Case for diagnosis. Diffuse ulcerated nodular lesions

Detalhes bibliográficos
Autor(a) principal: Martins,Paulo Henrique Teixeira
Data de Publicação: 2019
Outros Autores: Dallagnese,Gabriela, Luzzatto,Laura, Dantas,Manuela Lima
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Anais brasileiros de dermatologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962019000500615
Resumo: Abstract Langerhans cell histiocytosis is a rare clonal proliferative disease, characterized by the infiltration of one or multiple organs by histiocytes. Due to the diversity of signs and symptoms, the diagnosis of this disease is often late. The estimated incidence in adults is one to two cases per million, but the disease is probably underdiagnosed in this population. This report presents a case of disseminated Langerhans cell histiocytosis. The authors highlight the most characteristic aspects of this rare and heterogeneous disease, which usually presents as a challenging clinical diagnosis.
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spelling Case for diagnosis. Diffuse ulcerated nodular lesionsHistiocytosisInflammationNeoplasmsAbstract Langerhans cell histiocytosis is a rare clonal proliferative disease, characterized by the infiltration of one or multiple organs by histiocytes. Due to the diversity of signs and symptoms, the diagnosis of this disease is often late. The estimated incidence in adults is one to two cases per million, but the disease is probably underdiagnosed in this population. This report presents a case of disseminated Langerhans cell histiocytosis. The authors highlight the most characteristic aspects of this rare and heterogeneous disease, which usually presents as a challenging clinical diagnosis.Sociedade Brasileira de Dermatologia2019-10-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962019000500615Anais Brasileiros de Dermatologia v.94 n.5 2019reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1016/j.abd.2019.09.021info:eu-repo/semantics/openAccessMartins,Paulo Henrique TeixeiraDallagnese,GabrielaLuzzatto,LauraDantas,Manuela Limaeng2019-12-05T00:00:00Zoai:scielo:S0365-05962019000500615Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2019-12-05T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false
dc.title.none.fl_str_mv Case for diagnosis. Diffuse ulcerated nodular lesions
title Case for diagnosis. Diffuse ulcerated nodular lesions
spellingShingle Case for diagnosis. Diffuse ulcerated nodular lesions
Martins,Paulo Henrique Teixeira
Histiocytosis
Inflammation
Neoplasms
title_short Case for diagnosis. Diffuse ulcerated nodular lesions
title_full Case for diagnosis. Diffuse ulcerated nodular lesions
title_fullStr Case for diagnosis. Diffuse ulcerated nodular lesions
title_full_unstemmed Case for diagnosis. Diffuse ulcerated nodular lesions
title_sort Case for diagnosis. Diffuse ulcerated nodular lesions
author Martins,Paulo Henrique Teixeira
author_facet Martins,Paulo Henrique Teixeira
Dallagnese,Gabriela
Luzzatto,Laura
Dantas,Manuela Lima
author_role author
author2 Dallagnese,Gabriela
Luzzatto,Laura
Dantas,Manuela Lima
author2_role author
author
author
dc.contributor.author.fl_str_mv Martins,Paulo Henrique Teixeira
Dallagnese,Gabriela
Luzzatto,Laura
Dantas,Manuela Lima
dc.subject.por.fl_str_mv Histiocytosis
Inflammation
Neoplasms
topic Histiocytosis
Inflammation
Neoplasms
description Abstract Langerhans cell histiocytosis is a rare clonal proliferative disease, characterized by the infiltration of one or multiple organs by histiocytes. Due to the diversity of signs and symptoms, the diagnosis of this disease is often late. The estimated incidence in adults is one to two cases per million, but the disease is probably underdiagnosed in this population. This report presents a case of disseminated Langerhans cell histiocytosis. The authors highlight the most characteristic aspects of this rare and heterogeneous disease, which usually presents as a challenging clinical diagnosis.
publishDate 2019
dc.date.none.fl_str_mv 2019-10-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962019000500615
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962019000500615
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1016/j.abd.2019.09.021
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv Anais Brasileiros de Dermatologia v.94 n.5 2019
reponame:Anais brasileiros de dermatologia (Online)
instname:Sociedade Brasileira de Dermatologia (SBD)
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reponame_str Anais brasileiros de dermatologia (Online)
collection Anais brasileiros de dermatologia (Online)
repository.name.fl_str_mv Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)
repository.mail.fl_str_mv abd@sbd.org.br||revista@sbd.org.br
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