Due to the diversity of signs and symptoms, the diagnosis of this disease is often late. The estimated incidence in adults is one to two cases per million, but the disease is probably underdiagnosed in this population. This report presents a case of disseminated Langerhans cell histiocytosis. The authors highlight the most characteristic aspects of this rare and heterogeneous disease, which usually presents as a challenging clinical diagnosis. |
publishDate |
2019 |
dc.date.none.fl_str_mv |
2019-10-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962019000500615 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962019000500615 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1016/j.abd.2019.09.021 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
dc.source.none.fl_str_mv |
Anais Brasileiros de Dermatologia v.94 n.5 2019 reponame:Anais brasileiros de dermatologia (Online) instname:Sociedade Brasileira de Dermatologia (SBD) instacron:SBD |
instname_str |
Sociedade Brasileira de Dermatologia (SBD) |
instacron_str |
SBD |
institution |
SBD |
reponame_str |
Anais brasileiros de dermatologia (Online) |
collection |
Anais brasileiros de dermatologia (Online) |
repository.name.fl_str_mv |
Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD) |
repository.mail.fl_str_mv |
abd@sbd.org.br||revista@sbd.org.br |
_version_ |
1752126423486693376 |