Pulmonary alveolar microlithiasis. State-of-the-art review

Detalhes bibliográficos
Autor(a) principal: Francisco, Flávia Angélica Ferreira
Data de Publicação: 2013
Outros Autores: Silva, Jorge Luiz Pereira e, Hochhegger, Bruno, Zanetti, Gláucia Maria Ribeiro, Marchiori, Edson dos Santos
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Institucional da UFBA
Texto Completo: http://repositorio.ufba.br/ri/handle/ri/13423
Resumo: Texto completo. Acesso restrito. p. 1–9
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spelling Francisco, Flávia Angélica FerreiraSilva, Jorge Luiz Pereira eHochhegger, BrunoZanetti, Gláucia Maria RibeiroMarchiori, Edson dos SantosFrancisco, Flávia Angélica FerreiraSilva, Jorge Luiz Pereira eHochhegger, BrunoZanetti, Gláucia Maria RibeiroMarchiori, Edson dos Santos2013-10-31T18:02:25Z20130954-6111http://repositorio.ufba.br/ri/handle/ri/13423v. 107, n. 1Texto completo. Acesso restrito. p. 1–9Pulmonary alveolar microlithiasis (PAM) is a rare genetic lung disease characterized by calcifications within the alveoli. Mutations in the SLC34A2 gene, which encodes a type IIb sodiumphosphate cotransporter, are responsible for this disease, leading to intra-alveolar accumulation of phosphate that favors the formation of microliths. The hallmark of this disorder is clinical-radiological dissociation, with typical imaging findings that correlate well with specific pathological findings. The long-term prognosis is poor and no treatment has been discovered to date. The aim of this review is to describe the main pathological, clinical, and imaging aspects of PAM, ranging from its genetic basis to treatment.Submitted by Santiago Fabio (fabio.ssantiago@hotmail.com) on 2013-07-09T16:37:25Z No. of bitstreams: 1 aaaaaaaaaaaaaaaa.pdf: 796358 bytes, checksum: b0cf02f9274694442e46df1cdc7d3936 (MD5)Approved for entry into archive by Rodrigo Meirelles (rodrigomei@ufba.br) on 2013-10-31T18:02:25Z (GMT) No. of bitstreams: 1 aaaaaaaaaaaaaaaa.pdf: 796358 bytes, checksum: b0cf02f9274694442e46df1cdc7d3936 (MD5)Made available in DSpace on 2013-10-31T18:02:25Z (GMT). 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dc.title.pt_BR.fl_str_mv Pulmonary alveolar microlithiasis. State-of-the-art review
dc.title.alternative.pt_BR.fl_str_mv Respiratory Medicine
title Pulmonary alveolar microlithiasis. State-of-the-art review
spellingShingle Pulmonary alveolar microlithiasis. State-of-the-art review
Francisco, Flávia Angélica Ferreira
Pulmonary alveolar microlithiasis
Pulmonary diseases
Congenital diseases
Computed tomography
title_short Pulmonary alveolar microlithiasis. State-of-the-art review
title_full Pulmonary alveolar microlithiasis. State-of-the-art review
title_fullStr Pulmonary alveolar microlithiasis. State-of-the-art review
title_full_unstemmed Pulmonary alveolar microlithiasis. State-of-the-art review
title_sort Pulmonary alveolar microlithiasis. State-of-the-art review
author Francisco, Flávia Angélica Ferreira
author_facet Francisco, Flávia Angélica Ferreira
Silva, Jorge Luiz Pereira e
Hochhegger, Bruno
Zanetti, Gláucia Maria Ribeiro
Marchiori, Edson dos Santos
author_role author
author2 Silva, Jorge Luiz Pereira e
Hochhegger, Bruno
Zanetti, Gláucia Maria Ribeiro
Marchiori, Edson dos Santos
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Francisco, Flávia Angélica Ferreira
Silva, Jorge Luiz Pereira e
Hochhegger, Bruno
Zanetti, Gláucia Maria Ribeiro
Marchiori, Edson dos Santos
Francisco, Flávia Angélica Ferreira
Silva, Jorge Luiz Pereira e
Hochhegger, Bruno
Zanetti, Gláucia Maria Ribeiro
Marchiori, Edson dos Santos
dc.subject.por.fl_str_mv Pulmonary alveolar microlithiasis
Pulmonary diseases
Congenital diseases
Computed tomography
topic Pulmonary alveolar microlithiasis
Pulmonary diseases
Congenital diseases
Computed tomography
description Texto completo. Acesso restrito. p. 1–9
publishDate 2013
dc.date.accessioned.fl_str_mv 2013-10-31T18:02:25Z
dc.date.issued.fl_str_mv 2013
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://repositorio.ufba.br/ri/handle/ri/13423
dc.identifier.issn.none.fl_str_mv 0954-6111
dc.identifier.number.pt_BR.fl_str_mv v. 107, n. 1
identifier_str_mv 0954-6111
v. 107, n. 1
url http://repositorio.ufba.br/ri/handle/ri/13423
dc.language.iso.fl_str_mv eng
language eng
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.publisher.none.fl_str_mv Respiratory Medicine
publisher.none.fl_str_mv Respiratory Medicine
dc.source.pt_BR.fl_str_mv http://dx.doi.org/10.1016/j.rmed.2012.10.014
dc.source.none.fl_str_mv reponame:Repositório Institucional da UFBA
instname:Universidade Federal da Bahia (UFBA)
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instacron_str UFBA
institution UFBA
reponame_str Repositório Institucional da UFBA
collection Repositório Institucional da UFBA
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