Pulmonary alveolar microlithiasis. State-of-the-art review
Autor(a) principal: | |
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Data de Publicação: | 2013 |
Outros Autores: | , , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Repositório Institucional da UFBA |
Texto Completo: | http://repositorio.ufba.br/ri/handle/ri/13423 |
Resumo: | Texto completo. Acesso restrito. p. 1–9 |
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Francisco, Flávia Angélica FerreiraSilva, Jorge Luiz Pereira eHochhegger, BrunoZanetti, Gláucia Maria RibeiroMarchiori, Edson dos SantosFrancisco, Flávia Angélica FerreiraSilva, Jorge Luiz Pereira eHochhegger, BrunoZanetti, Gláucia Maria RibeiroMarchiori, Edson dos Santos2013-10-31T18:02:25Z20130954-6111http://repositorio.ufba.br/ri/handle/ri/13423v. 107, n. 1Texto completo. Acesso restrito. p. 1–9Pulmonary alveolar microlithiasis (PAM) is a rare genetic lung disease characterized by calcifications within the alveoli. Mutations in the SLC34A2 gene, which encodes a type IIb sodiumphosphate cotransporter, are responsible for this disease, leading to intra-alveolar accumulation of phosphate that favors the formation of microliths. The hallmark of this disorder is clinical-radiological dissociation, with typical imaging findings that correlate well with specific pathological findings. The long-term prognosis is poor and no treatment has been discovered to date. The aim of this review is to describe the main pathological, clinical, and imaging aspects of PAM, ranging from its genetic basis to treatment.Submitted by Santiago Fabio (fabio.ssantiago@hotmail.com) on 2013-07-09T16:37:25Z No. of bitstreams: 1 aaaaaaaaaaaaaaaa.pdf: 796358 bytes, checksum: b0cf02f9274694442e46df1cdc7d3936 (MD5)Approved for entry into archive by Rodrigo Meirelles (rodrigomei@ufba.br) on 2013-10-31T18:02:25Z (GMT) No. of bitstreams: 1 aaaaaaaaaaaaaaaa.pdf: 796358 bytes, checksum: b0cf02f9274694442e46df1cdc7d3936 (MD5)Made available in DSpace on 2013-10-31T18:02:25Z (GMT). No. of bitstreams: 1 aaaaaaaaaaaaaaaa.pdf: 796358 bytes, checksum: b0cf02f9274694442e46df1cdc7d3936 (MD5) Previous issue date: 2013SalvadorRespiratory Medicinehttp://dx.doi.org/10.1016/j.rmed.2012.10.014reponame:Repositório Institucional da UFBAinstname:Universidade Federal da Bahia (UFBA)instacron:UFBAPulmonary alveolar microlithiasisPulmonary diseasesCongenital diseasesComputed tomographyPulmonary alveolar microlithiasis. 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dc.title.pt_BR.fl_str_mv |
Pulmonary alveolar microlithiasis. State-of-the-art review |
dc.title.alternative.pt_BR.fl_str_mv |
Respiratory Medicine |
title |
Pulmonary alveolar microlithiasis. State-of-the-art review |
spellingShingle |
Pulmonary alveolar microlithiasis. State-of-the-art review Francisco, Flávia Angélica Ferreira Pulmonary alveolar microlithiasis Pulmonary diseases Congenital diseases Computed tomography |
title_short |
Pulmonary alveolar microlithiasis. State-of-the-art review |
title_full |
Pulmonary alveolar microlithiasis. State-of-the-art review |
title_fullStr |
Pulmonary alveolar microlithiasis. State-of-the-art review |
title_full_unstemmed |
Pulmonary alveolar microlithiasis. State-of-the-art review |
title_sort |
Pulmonary alveolar microlithiasis. State-of-the-art review |
author |
Francisco, Flávia Angélica Ferreira |
author_facet |
Francisco, Flávia Angélica Ferreira Silva, Jorge Luiz Pereira e Hochhegger, Bruno Zanetti, Gláucia Maria Ribeiro Marchiori, Edson dos Santos |
author_role |
author |
author2 |
Silva, Jorge Luiz Pereira e Hochhegger, Bruno Zanetti, Gláucia Maria Ribeiro Marchiori, Edson dos Santos |
author2_role |
author author author author |
dc.contributor.author.fl_str_mv |
Francisco, Flávia Angélica Ferreira Silva, Jorge Luiz Pereira e Hochhegger, Bruno Zanetti, Gláucia Maria Ribeiro Marchiori, Edson dos Santos Francisco, Flávia Angélica Ferreira Silva, Jorge Luiz Pereira e Hochhegger, Bruno Zanetti, Gláucia Maria Ribeiro Marchiori, Edson dos Santos |
dc.subject.por.fl_str_mv |
Pulmonary alveolar microlithiasis Pulmonary diseases Congenital diseases Computed tomography |
topic |
Pulmonary alveolar microlithiasis Pulmonary diseases Congenital diseases Computed tomography |
description |
Texto completo. Acesso restrito. p. 1–9 |
publishDate |
2013 |
dc.date.accessioned.fl_str_mv |
2013-10-31T18:02:25Z |
dc.date.issued.fl_str_mv |
2013 |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://repositorio.ufba.br/ri/handle/ri/13423 |
dc.identifier.issn.none.fl_str_mv |
0954-6111 |
dc.identifier.number.pt_BR.fl_str_mv |
v. 107, n. 1 |
identifier_str_mv |
0954-6111 v. 107, n. 1 |
url |
http://repositorio.ufba.br/ri/handle/ri/13423 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.publisher.none.fl_str_mv |
Respiratory Medicine |
publisher.none.fl_str_mv |
Respiratory Medicine |
dc.source.pt_BR.fl_str_mv |
http://dx.doi.org/10.1016/j.rmed.2012.10.014 |
dc.source.none.fl_str_mv |
reponame:Repositório Institucional da UFBA instname:Universidade Federal da Bahia (UFBA) instacron:UFBA |
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Universidade Federal da Bahia (UFBA) |
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UFBA |
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UFBA |
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Repositório Institucional da UFBA |
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Repositório Institucional da UFBA |
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