Guidelines for the management and treatment of periodic fever syndromes familial mediterranean fever

Detalhes bibliográficos
Autor(a) principal: Terreri, Maria Teresa R. A. [UNIFESP]
Data de Publicação: 2016
Outros Autores: Bernardo, Wanderley Marques, Len, Claudio Arnaldo [UNIFESP], Almeida da Silva, Clovis Artur, Ribeiro de Magalhaes, Cristina Medeiros, Sacchetti, Silvana B., Leme Ferriani, Virginia Paes, Petry Piotto, Daniela Gerent [UNIFESP], Cavalcanti, Andre de Souza, de Moraes, Ana Julia Pantoja, Sztajnbok, Flavio Roberto, Feitosa de Oliveira, Sheila Knupp, Arruda Campos, Lucia Maria, Bandeira, Marcia, Sena Teixeira Santos, Flavia Patricia, Magalhaes, Claudia Saad
Tipo de documento: Artigo
Idioma: por
Título da fonte: Repositório Institucional da UNIFESP
Texto Completo: http://dx.doi.org/10.1016/j.rbr.2015.08.006
http://repositorio.unifesp.br/handle/11600/49530
Resumo: Objective: To establish guidelines based on scientific evidence for the management of familial Mediterranean fever. Description of the evidence collection method: The Guideline was prepared from 5 clinical questions that were structured through PICO (Patient, Intervention or indicator, Comparison and Outcome), to search in key primary scientific information databases. After defining the potential studies to support the recommendations, these were graduated considering their strength of evidence and grade of recommendation. Results: 10,341 articles were retrieved and evaluated by title and abstract
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spelling Guidelines for the management and treatment of periodic fever syndromes familial mediterranean feverDiretrizes de conduta e tratamento de síndromes febris periódicas associadas a febre familiar do MediterrâneoFamilial Mediterranean FeverGuidelinesChildhoodFeverAutoinflammatory SyndromesAutoinflammatory SyndromesColchicine TherapyAmyloidosisActivationGenotypePatientAttacksTransplantationInterleukin-1CanakinumabObjective: To establish guidelines based on scientific evidence for the management of familial Mediterranean fever. Description of the evidence collection method: The Guideline was prepared from 5 clinical questions that were structured through PICO (Patient, Intervention or indicator, Comparison and Outcome), to search in key primary scientific information databases. After defining the potential studies to support the recommendations, these were graduated considering their strength of evidence and grade of recommendation. Results: 10,341 articles were retrieved and evaluated by title and abstractfrom these, 46 articles were selected to support the recommendations. Recommendations: 1. The diagnosis of FMF is based on clinical manifestations, characterized by recurrent febrile episodes associated with abdominal pain, chest or arthritis of large joints2. FMF is a genetic disease presenting an autosomal recessive trait, caused by mutation in the MEFV gene3. Laboratory tests are not specific, demonstrating high serum levels of inflammatory proteins in the acute phase of the disease, but also often showing high levels even between attacks. SAA serum levels may be especially useful in monitoring the effectiveness of treatment4. The therapy of choice is colchicinethis drug has proven effectiveness in preventing acute inflammatory episodes and progression towards amyloidosis in adults5. Based on the available information, the use of biological drugs appears to be an alternative for patients with FMF who do not respond or are intolerant to therapy with colchicine. (C) 2015 Elsevier Editora Ltda. All rights reserved.Setor de Reumatologia Pediátrica, Departamento de Pediatria, Universidade Federal de São Paulo (Unifesp), São Paulo, SP, BrasilCentro de Desenvolvimento de Educação Médica, Faculdade de Medicina, Universidade de São Paulo (USP), São Paulo, SP, BrasilUnidade de Reumatologia Pediátrica, Instituto da Criança, Faculdade de Medicina, Universidade de São Paulo (USP), São Paulo, SP, BrasilHospital da Criança de Brasília José Alencar (HCB), Brasília, DF, BrasilIrmandade da Santa Casa de Misericórdia de São Paulo, São Paulo, SP, BrasilServiço de Imunologia, Alergia e Reumatologia Pediátrica, Departamento de Pediatria, Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo (USP), Ribeirão Preto, SP, BrasilServiço de Reumatologia, Hospital das Clínicas, Universidade Federal de Pernambuco (UFPE), Recife, PE, BrasilUniversidade Federal do Pará (UFPA), Belém, PA, BrasilServiço de Reumatologia, Núcleo de Estudos da Saúde do Adolescente, Universidade do Estado do Rio de Janeiro (Uerj), Rio de Janeiro, RJ, BrasilInstituto de Puericultura e Pediatria Martagão Gesteira, Serviço de Reumatologia Pediátrica, Universidade Federal do Rio de Janeiro (UFRJ), Rio de Janeiro, RJ, BrasilHospital Pequeno Príncipe, Curitiba, PR, BrasilServiço de Reumatologia, Hospital das Clínicas, Universidade Federal de Minas Gerais (UFMG), Belo Horizonte, MG, BrasilUnidade de Reumatologia Pediátrica, Faculdade de Medicina de Botucatu, Universidade Estadual Paulista (Unesp), Botucatu, SP, BrasilSetor de Reumatologia Pediátrica, Departamento de Pediatria, Universidade Federal de São Paulo (Unifesp), São Paulo, SP, BrasilWeb of ScienceElsevier science inc2019-01-21T10:30:00Z2019-01-21T10:30:00Z2016info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersion37-43http://dx.doi.org/10.1016/j.rbr.2015.08.006Revista Brasileira De Reumatologia. New york, v. 56, n. 1, p. 37-43, 2016.10.1016/j.rbr.2015.08.006S0482-50042016000100037.pdf0482-5004S0482-50042016000100037http://repositorio.unifesp.br/handle/11600/49530WOS:000374895300007porRevista Brasileira De Reumatologiainfo:eu-repo/semantics/openAccessTerreri, Maria Teresa R. A. [UNIFESP]Bernardo, Wanderley MarquesLen, Claudio Arnaldo [UNIFESP]Almeida da Silva, Clovis ArturRibeiro de Magalhaes, Cristina MedeirosSacchetti, Silvana B.Leme Ferriani, Virginia PaesPetry Piotto, Daniela Gerent [UNIFESP]Cavalcanti, Andre de Souzade Moraes, Ana Julia PantojaSztajnbok, Flavio RobertoFeitosa de Oliveira, Sheila KnuppArruda Campos, Lucia MariaBandeira, MarciaSena Teixeira Santos, Flavia PatriciaMagalhaes, Claudia Saadreponame:Repositório Institucional da UNIFESPinstname:Universidade Federal de São Paulo (UNIFESP)instacron:UNIFESP2022-02-07T21:01:45Zoai:repositorio.unifesp.br/:11600/49530Repositório InstitucionalPUBhttp://www.repositorio.unifesp.br/oai/requestbiblioteca.csp@unifesp.bropendoar:34652022-02-07T21:01:45Repositório Institucional da UNIFESP - Universidade Federal de São Paulo (UNIFESP)false
dc.title.none.fl_str_mv Guidelines for the management and treatment of periodic fever syndromes familial mediterranean fever
Diretrizes de conduta e tratamento de síndromes febris periódicas associadas a febre familiar do Mediterrâneo
title Guidelines for the management and treatment of periodic fever syndromes familial mediterranean fever
spellingShingle Guidelines for the management and treatment of periodic fever syndromes familial mediterranean fever
Terreri, Maria Teresa R. A. [UNIFESP]
Familial Mediterranean Fever
Guidelines
Childhood
Fever
Autoinflammatory SyndromesAutoinflammatory Syndromes
Colchicine Therapy
Amyloidosis
Activation
Genotype
Patient
Attacks
Transplantation
Interleukin-1
Canakinumab
title_short Guidelines for the management and treatment of periodic fever syndromes familial mediterranean fever
title_full Guidelines for the management and treatment of periodic fever syndromes familial mediterranean fever
title_fullStr Guidelines for the management and treatment of periodic fever syndromes familial mediterranean fever
title_full_unstemmed Guidelines for the management and treatment of periodic fever syndromes familial mediterranean fever
title_sort Guidelines for the management and treatment of periodic fever syndromes familial mediterranean fever
author Terreri, Maria Teresa R. A. [UNIFESP]
author_facet Terreri, Maria Teresa R. A. [UNIFESP]
Bernardo, Wanderley Marques
Len, Claudio Arnaldo [UNIFESP]
Almeida da Silva, Clovis Artur
Ribeiro de Magalhaes, Cristina Medeiros
Sacchetti, Silvana B.
Leme Ferriani, Virginia Paes
Petry Piotto, Daniela Gerent [UNIFESP]
Cavalcanti, Andre de Souza
de Moraes, Ana Julia Pantoja
Sztajnbok, Flavio Roberto
Feitosa de Oliveira, Sheila Knupp
Arruda Campos, Lucia Maria
Bandeira, Marcia
Sena Teixeira Santos, Flavia Patricia
Magalhaes, Claudia Saad
author_role author
author2 Bernardo, Wanderley Marques
Len, Claudio Arnaldo [UNIFESP]
Almeida da Silva, Clovis Artur
Ribeiro de Magalhaes, Cristina Medeiros
Sacchetti, Silvana B.
Leme Ferriani, Virginia Paes
Petry Piotto, Daniela Gerent [UNIFESP]
Cavalcanti, Andre de Souza
de Moraes, Ana Julia Pantoja
Sztajnbok, Flavio Roberto
Feitosa de Oliveira, Sheila Knupp
Arruda Campos, Lucia Maria
Bandeira, Marcia
Sena Teixeira Santos, Flavia Patricia
Magalhaes, Claudia Saad
author2_role author
author
author
author
author
author
author
author
author
author
author
author
author
author
author
dc.contributor.author.fl_str_mv Terreri, Maria Teresa R. A. [UNIFESP]
Bernardo, Wanderley Marques
Len, Claudio Arnaldo [UNIFESP]
Almeida da Silva, Clovis Artur
Ribeiro de Magalhaes, Cristina Medeiros
Sacchetti, Silvana B.
Leme Ferriani, Virginia Paes
Petry Piotto, Daniela Gerent [UNIFESP]
Cavalcanti, Andre de Souza
de Moraes, Ana Julia Pantoja
Sztajnbok, Flavio Roberto
Feitosa de Oliveira, Sheila Knupp
Arruda Campos, Lucia Maria
Bandeira, Marcia
Sena Teixeira Santos, Flavia Patricia
Magalhaes, Claudia Saad
dc.subject.por.fl_str_mv Familial Mediterranean Fever
Guidelines
Childhood
Fever
Autoinflammatory SyndromesAutoinflammatory Syndromes
Colchicine Therapy
Amyloidosis
Activation
Genotype
Patient
Attacks
Transplantation
Interleukin-1
Canakinumab
topic Familial Mediterranean Fever
Guidelines
Childhood
Fever
Autoinflammatory SyndromesAutoinflammatory Syndromes
Colchicine Therapy
Amyloidosis
Activation
Genotype
Patient
Attacks
Transplantation
Interleukin-1
Canakinumab
description Objective: To establish guidelines based on scientific evidence for the management of familial Mediterranean fever. Description of the evidence collection method: The Guideline was prepared from 5 clinical questions that were structured through PICO (Patient, Intervention or indicator, Comparison and Outcome), to search in key primary scientific information databases. After defining the potential studies to support the recommendations, these were graduated considering their strength of evidence and grade of recommendation. Results: 10,341 articles were retrieved and evaluated by title and abstract
publishDate 2016
dc.date.none.fl_str_mv 2016
2019-01-21T10:30:00Z
2019-01-21T10:30:00Z
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://dx.doi.org/10.1016/j.rbr.2015.08.006
Revista Brasileira De Reumatologia. New york, v. 56, n. 1, p. 37-43, 2016.
10.1016/j.rbr.2015.08.006
S0482-50042016000100037.pdf
0482-5004
S0482-50042016000100037
http://repositorio.unifesp.br/handle/11600/49530
WOS:000374895300007
url http://dx.doi.org/10.1016/j.rbr.2015.08.006
http://repositorio.unifesp.br/handle/11600/49530
identifier_str_mv Revista Brasileira De Reumatologia. New york, v. 56, n. 1, p. 37-43, 2016.
10.1016/j.rbr.2015.08.006
S0482-50042016000100037.pdf
0482-5004
S0482-50042016000100037
WOS:000374895300007
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv Revista Brasileira De Reumatologia
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv 37-43
dc.publisher.none.fl_str_mv Elsevier science inc
publisher.none.fl_str_mv Elsevier science inc
dc.source.none.fl_str_mv reponame:Repositório Institucional da UNIFESP
instname:Universidade Federal de São Paulo (UNIFESP)
instacron:UNIFESP
instname_str Universidade Federal de São Paulo (UNIFESP)
instacron_str UNIFESP
institution UNIFESP
reponame_str Repositório Institucional da UNIFESP
collection Repositório Institucional da UNIFESP
repository.name.fl_str_mv Repositório Institucional da UNIFESP - Universidade Federal de São Paulo (UNIFESP)
repository.mail.fl_str_mv biblioteca.csp@unifesp.br
_version_ 1814268396440649728

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